Single-copy expression of an amyotrophic lateral sclerosis-linked TDP-43 mutation (M337V) in BAC transgenic mice leads to altered stress granule dynamics and progressive motor dysfunction
BAC 转基因小鼠中肌萎缩侧索硬化症相关 TDP-43 突变 (M337V) 的单拷贝表达导致应激颗粒动力学改变和进行性运动功能障碍
期刊:Neurobiology of Disease
影响因子:5.1
doi:10.1016/j.nbd.2018.09.024
David Gordon, Ruxandra Dafinca, Jakub Scaber, Javier Alegre-Abarrategui, Lucy Farrimond, Connor Scott, Daniel Biggs, Louisa Kent, Peter L Oliver, Benjamin Davies, Olaf Ansorge, Richard Wade-Martins, Kevin Talbot