日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Characterization of β-Hydroxybutyrate as a Cell Autonomous Fuel for Active Excitatory and Inhibitory Neurons: β-Hydroxybutyrate as a Fuel for Active Neurons

β-羟基丁酸作为活性兴奋性和抑制性神经元细胞自主燃料的表征:β-羟基丁酸作为活性神经元的燃料

Kirsten Bredvik, Charmaine Liu, Timothy A Ryan

A ratiometric ER calcium sensor for quantitative comparisons across cell types and subcellular regions

用于跨细胞类型和亚细胞区域定量比较的比例型内质网钙传感器

Ryan J Farrell, Kirsten G Bredvik, Michael B Hoppa, S Thomas Hennigan, Timothy A Brown, Timothy A Ryan

Accelerated transsulfuration metabolically defines a discrete subclass of amyotrophic lateral sclerosis patients

代谢过程中加速的转硫作用定义了肌萎缩侧索硬化症患者的一个独特亚型。

Chen, Qiuying; Konrad, Csaba; Sandhu, Davinder; Roychoudhury, Dipa; Schwartz, Benjamin I; Cheng, Roger R; Bredvik, Kirsten; Kawamata, Hibiki; Calder, Elizabeth L; Studer, Lorenz; Fischer, Steven M; Manfredi, Giovanni; Gross, Steven S

Early conservation benefits of a de facto marine protected area at San Clemente Island, California

加利福尼亚州圣克莱门特岛事实上的海洋保护区早期保护效益

Esgro, Michael W; Lindholm, James; Nickols, Kerry J; Bredvik, Jessica

ALS/FTD mutant CHCHD10 mice reveal a tissue-specific toxic gain-of-function and mitochondrial stress response

ALS/FTD 突变体 CHCHD10 小鼠表现出组织特异性毒性功能获得和线粒体应激反应。

Anderson, Corey J; Bredvik, Kirsten; Burstein, Suzanne R; Davis, Crystal; Meadows, Samantha M; Dash, Jalia; Case, Laure; Milner, Teresa A; Kawamata, Hibiki; Zuberi, Aamir; Piersigilli, Alessandra; Lutz, Cathleen; Manfredi, Giovanni

Nrf2 signaling links ER oxidative protein folding and calcium homeostasis in health and disease

Nrf2 信号与健康和疾病中的内质网氧化蛋白折叠和钙稳态相关

Veronica Granatiero, Csaba Konrad, Kirsten Bredvik, Giovanni Manfredi, Hibiki Kawamata

Fibroblast bioenergetics to classify amyotrophic lateral sclerosis patients

利用成纤维细胞生物能量学对肌萎缩侧索硬化症患者进行分类

Konrad, Csaba; Kawamata, Hibiki; Bredvik, Kirsten G; Arreguin, Andrea J; Cajamarca, Steven A; Hupf, Jonathan C; Ravits, John M; Miller, Timothy M; Maragakis, Nicholas J; Hales, Chadwick M; Glass, Jonathan D; Gross, Steven; Mitsumoto, Hiroshi; Manfredi, Giovanni

Mutant TDP-43 does not impair mitochondrial bioenergetics in vitro and in vivo

突变的 TDP-43 不会损害体内和体外的线粒体生物能量学

Hibiki Kawamata, Pablo Peixoto, Csaba Konrad, Gloria Palomo, Kirsten Bredvik, Meri Gerges, Federica Valsecchi, Leonard Petrucelli, John M Ravits, Anatoly Starkov, Giovanni Manfredi

Human SOD1 ALS Mutations in a Drosophila Knock-In Model Cause Severe Phenotypes and Reveal Dosage-Sensitive Gain- and Loss-of-Function Components

果蝇基因敲入模型中的人类 SOD1 ALS 突变导致严重的表型并揭示剂量敏感的功能获得和丧失成分

Aslı Şahin, Aaron Held, Kirsten Bredvik, Paxton Major, Toni-Marie Achilli, Abigail G Kerson, Kristi Wharton, Geoff Stilwell, Robert Reenan