日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Plasma proteome correlations with liver stiffness in pediatric cholestasis implicate epithelial to mesenchymal transition.

儿童胆汁淤积症中血浆蛋白质组与肝脏硬度的相关性表明上皮间质转化参与其中

Shneider Benjamin L, Kanchi Rupa S, Grimm Sandra L, Devaraj Sridevi, Emamaullee Juliet, Schraw Jeremy, Lupo Philip J, Bezerra Jorge A, Loomes Kathleen M, Magee John C, Sokol Ronald J, Wang Kasper S, Kriegmeier Alyssa, Hsu Evelyn, Molleston Jean P, Rosenthal Philip, Kohli Rohit, Karpen Saul J, Horslen Simon P, Jensen M Kyle, Barbetta Arianna, Coarfa Cristian

Increased serum GM-CSF at diagnosis of biliary atresia is associated with improved biliary drainage.

胆道闭锁诊断时血清 GM-CSF 水平升高与胆道引流改善相关

Taylor Sarah A, Harpavat Sanjiv, Gromer Kyle D, Andreev Victor, Loomes Kathleen M, Bezerra Jorge A, Jarasvaraparn Chaowapong, Wang Kasper, Horslen Simon, Rosenthal Philip, Teckman Jeffrey, Valentino Pamela L, Ng Vicky L, Karpen Saul J, Sokol Ronald J, Alonso Estella M, Mack Cara L

Prospective Multicenter Longitudinal Measurement of Liver Stiffness in School-Age Children With Cholestatic Liver Disease

前瞻性多中心纵向研究测量学龄期胆汁淤积性肝病患儿的肝脏硬度

Shneider, Benjamin L; Goodrich, Nathan P; Ye, Wen; Molleston, Jean P; Leung, Daniel H; Sokol, Ronald J; Cavallo, Laurel; Wang, Kasper; Valentino, Pamela L; Teckman, Jeffery H; Squires, James E; Sundaram, Shikha S; Rosenthal, Philip; Romero, Rene; Miethke, Alexander G; Loomes, Kathleen M; Kohli, Rohit; Karpen, Saul J; Kamath, Binita M; Jensen, M Kyle; Bezerra, Jorge A; Bass, Lee M; Magee, John C

Diagnostic accuracy of serum matrix metalloproteinase-7 as a biomarker of biliary atresia in a large North American cohort

血清基质金属蛋白酶-7作为胆道闭锁生物标志物的诊断准确性:一项北美大型队列研究

Pandurangi, Sindhu; Mourya, Reena; Nalluri, Shreya; Fei, Lin; Dong, Shun; Harpavat, Sanjiv; Guthery, Stephen L; Molleston, Jean P; Rosenthal, Philip; Sokol, Ronald J; Wang, Kasper S; Ng, Vicky; Alonso, Estella M; Hsu, Evelyn K; Karpen, Saul J; Loomes, Kathleen M; Magee, John C; Shneider, Benjamin L; Horslen, Simon P; Teckman, Jeffrey H; Bezerra, Jorge A

Similar brain proteomic signatures in Alzheimer’s disease and epilepsy

阿尔茨海默病和癫痫的脑蛋白质组学特征相似

Lertudomphonwanit, Chatmanee; Mourya, Reena; Fei, Lin; Zhang, Yue; Gutta, Sridevi; Yang, Li; Bove, Kevin E; Shivakumar, Pranavkumar; Bezerra, Jorge A; Nsangou, Yacoub Abelard Njipouombe; Wörheide, Maria A; Dönitz, Jürgen; Kastenmuller, Gabi; Arnold, Matthias; Wang, Biqi; Ding, Huitong; Qi, Derek; Tisminetzky, Mayra S; Murabito, Joanne M; Lin, Honghuang; Leitner, Dominique; Pires, Geoffrey; Kavanagh, Tomas; Kanshin, Evgeny; Askenazi, Manor; Ueberheide, Beatrix; Devinsky, Orrin; Drummond, Eleanor; Wisniewski, Thomas

Serum bile acids as a prognostic biomarker in biliary atresia following Kasai portoenterostomy

血清胆汁酸作为葛西氏肝门空肠吻合术后胆道闭锁的预后生物标志物

Harpavat, Sanjiv; Hawthorne, Kieran; Setchell, Kenneth D R; Rivas, Monica Narvaez; Henn, Lisa; Beil, Charlotte A; Karpen, Saul J; Ng, Vicky L; Alonso, Estella M; Bezerra, Jorge A; Guthery, Stephen L; Horslen, Simon; Loomes, Kathy M; McKiernan, Patrick; Magee, John C; Merion, Robert M; Molleston, Jean P; Rosenthal, Philip; Thompson, Richard J; Wang, Kasper S; Sokol, Ronald J; Shneider, Benjamin L

Genotype-phenotype relationships of truncating mutations, p.E297G and p.D482G in bile salt export pump deficiency

胆汁酸输出泵缺陷中截断突变 p.E297G 和 p.D482G 的基因型-表型关系

Felzen, Antonia; van Wessel, Daan B E; Gonzales, Emmanuel; Thompson, Richard J; Jankowska, Irena; Shneider, Benjamin L; Sokal, Etienne; Grammatikopoulos, Tassos; Kadaristiana, Agustina; Jacquemin, Emmanuel; Spraul, Anne; Lipiński, Patryk; Czubkowski, Piotr; Rock, Nathalie; Shagrani, Mohammad; Broering, Dieter; Nicastro, Emanuele; Kelly, Deirdre; Nebbia, Gabriella; Arnell, Henrik; Fischler, Björn; Hulscher, Jan B F; Serranti, Daniele; Arikan, Cigdem; Polat, Esra; Debray, Dominique; Lacaille, Florence; Goncalves, Cristina; Hierro, Loreto; Muñoz Bartolo, Gema; Mozer-Glassberg, Yael; Azaz, Amer; Brecelj, Jernej; Dezsőfi, Antal; Calvo, Pier Luigi; Grabhorn, Enke; Hartleif, Steffen; van der Woerd, Wendy J; Kamath, Binita M; Wang, Jian-She; Li, Liting; Durmaz, Özlem; Kerkar, Nanda; Jørgensen, Marianne Hørby; Fischer, Ryan; Jimenez-Rivera, Carolina; Alam, Seema; Cananzi, Mara; Laverdure, Noemie; Ferreira, Cristina Targa; Guerrero, Felipe Ordoñez; Wang, Heng; Sency, Valerie; Kim, Kyung Mo; Chen, Huey-Ling; de Carvalho, Elisa; Fabre, Alexandre; Bernabeu, Jesus Quintero; Zellos, Aglaia; Alonso, Estella M; Sokol, Ronald J; Suchy, Frederick J; Loomes, Kathleen M; McKiernan, Patrick J; Rosenthal, Philip; Turmelle, Yumirle; Horslen, Simon; Schwarz, Kathleen; Bezerra, Jorge A; Wang, Kasper; Hansen, Bettina E; Verkade, Henkjan J

Clinical spectrum and genetic causes of mitochondrial hepatopathy phenotype in children

儿童线粒体肝病表型的临床表现谱和遗传病因

Squires, James E; Miethke, Alexander G; Valencia, C Alexander; Hawthorne, Kieran; Henn, Lisa; Van Hove, Johan L K; Squires, Robert H; Bove, Kevin; Horslen, Simon; Kohli, Rohit; Molleston, Jean P; Romero, Rene; Alonso, Estella M; Bezerra, Jorge A; Guthery, Stephen L; Hsu, Evelyn; Karpen, Saul J; Loomes, Kathleen M; Ng, Vicky L; Rosenthal, Philip; Mysore, Krupa; Wang, Kasper S; Friederich, Marisa W; Magee, John C; Sokol, Ronald J

Recent Increase in Incidence of Severe Acute Hepatitis of Unknown Etiology in Children is Associated with Infection with Adenovirus and Other Nonhepatotropic Viruses

近期儿童不明原因重症急性肝炎发病率上升与腺病毒和其他非嗜肝病毒感染有关。

Peters, Anna L; Kim, Seung; Mourya, Reena; Asai, Akihiro; Taylor, Amy; Rogers, Michael; Campbell, Kathleen; Fei, Lin; Miethke, Alexander; Balistreri, William F; Bezerra, Jorge A

Customized Postoperative Therapy Improves Bile Drainage in Biliary Atresia: A Single Center Preliminary Report

个体化术后治疗改善胆道闭锁患者的胆汁引流:单中心初步报告

Pandurangi, Sindhu; Kim, Seung; Asai, Akihiro; Bondoc, Alexander; Balistreri, William; Campbell, Kathleen; Miethke, Alexander; Peters, Anna; Rogers, Michael; Taylor, Amy; Attia, Suzanna Labib; Gibbons, Troy; Mullapudi, Bhargava; Sheridan, Rachel; Tiao, Greg; Bezerra, Jorge A