日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

MEK inhibitor mirdametinib promotes fracture healing in osteofibrous dysplasia RASopathy

MEK抑制剂mirdametinib可促进骨纤维发育不良RAS病患者的骨折愈合。

Khalid, Aysha B; Denton, Kristin; Paria, Nandina; Oxendine, Ila; Wassell, Meghan; Cornelia, Reuel; Uppuganti, Sasidhar; Nyman, Jeffry S; Jagadeesh, G Jayashree; Ferreira, Carlos R; Conway, Simon J; Hammer, Robert E; Ritter, John; Nguyen, Mylinh; Podeszwa, David A; Klesse, Laura J; Wise, Carol A; Rios, Jonathan J

Correction to: Granulopoietic Dysregulation in a Patient-Tailored Mouse Model of Barth Syndrome

更正:巴特综合征患者定制小鼠模型中的粒细胞生成失调

Sierra Potchanant, Elizabeth A; Capitano, Maegan L; Edwards, Donna M; Ramdas, Baskar; Cooper, Scott; Ropa, James; Pay, S Louise; Sheth, Aditya; Snider, Paige L; Vernon, Hilary J; Tran, Ngoc-Tung; Kapur, Reuben; Conway, Simon J

BACH2 links β1-adrenergic receptor/β-arrestin1 signaling to MIAT to inhibit cardiac fibroblast activation and cardiomyocyte apoptosis

BACH2 将 β1-肾上腺素能受体/β-arrestin1 信号通路与 MIAT 连接起来,从而抑制心脏成纤维细胞活化和心肌细胞凋亡。

Moukette, Bruno; Teoh, Jian-Peng; Hashmi, Waleed J; Kawaguchi, Satoshi; Aonuma, Tatsuya; Moustapha, Hamedane; Welc, Steven S; Conway, Simon J; Liangpunsakul, Suthat; Yang, Lei; Desai, Ankit A; Kim, Il-Man

Cardiomyocyte-restricted MIAT deletion is sufficient to protect against murine myocardial infarction

心肌细胞特异性MIAT基因敲除足以预防小鼠心肌梗死。

Hayasaka, Taiki; Kawaguchi, Satoshi; Sepúlveda, Marisa N; Teoh, Jian-Peng; Moukette, Bruno; Aonuma, Tatsuya; Madhur, Meena S; Desai, Ankit A; Liangpunsakul, Suthat; Conway, Simon J; Kim, Il-Man

Focused ultrasound-mediated drug delivery of bevacizumab in treating NF2-related schwannomatosis in an animal model.

在动物模型中,利用聚焦超声介导的药物递送贝伐单抗治疗NF2相关神经鞘瘤病。

Spiegel Jennifer L, De Maio Alessandro, Patel Manita V, Ungar Omer J, Lai Carolyn, Truong Tra, Situ Yumai, Clapp D Wade, Conway Simon J, Chen Joseph M, Lin Vincent Y W, Hynynen Kullervo, O'Reilly Meaghan A, Le Trung N

What can ATP content tell us about Barth syndrome muscle phenotypes?

ATP含量能告诉我们巴特综合征肌肉表型的哪些信息?

Brault, Jeffrey J; Conway, Simon J

Deficient Cardiolipin Remodeling Alters Muscle Fiber Composition and Neuromuscular Connectivity in Barth Syndrome

巴特综合征中,心磷脂重塑不足会改变肌肉纤维组成和神经肌肉连接。

Matias, Catalina; Snider, Paige L; Sierra Potchanant, Elizabeth A; Huot, Joshua R; Raghav, Rahul; Chin, Michael T; Conway, Simon J; Brault, Jeffrey J

Fibroblast Smad7 Induction Protects the Remodeling Pressure-Overloaded Heart

成纤维细胞Smad7诱导可保护重塑期压力负荷过重的心脏

Humeres, Claudio; Shinde, Arti V; Tuleta, Izabela; Hernandez, Silvia C; Hanna, Anis; Huang, Shuaibo; Venugopal, Harikrishnan; Aguilan, Jennifer T; Conway, Simon J; Sidoli, Simone; Frangogiannis, Nikolaos G

Divergent Actions of Myofibroblast and Myocyte β(2)-Adrenoceptor in Heart Failure and Fibrotic Remodeling

肌成纤维细胞和肌细胞β(2)-肾上腺素受体在心力衰竭和纤维化重塑中的不同作用

Deng, Bingqing; Zhang, Yu; Zhu, Chaoqun; Wang, Ying; Weatherford, Eric; Xu, Bing; Liu, Xianhui; Conway, Simon J; Abel, E Dale; Xiang, Yang K

SPRR1A is a key downstream effector of MiR-150 during both maladaptive cardiac remodeling in mice and human cardiac fibroblast activation

SPRR1A是miR-150在小鼠心脏异常重塑和人类心脏成纤维细胞活化过程中的关键下游效应因子。

Kawaguchi, Satoshi; Moukette, Bruno; Sepúlveda, Marisa N; Hayasaka, Taiki; Aonuma, Tatsuya; Haskell, Angela K; Mah, Jessica; Liangpunsakul, Suthat; Tang, Yaoliang; Conway, Simon J; Kim, Il-Man