日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Rigorous evaluation of pathological α-synucleinopathy transmissibility between animals in an experimental model

在实验模型中对动物间病理性α-突触核蛋白病的传播性进行严格评估

Sacino, Amanda N; Golde, Todd E; Borchelt, David R; Giasson, Benoit I; Moehle, Mark S

Fast and slow strains of misfolded mutant superoxide dismutase 1 in familial amyotrophic lateral sclerosis

家族性肌萎缩侧索硬化症中错误折叠突变超氧化物歧化酶 1 的快慢两种菌株

Xu, Guilian; Dillon, Kristy; Lopez, Amanda; Brkic, Selma; Fromholt, Susan; Ostrow, Lyle W; Glass, Jonathan D; Chakrabarty, Paramita; Ayers, Jacob I; Borchelt, David R

Progressive Supranuclear Palsy PERK Haplotype B Selectively Translates DLX1 Promoting Tau Toxicity

进行性核上性麻痹症 PERK 单倍型 B 选择性翻译 DLX1 促进 Tau 毒性

Lessard, Christian B; Rubio Rubio, Diego; Tolton, Samantha; Criado-Marrero, Marangelie; Ravi, Sakthivel; Garza, Tristyn N; Koren, John; Philips, Jennifer; Bagchi, Pritha; McFarland, Karen; Chhangani, Deepak; Golde, Todd E; Giasson, Benoit I; Lewis, Jada; Chakrabarty, Paramita; LaVoie, Matthew J; Borchelt, David R; Seyfried, Nicholas T; Prokop, Stefan; Rincon-Limas, Diego E; Abisambra, Jose F

Efficient induction of motor neuron disease in transgenic G93A SOD1 mice by prion-like seeding

通过朊病毒样播种在转基因G93A SOD1小鼠中高效诱导运动神经元疾病

Xu, Guilian; Lopez, Amanda; Brkic, Selma; Fromholt, Susan; Chakrabarty, Paramita; Borchelt, David R

Correction: Collusion of α-Synuclein and Aβ aggravating co-morbidities in a novel prion-type mouse model

更正:α-突触核蛋白和Aβ的协同作用加剧了新型朊病毒型小鼠模型中的合并症

Lloyd, Grace M; Dhillon, Jess-Karan S; Gorion, Kimberly-Marie M; Riffe, Cara; Fromholt, Susan E; Xia, Yuxing; Giasson, Benoit I; Borchelt, David R

Multiple Factors Influence the Incubation Period of ALS Prion-like Transmission in SOD1 Transgenic Mice

多种因素影响SOD1转基因小鼠ALS朊病毒样传播的潜伏期

Ayers, Jacob I; Xu, Guilian; Lu, Qing; Dillon, Kristy; Fromholt, Susan; Borchelt, David R

Impact of APOE genotype on prion-type propagation of tauopathy

APOE基因型对tau蛋白病朊病毒型传播的影响

Williams, Tristan; Ruiz, Alejandra Jolie; Ruiz, Angelica Maria; Vo, Quan; Tsering, Wangchen; Xu, Guilian; McFarland, Karen; Giasson, Benoit I; Sullivan, Patrick; Borchelt, David R; Chakrabarty, Paramita

Soluble brain homogenates from diverse human and mouse sources preferentially seed diffuse Aβ plaque pathology when injected into newborn mouse hosts

将来自不同人类和小鼠来源的可溶性脑匀浆注射到新生小鼠体内后,会优先诱导弥漫性Aβ斑块病变的发生。

Moore, Brenda D; Levites, Yona; Xu, Guilian; Hampton, Hailey; Adamo, Munir F; Croft, Cara L; Futch, Hunter S; Moran, Corey; Fromholt, Susan; Janus, Christopher; Prokop, Stefan; Dickson, Dennis; Lewis, Jada; Giasson, Benoit I; Golde, Todd E; Borchelt, David R

Pathogenic tau recruits wild-type tau into brain inclusions and induces gut degeneration in transgenic SPAM mice

致病性tau蛋白将野生型tau蛋白募集到脑内包涵体中,并诱导转基因SPAM小鼠肠道退化。

Xia, Yuxing; Prokop, Stefan; Bell, Brach M; Gorion, Kimberly-Marie M; Croft, Cara L; Nasif, Lith; Xu, Guilian; Riffe, Cara J; Manaois, Alyssa N; Strang, Kevin H; Quintin, Stephan S; Paterno, Giavanna; Tansey, Malú Gámez; Borchelt, David R; Golde, Todd E; Giasson, Benoit I

Modeling the Competition between Misfolded Aβ Conformers That Produce Distinct Types of Amyloid Pathology in Alzheimer's Disease

模拟错误折叠的Aβ构象异构体之间的竞争,这些构象异构体在阿尔茨海默病中产生不同类型的淀粉样蛋白病理

Xu, Guilian; Fromholt, Susan; Borchelt, David R