日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Real-Time MRI With Deep Learning for Efficient Evaluation of Neuromuscular Breathing Impairment

利用深度学习进行实时磁共振成像以高效评估神经肌肉呼吸障碍

Zeng, Rachel; Al-Bourini, Omar; Lettermann, Leonie; Lettermann, Leon; Olgemöller, Ulrike; Hofer, Sabine; Boentert, Matthias; Friede, Tim; Nietert, Manuel; Voit, Dirk; Frahm, Jens; Uecker, Martin; Seif Amir Hosseini, Ali; Schmidt, Jens

Between guidelines and reality: expert neurologists' perspectives on structural resources for ALS care in Germany

指南与现实之间:德国神经科专家对ALS护理结构性资源的看法

Linse, Katharina; Lulé, Dorothée; Schöberl, Florian; Reilich, Peter; Ilse, Benjamin; Metelmann, Moritz; Eickhoff, Clemens; Bublitz, Sarah; Lorenzl, Stefan; Boentert, Matthias; Petri, Susanne; Rödiger, Annekathrin; Smesny, Uta; Wolf, Joachim; Weyen, Ute; Zeller, Daniel; Dorst, Johannes; Maier, André; Meyer, Thomas; Lingor, Paul; Hermann, Andreas; Regensburger, Martin; Großkreutz, Julian; Runge, Clemens; Lapp, Hanna Sophie; Freigang, Maren; Vidovic, Maximilian; Aust, Elisa; Weber, Constanze; Günther, René

Shared prognostic information in amyotrophic lateral sclerosis - systematic assessment of the patients' perception of neurofilament light chain and the ALS functional rating scale

肌萎缩侧索硬化症预后信息的共享——系统评估患者对神经丝轻链和ALS功能评定量表的感知

Möhwald, Lukas Maximilian; Maier, André; Grehl, Torsten; Weyen, Ute; Weydt, Patrick; Günther, René; Lingor, Paul; Göricke, Bettina; Petri, Susanne; Grosskreutz, Julian; Boentert, Matthias; Cordts, Isabell; Weishaupt, Jochen H; Dorst, Johannes; Münch, Christoph; Meyer, Thomas; Baum, Petra

Motor phenotypes of amyotrophic lateral sclerosis - a three-determinant anatomical classification based on the region of onset, propagation of motor symptoms, and the degree of upper and lower motor neuron dysfunction

肌萎缩侧索硬化症的运动表型——基于发病区域、运动症状扩散以及上、下运动神经元功能障碍程度的三因素解剖学分类

Meyer, Thomas; Boentert, Matthias; Großkreutz, Julian; Weydt, Patrick; Bernsen, Sarah; Reilich, Peter; Steinbach, Robert; Rödiger, Annekathrin; Wolf, Joachim; Weyen, Ute; Ludolph, Albert C; Weishaupt, Jochen; Petri, Susanne; Lingor, Paul; Günther, René; Löscher, Wolfgang; Weber, Markus; Münch, Christoph; Maier, André; Grehl, Torsten

Efficacy of Switching Therapy From Alglucosidase Alfa to Avalglucosidase Alfa on Respiratory Function in Participants With Late-Onset Pompe Disease: A Post Hoc Analysis From the COMET Trial

在晚发型庞贝病患者中,从阿糖苷酶α换用阿伐糖苷酶α治疗对呼吸功能的影响:COMET试验的事后分析

Kishnani, Priya S; Boentert, Matthias; Wenninger, Stephan; Berger, Kenneth I; Msihid, Jérôme; O'Callaghan, Lasair; Essadi-Addou, Rachida; Gallego, Victor; Rawat, Neeraj Singh; Huynh-Ba, Olivier; Diaz-Manera, Jordi

In-depth analysis of data from the RAS-ALS study reveals new insights in rasagiline treatment for amyotrophic lateral sclerosis

对 RAS-ALS 研究数据的深入分析揭示了雷沙吉兰治疗肌萎缩侧索硬化症的新见解

Schuster, Joachim; Dreyhaupt, Jens; Mönkemöller, Karla; Dupuis, Luc; Dieterlé, Stéphane; Weishaupt, Jochen H; Kassubek, Jan; Petri, Susanne; Meyer, Thomas; Grosskreutz, Julian; Schrank, Berthold; Boentert, Matthias; Emmer, Alexander; Hermann, Andreas; Zeller, Daniel; Prudlo, Johannes; Winkler, Andrea S; Grehl, Torsten; Heneka, Michael T; Johannesen, Siw; Göricke, Bettina; Witzel, Simon; Dorst, Johannes; Ludolph, Albert C

Serum neurofilament light chain in distinct phenotypes of amyotrophic lateral sclerosis: A longitudinal, multicenter study

肌萎缩侧索硬化症不同表型患者血清神经丝轻链水平:一项纵向多中心研究

Meyer, Thomas; Dreger, Marie; Grehl, Torsten; Weyen, Ute; Kettemann, Dagmar; Weydt, Patrick; Günther, René; Lingor, Paul; Petri, Susanne; Koch, Jan Christoph; Großkreutz, Julian; Rödiger, Annekathrin; Baum, Petra; Hermann, Andreas; Prudlo, Johannes; Boentert, Matthias; Weishaupt, Jochen H; Löscher, Wolfgang N; Dorst, Johannes; Koc, Yasemin; Bernsen, Sarah; Cordts, Isabell; Vidovic, Maximilian; Steinbach, Robert; Metelmann, Moritz; Kleinveld, Vera E; Norden, Jenny; Ludolph, Albert; Walter, Bertram; Schumann, Peggy; Münch, Christoph; Körtvélyessy, Péter; Maier, André

Applying the win ratio method in clinical trials of orphan drugs: an analysis of data from the COMET trial of avalglucosidase alfa in patients with late-onset Pompe disease

在孤儿药临床试验中应用胜率法:对晚发型庞贝病患者服用阿伐葡萄糖苷酶α的COMET试验数据分析

Boentert, Matthias; Berger, Kenneth I; Díaz-Manera, Jordi; Dimachkie, Mazen M; Hamed, Alaa; Riou França, Lionel; Thibault, Nathan; Shukla, Pragya; Ishak, Jack; Caro, J Jaime

Patients' and caregivers' perception of multidimensional and palliative care in amyotrophic lateral sclerosis - protocol of a German multicentre study

肌萎缩侧索硬化症患者及其照护者对多维度和姑息治疗的认知——一项德国多中心研究方案

Linse, Katharina; Weber, Constanze; Reilich, Peter; Schöberl, Florian; Boentert, Matthias; Petri, Susanne; Rödiger, Annekathrin; Posa, Andreas; Otto, Markus; Wolf, Joachim; Zeller, Daniel; Brunkhorst, Robert; Koch, Jan; Hermann, Andreas; Großkreutz, Julian; Schröter, Carsten; Groß, Martin; Lingor, Paul; Machetanz, Gerrit; Semmler, Luisa; Dorst, Johannes; Lulé, Dorothée; Ludolph, Albert; Meyer, Thomas; Maier, André; Metelmann, Moritz; Regensburger, Martin; Winkler, Jürgen; Schrank, Berthold; Kohl, Zacharias; Hagenacker, Tim; Brakemeier, Svenja; Weyen, Ute; Weiler, Markus; Lorenzl, Stefan; Bublitz, Sarah; Weydt, Patrick; Grehl, Torsten; Kotterba, Sylvia; Lapp, Hanna-Sophie; Freigang, Maren; Vidovic, Maximilian; Aust, Elisa; Günther, René

[End of life perspectives: a systematic survey of patients with amyotrophic lateral sclerosis]

[生命末期视角:肌萎缩侧索硬化症患者的系统调查]

Eickhoff, Clemens; Schöne-Seifert, Bettina; Kettemann, Dagmar; Bormann, Eike; Grehl, Torsten; Boentert, Matthias; Koch, Jan C; Schmitt, Carolina; Schrank, Bertold; Schröter, Carsten; Meyer, Thomas