Coenzyme Q10 Supplementation Increases Removal of the ATXN3 Polyglutamine Repeat, Reducing Cerebellar Degeneration and Improving Motor Dysfunction in Murine Spinocerebellar Ataxia Type 3
辅酶Q10补充剂可促进ATXN3多聚谷氨酰胺重复序列的清除,从而减少小鼠脊髓小脑性共济失调3型的小脑变性并改善运动功能障碍
期刊:Nutrients
影响因子:5
doi:10.3390/nu14173593
Wu, Yu-Ling; Chang, Jui-Chih; Sun, Hai-Lun; Cheng, Wen-Ling; Yen, Yu-Pei; Lin, Yong-Shiou; Chao, Yi-Chun; Liu, Ko-Hung; Huang, Ching-Shan; Liu, Kai-Li; Liu, Chin-San