日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Dutch clinical practice guideline for paediatric palliative care: a systematic review and recommendations on psychosocial care including preloss and bereavement care

荷兰儿科姑息治疗临床实践指南:一项关于心理社会关怀(包括临终关怀和丧亲关怀)的系统性回顾和建议

van Teunenbroek, Kim C; Mulder, Renée L; Verhagen, A A Eduard; Kremer, Leontien C M; Falkenburg, Jeanette L; Honig-Mazer, Petra; van den Bergh, Esther M M; Kars, Marijke C; Verheijden, Johannes M A; Rippen, Hester; Borggreve, Brigitt C M; Kochen, Eline M; Michiels, Erna M C

GRID1/GluD1 homozygous variants linked to intellectual disability and spastic paraplegia impair mGlu1/5 receptor signaling and excitatory synapses

与智力障碍和痉挛性截瘫相关的GRID1/GluD1纯合变异会损害mGlu1/5受体信号传导和兴奋性突触。

Ung, Dévina C; Pietrancosta, Nicolas; Badillo, Elena Baz; Raux, Brigitt; Tapken, Daniel; Zlatanovic, Andjela; Doridant, Adrien; Pode-Shakked, Ben; Raas-Rothschild, Annick; Elpeleg, Orly; Abu-Libdeh, Bassam; Hamed, Nasrin; Papon, Marie-Amélie; Marouillat, Sylviane; Thépault, Rose-Anne; Stevanin, Giovanni; Elegheert, Jonathan; Letellier, Mathieu; Hollmann, Michael; Lambolez, Bertrand; Tricoire, Ludovic; Toutain, Annick; Hepp, Régine; Laumonnier, Frédéric

Unexpected Noncovalent Off-Target Activity of Clinical BTK Inhibitors Leads to Discovery of a Dual NUDT5/14 Antagonist

临床 BTK 抑制剂的意外非共价脱靶活性促成双重 NUDT5/14 拮抗剂的发现

Esra Balıkçı, Anne-Sophie M C Marques, Ludwig G Bauer, Raina Seupel, James Bennett, Brigitt Raux, Karly Buchan, Klemensas Simelis, Usha Singh, Catherine Rogers, Jennifer Ward, Carol Cheng, Tamas Szommer, Kira Schützenhofer, Jonathan M Elkins, David L Sloman, Ivan Ahel, Oleg Fedorov, Paul E Brennan, 

A Dutch paediatric palliative care guideline: a systematic review and evidence-based recommendations for symptom treatment

荷兰儿科姑息治疗指南:症状治疗的系统评价和循证建议

van Teunenbroek, Kim C; Mulder, Renée L; Ahout, Inge M L; Bindels-de Heus, Karen G C B; Delsman-van Gelder, Catharina M; Galimont-Collen, Annemie F S; de Groot, Marinka A R; Heitink-Polle, Katja M J; Looijestijn, Jeffry; Mensink, Maarten O; Mulder, Selma; Schieving, Jolanda H; Schouten-van Meeteren, Antoinette Y N; Verheijden, Johannes M A; Rippen, Hester; Borggreve, Brigitt C M; Kremer, Leontien C M; Verhagen, A A Eduard; Michiels, Erna M C

A Dutch paediatric palliative care guideline: a systematic review and recommendations on advance care planning and shared decision-making

荷兰儿科姑息治疗指南:关于预先照护计划和共同决策的系统评价和建议

van Teunenbroek, Kim C; Mulder, Renée L; van Heel, Dayna A M; Fahner, Jurrianne C; de Vos-Broerse, Mirjam A; Verheijden, Johannes M A; Rippen, Hester; Borggreve, Brigitt C M; Kremer, Leontien C M; Kars, Marijke C; Michiels, Erna M C; Verhagen, A A Eduard

Palliative care for children: methodology for the development of a national clinical practice guideline

儿童姑息治疗:制定国家临床实践指南的方法

van Teunenbroek, Kim C; Kremer, Leontien C M; Verhagen, A A Eduard; Verheijden, Johannes M A; Rippen, Hester; Borggreve, Brigitt C M; Michiels, Erna M C; Mulder, Renée L

Understanding U.S. Health Systems: Using Mixed Methods to Unpack Organizational Complexity

了解美国医疗体系:运用混合方法剖析组织复杂性

Ridgely, M Susan; Duffy, Erin; Wolf, Laura; Vaiana, Mary; Scanlon, Dennis; Buttorff, Christine; Leitzell, Brigitt; Ahluwalia, Sangeeta; Hilton, Lara; Agniel, Denis; Haviland, Amelia; Damberg, Cheryl L

Pegylated, full-length, recombinant factor VIII for prophylactic and on-demand treatment of severe hemophilia A

用于预防和按需治疗重型血友病A的聚乙二醇化全长重组凝血因子VIII

Konkle, Barbara A; Stasyshyn, Oleksandra; Chowdary, Pratima; Bevan, David H; Mant, Tim; Shima, Midori; Engl, Werner; Dyck-Jones, Jacqueline; Fuerlinger, Monika; Patrone, Lisa; Ewenstein, Bruce; Abbuehl, Brigitt

The dichloromethane extract of the ethnomedicinal plant Neurolaena lobata inhibits NPM/ALK expression which is causal for anaplastic large cell lymphomagenesis

民族药用植物 Neurolaena lobata 的二氯甲烷提取物可抑制 NPM/ALK 表达,而 NPM/ALK 表达是间变性大细胞淋巴瘤发生的原因

Christine Unger, Ruxandra Popescu, Benedikt Giessrigl, Daniela Laimer, Susanne Heider, Mareike Seelinger, Rene Diaz, Bruno Wallnöfer, Gerda Egger, Melanie Hassler, Martin Knöfler, Leila Saleh, Emine Sahin, Michael Grusch, Monika Fritzer-Szekeres, Helmut Dolznig, Richard Frisch, Lukas Kenner, Brigitt

Experience of Advate rAHF-PFM in previously untreated patients and minimally treated patients with haemophilia A

Advate rAHF-PFM 在既往未接受治疗和仅接受过少量治疗的 A 型血友病患者中的应用经验

Auerswald, Guenter; Thompson, Alexis A; Recht, Michael; Brown, Deborah; Liesner, Raina; Guzmán-Becerra, Norma; Dyck-Jones, Jacqueline; Ewenstein, Bruce; Abbuehl, Brigitt