日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Opantimirs: A class of antagonizing microRNAs that upregulate Opa1 and improve mitochondrial and disuse myopathies

Opantimirs:一类拮抗性microRNA,可上调Opa1并改善线粒体和废用性肌病。

Andre Djalalvandi ,Keisuke Takeda ,Francesca Grespi ,Hualin Fan ,Tiago Branco Fonseca ,Leonardo Nogara ,Saman Sharifi ,Carlotta Barison ,Martina Semenzato ,Akiko Omori ,Raffaele Cerutti ,Davide Steffan ,Lorenza Tsansizi ,Valeria Balmaceda ,Lukas Alan ,Camilla Bean ,Bert Blaauw ,Carlo Viscomi ,Luca Scorrano

Zebrafish polg2 knock-out recapitulates human POLG-disorders; implications for drug treatment

斑马鱼 polg2 基因敲除重现人类 POLG 疾病;对药物治疗的意义

Raquel Brañas Casas, Alessandro Zuppardo, Giovanni Risato, Alberto Dinarello, Rudy Celeghin, Camilla Fontana, Eleonora Grelloni, Alexandru Ionut Gilea, Carlo Viscomi, Andrea Rasola, Luisa Dalla Valle, Tiziana Lodi, Enrico Baruffini, Nicola Facchinello, Francesco Argenton, Natascia Tiso

NAD+ repletion with niacin counteracts cancer cachexia

补充烟酸和 NAD+ 可抵消癌症恶病质

Marc Beltrà #, Noora Pöllänen #, Claudia Fornelli, Kialiina Tonttila, Myriam Y Hsu, Sandra Zampieri, Lucia Moletta, Samantha Corrà, Paolo E Porporato, Riikka Kivelä, Carlo Viscomi, Marco Sandri, Juha J Hulmi, Roberta Sartori, Eija Pirinen, Fabio Penna

Tissue-specific differences in the assembly of mitochondrial Complex I are revealed by a novel ENU mutation in ECSIT

ECSIT 中的新 ENU 突变揭示了线粒体复合物 I 组装的组织特异性差异

Thomas Nicol, Sara Falcone, Andrew Blease, Pratik Vikhe, Gabriele Civiletto, Saleh Salman Omairi, Carlo Viscomi, Ketan Patel, Paul K Potter

Structural rather than catalytic role for mitochondrial respiratory chain supercomplexes

线粒体呼吸链超复合物的结构作用而非催化作用

Michele Brischigliaro, Alfredo Cabrera-Orefice, Susanne Arnold, Carlo Viscomi, Massimo Zeviani, Erika Fernández-Vizarra

Drosophila Mpv17 forms an ion channel and regulates energy metabolism

果蝇Mpv17形成离子通道并调节能量代谢

Samantha Corrà, Vanessa Checchetto, Michele Brischigliaro, Chiara Rampazzo, Emanuela Bottani, Cristina Gagliani, Katia Cortese, Cristiano De Pittà, Marco Roverso, Diego De Stefani, Sara Bogialli, Massimo Zeviani, Carlo Viscomi, Ildiko Szabò, Rodolfo Costa

PPAR-gamma agonist pioglitazone recovers mitochondrial quality control in fibroblasts from PITRM1-deficient patients

PPAR-γ激动剂吡格列酮可恢复PITRM1缺陷患者成纤维细胞的线粒体质量控制

Alessia Di Donfrancesco ,Christian Berlingieri ,Marta Giacomello ,Chiara Frascarelli ,Ana Paula Magalhaes Rebelo ,Laurence A Bindoff ,Segel Reeval ,Paul Renbaum ,Filippo M Santorelli ,Giulia Massaro ,Carlo Viscomi ,Massimo Zeviani ,Daniele Ghezzi ,Emanuela Bottani ,Dario Brunetti

Rapid fractionation of mitochondria from mouse liver and heart reveals in vivo metabolite compartmentation

小鼠肝脏和心脏线粒体的快速分离揭示了体内代谢物的区室化

Fay M Allen, Ana S H Costa, Anja V Gruszczyk, Georgina R Bates, Hiran A Prag, Efterpi Nikitopoulou, Carlo Viscomi, Christian Frezza, Andrew M James, Michael P Murphy

Double administration of self-complementary AAV9NDUFS4 prevents Leigh disease in Ndufs4-/- mice

双剂量自身互补的 AAV9NDUFS4 治疗可预防 Ndufs4-/- 小鼠患上 Leigh 病

Samantha Corrà, Raffaele Cerutti, Valeria Balmaceda, Carlo Viscomi, Massimo Zeviani

CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B

CG7630 是果蝇细胞色素 c 氧化酶亚基 COX7B 的同源物

Michele Brischigliaro, Alfredo Cabrera-Orefice, Mattia Sturlese, Dei M Elurbe, Elena Frigo, Erika Fernandez-Vizarra, Stefano Moro, Martijn A Huynen, Susanne Arnold, Carlo Viscomi, Massimo Zeviani