Mutant SPART causes defects in mitochondrial protein import and bioenergetics reversed by Coenzyme Q
突变型SPART会导致线粒体蛋白输入和生物能量学缺陷,而辅酶Q可以逆转这种缺陷。
期刊:Open Biology
影响因子:3.6
doi:10.1098/rsob.230040
Diquigiovanni, Chiara; Rizzardi, Nicola; Kampmeier, Antje; Liparulo, Irene; Bianco, Francesca; De Nicolo, Bianca; Cataldi-Stagetti, Erica; Cuna, Elisabetta; Severi, Giulia; Seri, Marco; Bertrand, Miriam; Haack, Tobias B; Marina, Adela Della; Braun, Frederik; Fato, Romana; Kuechler, Alma; Bergamini, Christian; Bonora, Elena