日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Correction: The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome

更正:化学伴侣4-苯基丁酸可挽救COL3A1基因突变导致的血管型埃勒斯-当洛斯综合征的分子细胞缺陷。

Omar, Ramla; Lee, Michelle Aw; Gonzalez-Trueba, Laura; Thomson, Cameron R; Hansen, Uwe; Lianos, Spyridonas; Hazarika, Snoopy; El Abdallah, Omar Hmeh; Ammar, Malak A; Cassels, Jennifer; Michie, Alison M; Bulleid, Neil J; Malfait, Fransiska; Van Agtmael, Tom

The chemical chaperone 4-phenylbutyric acid rescues molecular cell defects of COL3A1 mutations that cause vascular Ehlers Danlos Syndrome.

化学伴侣 4-苯基丁酸可挽救导致血管型埃勒斯-当洛斯综合征的 COL3A1 突变的分子细胞缺陷

Omar Ramla, Lee Michelle Aw, Gonzalez-Trueba Laura, Thomson Cameron R, Hansen Uwe, Lianos Spyridonas, Hazarika Snoopy, El Abdallah Omar Hmeh, Ammar Malak A, Cassels Jennifer, Michie Alison M, Bulleid Neil J, Malfait Fransiska, Van Agtmael Tom

Distinct role of ERp57 and ERdj5 as a disulfide isomerase and reductase during ER protein folding

ERp57 和 ERdj5 在 ER 蛋白质折叠过程中作为二硫键异构酶和还原酶的不同作用

Philip John Robinson, Marie Anne Pringle, Bethany Fleming, Neil John Bulleid

Dietary-derived vitamin B12 protects Caenorhabditis elegans from thiol-reducing agents.

膳食来源的维生素 B12 可保护秀丽隐杆线虫免受硫醇还原剂的侵害

Winter Alan D, Tjahjono Elissa, Beltrán Leonardo J, Johnstone Iain L, Bulleid Neil J, Page Antony P

Activation of the UPR sensor ATF6α is regulated by its redox-dependent dimerization and ER retention by ERp18

UPR 传感器 ATF6α 的激活受其氧化还原依赖性二聚化和 ERp18 的 ER 保留调控

Ojore Benedict Valentine Oka, Arvin Shedrach Pierre, Marie Anne Pringle, Wanida Tungkum, Zhenbo Cao, Bethany Fleming, Neil John Bulleid

A cytosolic reductase pathway is required for efficient N-glycosylation of an STT3B-dependent acceptor site

胞浆还原酶途径是 STT3B 依赖性受体位点有效 N-糖基化所必需的

Marcel van Lith, Marie Anne Pringle, Bethany Fleming, Giorgia Gaeta, Jisu Im, Reid Gilmore, Neil J Bulleid

Mollaret's triangle: An important neuroanatomical territory for all clinicians

莫拉雷三角:所有临床医生都必须关注的重要神经解剖区域

Bulleid, Lindsey; Hughes, Tom; Leach, Paul

Structure and Electron-Transfer Pathway of the Human Methionine Sulfoxide Reductase MsrB3.

人甲硫氨酸亚砜还原酶 MsrB3 的结构和电子转移途径

Javitt Gabriel, Cao Zhenbo, Resnick Efrat, Gabizon Ronen, Bulleid Neil J, Fass Deborah

Mechanisms of Disulfide Bond Formation in Nascent Polypeptides Entering the Secretory Pathway

新生多肽进入分泌途径时二硫键形成的机制

Robinson, Philip J; Bulleid, Neil J

The mammalian cytosolic thioredoxin reductase pathway acts via a membrane protein to reduce ER-localised proteins

哺乳动物细胞浆硫氧还蛋白还原酶途径通过膜蛋白起作用,减少内质网定位蛋白

Xiaofei Cao, Sergio Lilla, Zhenbo Cao, Marie Anne Pringle, Ojore B V Oka, Philip J Robinson, Tomasz Szmaja, Marcel van Lith, Sara Zanivan, Neil J Bulleid