日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Childhood isolated C3d-positive AIHA: favorable prognosis but rare relapse or associated immunodeficiency

儿童孤立性C3d阳性自身免疫性溶血性贫血:预后良好,但复发或伴有免疫缺陷的情况罕见

Blachez, Marion; Aladjidi, Nathalie; Modot, Thomas; Fernandes, Helder; Garnier, Nathalie; Chastagner, Pascal; Bayart, Sophie; Armari-Alla, Corinne; Piguet, Christophe; Pasquet, Marlène; Paillard, Catherine; Pluchart, Claire; Guitton, Corinne; Thomas, Caroline; Barlogis, Vincent; Pellier, Isabelle; Stephan, Jean-Louis; Benadiba, Joy; Jeziorski, Eric; Deparis, Marianna; Carausu, Liana; Cheikh, Nathalie; Li-Thiao Te, Valérie; Lejeune, Julien; Marie-Cardine, Aude; Millot, Frédéric; Abou Chahla, Wadih; Gay, Sophie; Alimi, Aurélia; Petit, Arnaud; Castelle, Martin; Moshous, Despina; Picard, Capucine; Rieux-Laucat, Frédéric; Leblanc, Thierry; Ducassou, Stéphane; Leverger, Guy; Fahd, Mony; Héritier, Sébastien

Azathioprine or mycophenolate mofetil for pediatric autoimmune cytopenia: a propensity score-matched study

硫唑嘌呤或吗替麦考酚酯治疗儿童自身免疫性血细胞减少症:一项倾向评分匹配研究

Pincez, Thomas; Fernandes, Helder; Leverger, Guy; Barlogis, Vincent; Fahd, Mony; Garnier, Nathalie; Paillard, Catherine; Guitton, Corinne; Abou Chahla, Wadih; Pasquet, Marlène; Jeziorski, Eric; Castelle, Martin; Bayart, Sophie; Pellier, Isabelle; Thomas, Caroline; Pagnier, Anne; Benadiba, Joy; Li Thiao Te, Valérie; Cheikh, Nathalie; Lejeune, Julien; Deparis, Marianna; Marie-Cardine, Aude; Chastagner, Pascal; Desplantes, Claire; Millot, Frédéric; Vic, Philippe; Thouvenin, Sandrine; Piguet, Christophe; Pluchart, Claire; Leblanc, Thierry; Héritier, Sébastien; Aladjidi, Nathalie

Bilateral idiopathic peripapillary choroidal neovascularization in a child with bruton disease: a case report

布鲁顿病患儿双侧特发性视乳头周围脉络膜新生血管:病例报告

Kerkouri, Sarah; Dinahet, Jeanne Le; Bourhis, Marianne; Henry, Chloé; Castelle, Martin; Robert, Matthieu P; Cochener-Lamard, Béatrice

Severe inflammation and lineage skewing are associated with poor engraftment of engineered hematopoietic stem cells in patients with sickle cell disease

严重的炎症和谱系偏倚与镰状细胞病患者体内工程化造血干细胞移植失败有关。

Steicy Sobrino ,Laure Joseph ,Elisa Magrin ,Anne Chalumeau ,Nicolas Hebert ,Alice Corsia ,Adeline Denis ,Cécile Roudaut ,Clotilde Aussel ,Olivia Leblanc ,Mégane Brusson ,Tristan Felix ,Jean-Sebastien Diana ,Angelina Petrichenko ,Jana El Etri ,Auria Godard ,Eden Tibi ,Sandra Manceau ,Jean Marc Treluyer ,Fulvio Mavilio ,Frederic D Bushman ,Ambroise Marcais ,Martin Castelle ,Benedicte Neven ,Olivier Hermine ,Sylvain Renolleau ,Alessandra Magnani ,Vahid Asnafi ,Wassim El Nemer ,Pablo Bartolucci ,Emmanuelle Six ,Michaela Semeraro ,Annarita Miccio ,Marina Cavazzana

Integration of therapeutic cargo into the human genome with programmable type V-K CAST

利用可编程VK CAST将治疗性载荷整合到人类基因组中

Jason Liu # ,Daniela S Aliaga Goltsman # ,Lisa M Alexander ,Khak Khak Khayi ,Jennifer H Hong ,Drew T Dunham ,Christine A Romano ,Morayma M Temoche-Diaz ,Shailaja Chadha ,Rodrigo Fregoso Ocampo ,Jennifer Oki-O'Connell ,Owen P Janson ,Keirstinne Turcios ,Liliana Gonzalez-Osorio ,Jared Muysson ,Jenat Rahman ,Sarah M Laperriere ,Audra E Devoto ,Cindy J Castelle ,Cristina N Butterfield ,Gregory J Cost ,Christopher T Brown ,Brian C Thomas

Immunosuppression-Free Kidney Transplantation after Haploidentical Hematopoietic Stem Cell Transplantation in Fanconi Anemia

范可尼贫血症患者在单倍体造血干细胞移植后进行无免疫抑制剂肾移植

Kachmar, Jessica; Castelle, Martin; Gilles, David Saint; Terinte-Balcan, George; Boistault, Margaux; Blanc, Thomas; Zuber, Julien; Preka, Evgenia; Boyer, Olivia; Charbit, Marina; Dorval, Guillaume

Consecutive non-Aspergillus Fungal Invasive Infections in Chronic Granulomatous Disease: Data from the French National Reference Center for Primary ImmunoDeficiencies and literature review

慢性肉芽肿病中非曲霉菌侵袭性真菌的连续感染:来自法国国家原发性免疫缺陷参考中心的数据及文献综述

Lefevre, Leïla; Paccoud, Olivier; Neven, Bénédicte; Bougnoux, Marie-Elisabeth; Alligon, Mickaël; Bruneau, Julie; Fischer, Alain; Moshous, Despina; Bustamante, Jacinta; Picard, Capucine; Poiree, Sylvain; Guery, Romain; Castelle, Martin; Suarez, Felipe; Marcais, Ambroise; Cheminant, Morgane; Rouzaud, Claire; Hermoso, Dea Garcia; Salvator, Hélène; Catherinot, Emilie; Pilmis, Benoit; Luca, Luminita; Brion, Jean-Paul; Revest, Matthieu; Gandemer, Virginie; Lelievre, Lucie; Alvarez, Muriel; Conrad, Anne; Fouyssac, Fanny; Gaud, Catherine; Blumental, Sophie; Blanche, Stéphane; Lortholary, Olivier; Mahlaoui, Nizar; Lanternier, Fanny

Coastal shoreline change assessments at global scales

全球尺度上的海岸线变化评估

Warrick, Jonathan A; Buscombe, Daniel; Vos, Kilian; Bryan, Karin R; Castelle, Bruno; Cooper, J Andrew G; Harley, Mitch D; Jackson, Derek W T; Ludka, Bonnie C; Masselink, Gerd; Palmsten, Margaret L; Ruiz de Alegria-Arzaburu, Amaia; Sénéchal, Nadia; Sherwood, Christopher R; Short, Andrew D; Sogut, Erdinc; Splinter, Kristen D; Stephenson, Wayne J; Syvitski, Jaia; Young, Adam P

On behalf of the SFGM-TC: Real-life use of third-party virus-specific T-cell transfer in immunocompromised transplanted patients

代表SFGM-TC:第三方病毒特异性T细胞转移在免疫功能低下移植患者中的实际应用

Leroyer, Esther Hazane; Petitpain, Nadine; Morisset, Stéphane; Neven, Bénédicte; Castelle, Martin; Winter, Sarah; Souchet, Laetitia; Morel, Véronique; Le Cann, Marie; Fahd, Mony; Yacouben, Karima; Mechinaud, Françoise; Ouachée-Chardin, Marie; Renard, Cécile; Wallet, Hélène Labussière; Angoso, Marie; Jubert, Charlotte; Chevallier, Patrice; Léger, Alexandra; Rialland, Fanny; Dhedin, Nathalie; Robin, Christine; Maury, Sébastien; Beckerich, Florence; Beauvais, David; Cluzeau, Thomas; Loschi, Michaël; Fernster, Alina; Bittencourt, Marcelo De Carvalho; Cravat, Maxime; Bilger, Karin; Clément, Laurence; Decot, Véronique; Gauthier, Mélanie; Legendre, Anne; Larghero, Jérôme; Ouedrani, Amani; Martin-Blondel, Guillaume; Pochon, Cécile; Reppel, Loïc; Rouard, Hélène; Nguyen-Quoc, Stéphanie; Dalle, Jean-Hugues; D'Aveni, Maud; Bensoussan, Danièle

Somatic RAP1B gain-of-function variant underlies isolated thrombocytopenia and immunodeficiency

体细胞 RAP1B 功能获得性变异是孤立性血小板减少症和免疫缺陷的根本原因

Marta Benavides-Nieto ,Frédéric Adam ,Emmanuel Martin ,Charlotte Boussard ,Chantal Lagresle-Peyrou ,Isabelle Callebaut ,Alexandre Kauskot ,Christelle Repérant ,Miao Feng ,Jean-Claude Bordet ,Martin Castelle ,Guillaume Morelle ,Chantal Brouzes ,Mohammed Zarhrate ,Patricia Panikulam ,Nathalie Lambert ,Capucine Picard ,Damien Bodet ,Jérémie Rouger-Gaudichon ,Patrick Revy ,Jean-Pierre de Villartay ,Despina Moshous