日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Modeling immune lineage co-development in human pluripotent stem cell-derived liver organoids

利用人类多能干细胞衍生的肝脏类器官模拟免疫谱系共同发育

Rezvani, Milad; Quach, Susanna; Lewis, Kyle; Saiki, Norikazu; Xue, Chuqing; Kimura, Masaki; Iwasawa, Kentaro; Weihs, Julian; Elzobair, Tahlil; Al Reza, Hasan; Cai, Yuqi; Zhang, RanRan; Milton, Yuka; Chaturvedi, Praneet; Thorner, Konrad; Nayak, Ramesh C; Munera, Jorge; Kramer, Phillip; Davis, Brian R; Balamurugan, Appakalai N; Ahmed, Yeni Ait; Finke, Marcel; Behncke, Rose Yinghan; Guillot, Adrien; Hägerling, René; Polansky, Julia K; Bufler, Philip; Cancelas, Jose A; Zorn, Aaron M; Wells, James M; Yoshimoto, Momoko; Takebe, Takanori

Author Correction: Next-generation phenotyping integrated in a national framework for patients with ultrarare disorders improves genetic diagnostics and yields new molecular findings

作者更正:将新一代表型分析技术整合到国家层面的超罕见病患者诊疗框架中,可改进基因诊断并产生新的分子发现。

Schmidt, Axel; Danyel, Magdalena; Grundmann, Kathrin; Brunet, Theresa; Klinkhammer, Hannah; Hsieh, Tzung-Chien; Engels, Hartmut; Peters, Sophia; Knaus, Alexej; Moosa, Shahida; Averdunk, Luisa; Boschann, Felix; Sczakiel, Henrike Lisa; Schwartzmann, Sarina; Mensah, Martin Atta; Pantel, Jean Tori; Holtgrewe, Manuel; Bösch, Annemarie; Weiß, Claudia; Weinhold, Natalie; Suter, Aude-Annick; Stoltenburg, Corinna; Neugebauer, Julia; Kallinich, Tillmann; Kaindl, Angela M; Holzhauer, Susanne; Bührer, Christoph; Bufler, Philip; Kornak, Uwe; Ott, Claus-Eric; Schülke, Markus; Nguyen, Hoa Huu Phuc; Hoffjan, Sabine; Grasemann, Corinna; Rothoeft, Tobias; Brinkmann, Folke; Matar, Nora; Sivalingam, Sugirthan; Perne, Claudia; Mangold, Elisabeth; Kreiss, Martina; Cremer, Kirsten; Betz, Regina C; Mücke, Martin; Grigull, Lorenz; Klockgether, Thomas; Spier, Isabel; Heimbach, André; Bender, Tim; Brand, Fabian; Stieber, Christiane; Morawiec, Alexandra Marzena; Karakostas, Pantelis; Schäfer, Valentin S; Bernsen, Sarah; Weydt, Patrick; Castro-Gomez, Sergio; Aziz, Ahmad; Grobe-Einsler, Marcus; Kimmich, Okka; Kobeleva, Xenia; Önder, Demet; Lesmann, Hellen; Kumar, Sheetal; Tacik, Pawel; Bhasin, Meghna Ahuja; Incardona, Pietro; Lee-Kirsch, Min Ae; Berner, Reinhard; Schuetz, Catharina; Körholz, Julia; Kretschmer, Tanita; Di Donato, Nataliya; Schröck, Evelin; Heinen, André; Reuner, Ulrike; Hanßke, Amalia-Mihaela; Kaiser, Frank J; Manka, Eva; Munteanu, Martin; Kuechler, Alma; Cordula, Kiewert; Hirtz, Raphael; Schlapakow, Elena; Schlein, Christian; Lisfeld, Jasmin; Kubisch, Christian; Herget, Theresia; Hempel, Maja; Weiler-Normann, Christina; Ullrich, Kurt; Schramm, Christoph; Rudolph, Cornelia; Rillig, Franziska; Groffmann, Maximilian; Muntau, Ania; Tibelius, Alexandra; Schwaibold, Eva M C; Schaaf, Christian P; Zawada, Michal; Kaufmann, Lilian; Hinderhofer, Katrin; Okun, Pamela M; Kotzaeridou, Urania; Hoffmann, Georg F; Choukair, Daniela; Bettendorf, Markus; Spielmann, Malte; Ripke, Annekatrin; Pauly, Martje; Münchau, Alexander; Lohmann, Katja; Hüning, Irina; Hanker, Britta; Bäumer, Tobias; Herzog, Rebecca; Hellenbroich, Yorck; Westphal, Dominik S; Strom, Tim; Kovacs, Reka; Riedhammer, Korbinian M; Mayerhanser, Katharina; Graf, Elisabeth; Brugger, Melanie; Hoefele, Julia; Oexle, Konrad; Mirza-Schreiber, Nazanin; Berutti, Riccardo; Schatz, Ulrich; Krenn, Martin; Makowski, Christine; Weigand, Heike; Schröder, Sebastian; Rohlfs, Meino; Vill, Katharina; Hauck, Fabian; Borggraefe, Ingo; Müller-Felber, Wolfgang; Kurth, Ingo; Elbracht, Miriam; Knopp, Cordula; Begemann, Matthias; Kraft, Florian; Lemke, Johannes R; Hentschel, Julia; Platzer, Konrad; Strehlow, Vincent; Abou Jamra, Rami; Kehrer, Martin; Demidov, German; Beck-Wödl, Stefanie; Graessner, Holm; Sturm, Marc; Zeltner, Lena; Schöls, Ludger J; Magg, Janine; Bevot, Andrea; Kehrer, Christiane; Kaiser, Nadja; Turro, Ernest; Horn, Denise; Grüters-Kieslich, Annette; Klein, Christoph; Mundlos, Stefan; Nöthen, Markus; Riess, Olaf; Meitinger, Thomas; Krude, Heiko; Krawitz, Peter M; Haack, Tobias; Ehmke, Nadja; Wagner, Matias

Circulating Extracellular Vesicles as Putative Mediators of Cardiovascular Disease in Paediatric Chronic Kidney Disease

循环细胞外囊泡作为儿童慢性肾脏病心血管疾病的潜在介质

Behrens, Felix; Holle, Johannes; Chen, Chia-Yu; Ginsbach, Laura F; Krause, Benjamin C; Bruning, Ulrike; Kriegel, Fabian L; Kaiser, Toralf; Szijártó, István A; Anandakumar, Harithaa; Lehmann, Katrin; Schumacher, Fabian; Durek, Pawel; Heinrich, Frederik F; Lodka, Dörte; Hoffmann, Carina; Borchardt, André A; Peters, Lisa; Michalick, Laura; Querfeld, Uwe; Bufler, Philip; Luch, Andreas; Kleuser, Burkhard; Kirwan, Jennifer A; Forslund, Sofia K; Thumfahrt, Julia; Müller, Dominik; Wilck, Nicola; Mashreghi, Mir-Farzin; Löber, Ulrike; Bartolomaeus, Hendrik; Kuebler, Wolfgang M; Simmons, Szandor

Paediatric acute liver failure: A prospective, nationwide, population-based surveillance study in Germany

德国一项前瞻性、全国性、基于人群的儿童急性肝衰竭监测研究

Lenz, Dominic; Abdulaziz, Muhammad; Peters, Bianca; Wagner, Matias; Schlieben, Lea D; Corman, Victor M; Baumann, Ulrich; Bufler, Philip; Dattner, Tal; Ganschow, Rainer; Genzel, Kristin; Hammann, Nicole; Hartleif, Steffen; Hegen, Bianca; Henning, Stephan; Hoerning, André; Jankofsky, Martin; Junge, Norman; Kathemann, Simone; Knoppke, Birgit; Kohl-Sobania, Martina; Laass, Martin; Lainka, Elke; Lurz, Eberhard; Melter, Michael; Müller, Hanna; Pilic, Denisa; Ries, Markus; Schiefele, Lisa; Schwerd, Tobias; Sturm, Ekkehard; Wegner, Mechtild; Urschitz, Michael S; Garbade, Sven F; Wenning, Daniel; Drosten, Christian; Fichtner, Alexander; Kölker, Stefan; Hoffmann, Georg F; Prokisch, Holger; Staufner, Christian

The burden of Alagille syndrome: uncovering the potential of emerging therapeutics - a comprehensive systematic literature review

阿拉吉勒综合征的负担:揭示新兴疗法的潜力——一项全面的系统性文献综述

Bufler, Philip; Howard, Robin; Quadrado, Lucia; Lacey, Guy; Terner-Rosenthal, Jolan; Goldstein, Andrea; Vig, Pamela; Kelly, Deirdre

Next-generation phenotyping integrated in a national framework for patients with ultrarare disorders improves genetic diagnostics and yields new molecular findings

将新一代表型分析技术整合到国家级框架中,用于治疗罕见病患者,可改进基因诊断并产生新的分子发现。

Schmidt, Axel; Danyel, Magdalena; Grundmann, Kathrin; Brunet, Theresa; Klinkhammer, Hannah; Hsieh, Tzung-Chien; Engels, Hartmut; Peters, Sophia; Knaus, Alexej; Moosa, Shahida; Averdunk, Luisa; Boschann, Felix; Sczakiel, Henrike Lisa; Schwartzmann, Sarina; Mensah, Martin Atta; Pantel, Jean Tori; Holtgrewe, Manuel; Bösch, Annemarie; Weiß, Claudia; Weinhold, Natalie; Suter, Aude-Annick; Stoltenburg, Corinna; Neugebauer, Julia; Kallinich, Tillmann; Kaindl, Angela M; Holzhauer, Susanne; Bührer, Christoph; Bufler, Philip; Kornak, Uwe; Ott, Claus-Eric; Schülke, Markus; Nguyen, Hoa Huu Phuc; Hoffjan, Sabine; Grasemann, Corinna; Rothoeft, Tobias; Brinkmann, Folke; Matar, Nora; Sivalingam, Sugirthan; Perne, Claudia; Mangold, Elisabeth; Kreiss, Martina; Cremer, Kirsten; Betz, Regina C; Mücke, Martin; Grigull, Lorenz; Klockgether, Thomas; Spier, Isabel; Heimbach, André; Bender, Tim; Brand, Fabian; Stieber, Christiane; Morawiec, Alexandra Marzena; Karakostas, Pantelis; Schäfer, Valentin S; Bernsen, Sarah; Weydt, Patrick; Castro-Gomez, Sergio; Aziz, Ahmad; Grobe-Einsler, Marcus; Kimmich, Okka; Kobeleva, Xenia; Önder, Demet; Lesmann, Hellen; Kumar, Sheetal; Tacik, Pawel; Bhasin, Meghna Ahuja; Incardona, Pietro; Lee-Kirsch, Min Ae; Berner, Reinhard; Schuetz, Catharina; Körholz, Julia; Kretschmer, Tanita; Di Donato, Nataliya; Schröck, Evelin; Heinen, André; Reuner, Ulrike; Hanßke, Amalia-Mihaela; Kaiser, Frank J; Manka, Eva; Munteanu, Martin; Kuechler, Alma; Cordula, Kiewert; Hirtz, Raphael; Schlapakow, Elena; Schlein, Christian; Lisfeld, Jasmin; Kubisch, Christian; Herget, Theresia; Hempel, Maja; Weiler-Normann, Christina; Ullrich, Kurt; Schramm, Christoph; Rudolph, Cornelia; Rillig, Franziska; Groffmann, Maximilian; Muntau, Ania; Tibelius, Alexandra; Schwaibold, Eva M C; Schaaf, Christian P; Zawada, Michal; Kaufmann, Lilian; Hinderhofer, Katrin; Okun, Pamela M; Kotzaeridou, Urania; Hoffmann, Georg F; Choukair, Daniela; Bettendorf, Markus; Spielmann, Malte; Ripke, Annekatrin; Pauly, Martje; Münchau, Alexander; Lohmann, Katja; Hüning, Irina; Hanker, Britta; Bäumer, Tobias; Herzog, Rebecca; Hellenbroich, Yorck; Westphal, Dominik S; Strom, Tim; Kovacs, Reka; Riedhammer, Korbinian M; Mayerhanser, Katharina; Graf, Elisabeth; Brugger, Melanie; Hoefele, Julia; Oexle, Konrad; Mirza-Schreiber, Nazanin; Berutti, Riccardo; Schatz, Ulrich; Krenn, Martin; Makowski, Christine; Weigand, Heike; Schröder, Sebastian; Rohlfs, Meino; Vill, Katharina; Hauck, Fabian; Borggraefe, Ingo; Müller-Felber, Wolfgang; Kurth, Ingo; Elbracht, Miriam; Knopp, Cordula; Begemann, Matthias; Kraft, Florian; Lemke, Johannes R; Hentschel, Julia; Platzer, Konrad; Strehlow, Vincent; Abou Jamra, Rami; Kehrer, Martin; Demidov, German; Beck-Wödl, Stefanie; Graessner, Holm; Sturm, Marc; Zeltner, Lena; Schöls, Ludger J; Magg, Janine; Bevot, Andrea; Kehrer, Christiane; Kaiser, Nadja; Turro, Ernest; Horn, Denise; Grüters-Kieslich, Annette; Klein, Christoph; Mundlos, Stefan; Nöthen, Markus; Riess, Olaf; Meitinger, Thomas; Krude, Heiko; Krawitz, Peter M; Haack, Tobias; Ehmke, Nadja; Wagner, Matias

Patient-derived organoid biobank identifies epigenetic dysregulation of intestinal epithelial MHC-I as a novel mechanism in severe Crohn's Disease

患者来源的类器官生物库发现,肠上皮MHC-I的表观遗传失调是重症克罗恩病的一种新机制

Dennison, Thomas W; Edgar, Rachel D; Payne, Felicity; Nayak, Komal M; Ross, Alexander D B; Cenier, Aurelie; Glemas, Claire; Giachero, Federica; Foster, April R; Harris, Rebecca; Kraiczy, Judith; Salvestrini, Camilla; Stavrou, Georgia; Torrente, Franco; Brook, Kimberley; Trayers, Claire; Elmentaite, Rasa; Youssef, Gehad; Tél, Bálint; Winton, Douglas James; Skoufou-Papoutsaki, Nefeli; Adler, Sam; Bufler, Philip; Azabdaftari, Aline; Jenke, Andreas; G, Natasha; Thomas, Natasha; Miele, Erasmo; Al-Mohammad, Abdulrahman; Guarda, Greta; Kugathasan, Subra; Venkateswaran, Suresh; Clatworthy, Menna R; Castro-Dopico, Tomas; Suchanek, Ondrej; Strisciuglio, Caterina; Gasparetto, Marco; Lee, Seokjun; Xu, Xingze; Bello, Erica; Han, Namshik; Zerbino, Daniel R; Teichmann, Sarah A; Nys, Josquin; Heuschkel, Robert; Perrone, Francesca; Zilbauer, Matthias

Genetic landscape of pediatric acute liver failure of indeterminate origin

儿童不明原因急性肝衰竭的遗传图谱

Lenz, Dominic; Schlieben, Lea D; Shimura, Masaru; Bianzano, Alyssa; Smirnov, Dmitrii; Kopajtich, Robert; Berutti, Riccardo; Adam, Rüdiger; Aldrian, Denise; Baric, Ivo; Baumann, Ulrich; Bozbulut, Neslihan E; Brugger, Melanie; Brunet, Theresa; Bufler, Philip; Burnytė, Birutė; Calvo, Pier L; Crushell, Ellen; Dalgiç, Buket; Das, Anibh M; Dezsőfi, Antal; Distelmaier, Felix; Fichtner, Alexander; Freisinger, Peter; Garbade, Sven F; Gaspar, Harald; Goujon, Louise; Hadzic, Nedim; Hartleif, Steffen; Hegen, Bianca; Hempel, Maja; Henning, Stephan; Hoerning, Andre; Houwen, Roderick; Hughes, Joanne; Iorio, Raffaele; Iwanicka-Pronicka, Katarzyna; Jankofsky, Martin; Junge, Norman; Kanavaki, Ino; Kansu, Aydan; Kaspar, Sonja; Kathemann, Simone; Kelly, Deidre; Kirsaçlioğlu, Ceyda T; Knoppke, Birgit; Kohl, Martina; Kölbel, Heike; Kölker, Stefan; Konstantopoulou, Vassiliki; Krylova, Tatiana; Kuloğlu, Zarife; Kuster, Alice; Laass, Martin W; Lainka, Elke; Lurz, Eberhard; Mandel, Hanna; Mayerhanser, Katharina; Mayr, Johannes A; McKiernan, Patrick; McClean, Patricia; McLin, Valerie; Mention, Karine; Müller, Hanna; Pasquier, Laurent; Pavlov, Martin; Pechatnikova, Natalia; Peters, Bianca; Petković Ramadža, Danijela; Piekutowska-Abramczuk, Dorota; Pilic, Denisa; Rajwal, Sanjay; Rock, Nathalie; Roetig, Agnès; Santer, René; Schenk, Wilfried; Semenova, Natalia; Sokollik, Christiane; Sturm, Ekkehard; Taylor, Robert W; Tschiedel, Eva; Urbonas, Vaidotas; Urreizti, Roser; Vermehren, Jan; Vockley, Jerry; Vogel, Georg-Friedrich; Wagner, Matias; van der Woerd, Wendy; Wortmann, Saskia B; Zakharova, Ekaterina; Hoffmann, Georg F; Meitinger, Thomas; Murayama, Kei; Staufner, Christian; Prokisch, Holger

Fetal Liver-like Organoids Recapitulate Blood-Liver Niche Development and Multipotent Hematopoiesis from Human Pluripotent Stem Cells

胎肝样类器官可重现血液-肝脏微环境发育和人类多能干细胞的多能造血作用

Rezvani, Milad; Lewis, Kyle; Quach, Susanna; Iwasawa, Kentaro; Weihs, Julian; Reza, Hasan; Cai, Yuqi; Kimura, Masaki; Zhang, RanRan; Milton, Yuka; Chaturvedi, Praneet; Thorner, Konrad; Nayak, Ramesh C; Munera, Jorge O; Kramer, Phillip; Davis, Brian; Balamurugan, Appakalai; Ait Ahmed, Yeni; Finke, Marcel; Behncke, Rose Yinghan; Guillot, Adrien; Haegerling, Rene; Polansky, Julia; Bufler, Philip; Cancelas, Jose; Wells, James; Yoshimoto, Momoko; Takebe, Takanori

Modulation of intestinal IL-37 expression and its impact on the epithelial innate immune response and barrier integrity

肠道IL-37表达的调控及其对上皮固有免疫反应和屏障完整性的影响

Kröhn, Laura; Azabdaftari, Aline; Heuberger, Julian; Hudert, Christian; Zilbauer, Matthias; Breiderhoff, Tilman; Bufler, Philip