日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Alpha-defensins increase NTHi binding but not engulfment by the macrophages enhancing airway inflammation in Alpha-1 antitrypsin deficiency

α-防御素可增加非典型流感嗜血杆菌(NTHi)与巨噬细胞的结合,但不会增加巨噬细胞对其的吞噬作用,从而加剧α1-抗胰蛋白酶缺乏症患者的气道炎症。

Lee, Jungnam; Mohammad, Naweed; Han, Kyudong; Flagg-Dowie, Tammy; Magallon, Maria; Brantly, Mark L; Serban, Karina A

Monocyte NLRP3 inflammasome and interleukin-1β activation modulated by alpha-1 antitrypsin therapy in deficient individuals

在缺乏α1-抗胰蛋白酶的个体中,单核细胞NLRP3炎症小体和白细胞介素-1β的激活受α1-抗胰蛋白酶治疗的调节

Gogoi, Debananda; Yu, Howard; Casey, Michelle; Baird, Rory; Yusuf, Azeez; Forde, Luke; O' Brien, Michael E; West, Jesse R; Flagg, Tammy; McElvaney, Noel G; Eden, Edward; Mueller, Christian; Brantly, Mark L; Geraghty, Patrick; Reeves, Emer P

Recombinant Alpha-1 Antitrypsin-Fc Fusion Protein INBRX-101 in Adults With Alpha-1 Antitrypsin Deficiency: A Phase 1 Study

重组α1-抗胰蛋白酶-Fc融合蛋白INBRX-101治疗成人α1-抗胰蛋白酶缺乏症:一项I期研究

Brantly, Mark L; Kuhn, Brooks T; Farah, Humam W; Mahadeva, Ravi; Cole, Alexandra; Chang, Catherina L; Brown, Cynthia D; Campos, Michael A; Lascano, Jorge E; Babcock, Erin K; Bhagwat, Sharvari P; Boyea, Teresa F; Veldstra, Carson A; Andrianov, Vasily; Kalabus, James L; Eckelman, Brendan P; Veale, Andrew G

Development of a risk score to increase detection of severe alpha-1 antitrypsin deficiency

开发风险评分以提高严重α1-抗胰蛋白酶缺乏症的检出率

Riley, E Leonard; Brunson, J Cory; Eydgahi, Soroush; Brantly, Mark L; Lascano, Jorge E

Multiplexing AAV Serotype-Specific Neutralizing Antibodies in Preclinical Animal Models and Humans

在临床前动物模型和人体中应用多重AAV血清型特异性中和抗体

Kuoch, Hisae; Krotova, Karina; Graham, Melanie L; Brantly, Mark L; Aslanidi, George

Novel SERPINA1 Alleles Identified through a Large Alpha-1 Antitrypsin Deficiency Screening Program and Review of Known Variants

通过大规模α1-抗胰蛋白酶缺乏症筛查计划和对已知变异的回顾,鉴定出新的SERPINA1等位基因

Wiesemann, Gayle S; Oshins, Regina A; Flagg, Tammy O; Brantly, Mark L

Analysis of the MILES cohort reveals determinants of disease progression and treatment response in lymphangioleiomyomatosis.

MILES队列分析揭示了淋巴管肌瘤病疾病进展和治疗反应的决定因素

Gupta Nishant, Lee Hye-Seung, Young Lisa R, Strange Charlie, Moss Joel, Singer Lianne G, Nakata Koh, Barker Alan F, Chapman Jeffrey T, Brantly Mark L, Stocks James M, Brown Kevin K, Lynch Joseph P 3rd, Goldberg Hilary J, Downey Gregory P, Taveira-DaSilva Angelo M, Krischer Jeffrey P, Setchell Kenneth, Trapnell Bruce C, Inoue Yoshikazu, McCormack Francis X

Chemokine signaling axis between endothelial and myeloid cells regulates development of pulmonary hypertension associated with pulmonary fibrosis and hypoxia

内皮细胞和髓系细胞之间的趋化因子信号轴调控与肺纤维化和缺氧相关的肺动脉高压的发展。

Oliveira, Aline C; Fu, Chunhua; Lu, Yuanqing; Williams, Mason A; Pi, Liya; Brantly, Mark L; Ventetuolo, Corey E; Raizada, Mohan K; Mehrad, Borna; Scott, Edward W; Bryant, Andrew J

Alpha-1 Antitrypsin Attenuates Acute Lung Allograft Injury in a Rat Lung Transplant Model

α1-抗胰蛋白酶可减轻大鼠肺移植模型中的急性肺同种异体移植损伤

Emtiazjoo, Amir M; Hu, Hanbo; Lu, Li; Brantly, Mark L

Myeloid-derived Suppressor Cells Are Necessary for Development of Pulmonary Hypertension

髓系来源的抑制细胞是肺动脉高压发展所必需的

Bryant, Andrew J; Shenoy, Vinayak; Fu, Chunhua; Marek, George; Lorentsen, Kyle J; Herzog, Erica L; Brantly, Mark L; Avram, Dorina; Scott, Edward W