Col6a1 knock-in mice provide a promising pre-clinical model for collagen VI-related dystrophies.
Col6a1 敲入小鼠为胶原蛋白 VI 相关营养不良症提供了一个有前景的临床前模型。
期刊:Disease Models & Mechanisms
影响因子:3.3
doi:10.1242/dmm.052460
López-Márquez ArÃstides, Badosa Carmen, Enjuanes-Ruiz Lluis, Hernández-Carabias Patricia, Sánchez-MartÃn Manuel, Cadot Bruno, Guesmia Zoheir, Georvasilis Ioannis, Balsells Sol, Blanco-Ramos Marcos, Puighermanal Emma, Quintana Albert, Roldán Mònica, Allamand Valérie, Jiménez-Mallebrera Cecilia