Enhanced lysosomal exocytosis and altered growth factor signaling are associated with cartilage pathology in a model of mucopolysaccharidosis type IVA.
在粘多糖贮积症 IVA 型模型中,溶酶体胞吐作用增强和生长因子信号传导改变与软骨病理有关。
期刊:Disease Models & Mechanisms
影响因子:3.3
doi:10.1242/dmm.052582
Lee Jen-Jie, Lu Po-Nien, Dukes-Rimsky Lynn, Jeter Chelsi, Colonna Maxwell B, Poplawski Andrzej B, Arno Gavin, Hallman Jenna, Underwood Christina, Basu Amrita, Pollard Laura, Weiss Ryan J, Steet Richard, Flanagan-Steet Heather