日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A mouse model of cardiac immunoglobulin light chain amyloidosis reveals insights into tissue accumulation and toxicity of amyloid fibrils

小鼠心脏免疫球蛋白轻链淀粉样变性模型揭示了淀粉样原纤维在组织中的积累和毒性

Martinez-Rivas, Gemma; Ayala, Maria Victoria; Bender, Sebastien; Codo, Gilles Roussine; Swiderska, Weronika Karolina; Lampis, Alessio; Pedroza, Laura; Merdanovic, Melisa; Sicard, Pierre; Pinault, Emilie; Richard, Laurence; Lavatelli, Francesca; Giorgetti, Sofia; Canetti, Diana; Rinsant, Alexa; Kaaki, Sihem; Ory, Cécile; Oblet, Christelle; Pollet, Justine; Naser, Eyad; Carpinteiro, Alexander; Roussel, Muriel; Javaugue, Vincent; Jaccard, Arnaud; Bonaud, Amélie; Delpy, Laurent; Ehrmann, Michael; Bridoux, Frank; Sirac, Christophe

CXCR4 signaling determines the fate of hematopoietic multipotent progenitors by stimulating mTOR activity and mitochondrial metabolism.

CXCR4 信号通过刺激 mTOR 活性和线粒体代谢来决定造血多能祖细胞的命运

Rondeau Vincent, Kalogeraki Maria, Roland Lilian, Nader Zeina Abou, Gourhand Vanessa, Bonaud Amélie, Lemos Julia, Khamyath Mélanie, Moulin Clémentine, Schell Bérénice, Delord Marc, Bidaut Ghislain, Lecourt Séverine, Freitas Christelle, Anginot Adrienne, Mazure Nathalie, McDermott David H, Parietti Véronique, Setterblad Niclas, Dulphy Nicolas, Bachelerie Françoise, Aurrand-Lions Michel, Stockholm Daniel, Lobry Camille, Murphy Philip M, Espéli Marion, Mancini Stéphane J C, Balabanian Karl

WHIM Syndrome-linked CXCR4 mutations drive osteoporosis

WHIM 综合征相关 CXCR4 突变导致骨质疏松症

Adrienne Anginot #, Julie Nguyen #, Zeina Abou Nader #, Vincent Rondeau, Amélie Bonaud, Maria Kalogeraki, Antoine Boutin, Julia P Lemos, Valeria Bisio, Joyce Koenen, Lea Hanna Doumit Sakr, Amandine Picart, Amélie Coudert, Sylvain Provot, Nicolas Dulphy, Michel Aurrand-Lions, Stéphane J C Mancini, Gw

Sec22b is a critical and nonredundant regulator of plasma cell maintenance

Sec22b 是浆细胞维持的关键且非冗余的调节剂

Amélie Bonaud, Laetitia Gargowitsch, Simon M Gilbert, Elanchezhian Rajan, Pablo Canales-Herrerias, Daniel Stockholm, Nabila F Rahman, Mark O Collins, Hakan Taskiran, Danika L Hill, Andres Alloatti, Nagham Alouche, Stéphanie Balor, Vanessa Soldan, Daniel Gillet, Julien Barbier, Françoise Bachelerie, 

Fine-tuning of MEK signaling is pivotal for limiting B and T cell activation

MEK 信号的微调对于限制 B 细胞和 T 细胞活化至关重要

Nicolas Houde, Laurent Beuret, Amélie Bonaud, Simon-Pierre Fortier-Beaulieu, Kim Truchon-Landry, Rifdat Aoidi, Émilie Pic, Nagham Alouche, Vincent Rondeau, Géraldine Schlecht-Louf, Karl Balabanian, Marion Espéli, Jean Charron

Hematologic disorder-associated Cxcr4 gain-of-function mutation leads to uncontrolled extrafollicular immune response

血液系统疾病相关的Cxcr4功能获得性突变导致不受控制的滤泡外免疫反应

Alouche, Nagham; Bonaud, Amélie; Rondeau, Vincent; Hussein-Agha, Rim; Nguyen, Julie; Bisio, Valeria; Khamyath, Mélanie; Crickx, Etienne; Setterblad, Niclas; Dulphy, Nicolas; Mahevas, Matthieu; McDermott, David H; Murphy, Philip M; Balabanian, Karl; Espéli, Marion

Hematopoietic Multipotent Progenitors and Plasma Cells: Neighbors or Roommates in the Mouse Bone Marrow Ecosystem?

造血多能祖细胞和浆细胞:小鼠骨髓生态系统中的邻居还是室友?

Bonaud, Amélie; Lemos, Julia P; Espéli, Marion; Balabanian, Karl

IgH 3' regulatory region increases ectopic class switch recombination

IgH 3' 调节区增加异位类别转换重组

Sandrine Le Noir, Amélie Bonaud, Bastien Hervé, Audrey Baylet, François Boyer, Sandrine Lecardeur, Zeliha Oruc, Christophe Sirac, Michel Cogné

Comprehensive molecular characterization of a heavy chain deposition disease case

对一例重链沉积病病例进行全面的分子表征

Bender, Sébastien; Ayala, Maria Victoria; Javaugue, Vincent; Bonaud, Amélie; Cogné, Michel; Touchard, Guy; Jaccard, Arnaud; Bridoux, Frank; Sirac, Christophe

Impaired Lysosomal Function Underlies Monoclonal Light Chain-Associated Renal Fanconi Syndrome

溶酶体功能障碍是单克隆轻链相关肾范可尼综合征的根本原因

Luciani, Alessandro; Sirac, Christophe; Terryn, Sara; Javaugue, Vincent; Prange, Jenny Ann; Bender, Sébastien; Bonaud, Amélie; Cogné, Michel; Aucouturier, Pierre; Ronco, Pierre; Bridoux, Frank; Devuyst, Olivier