日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Defining RNA oligonucleotides that reverse deleterious phase transitions of RNA-binding proteins with prion-like domains.

确定能够逆转具有朊病毒样结构域的 RNA 结合蛋白的有害相变的 RNA 寡核苷酸。

Guo Lin, Mann Jacob R, Mauna Jocelyn C, Copley Katie E, Wang Hejia, Rubien Jack D, Bergmann Cristian A, Carey Jenny L, Merjane Jessica, Ngo Marilyn, Xu Jiazhen, Odeh Hana M, Lin JiaBei, Lee Bo Lim, Ganser Laura, Robinson Emma, Kim Kevin M, Murthy Anastasia C, Paul Tapas, Portz Bede, Gleixner Amanda M, Diaz Zamia, Smirnov Ashleigh, Padilla George, Lavorando Ellen, Espy Carolann, Shang Yulei, Huang Eric J, Chesi Alessandra, Fawzi Nicolas L, Myong Sua, Donnelly Christopher J, Shorter James

Scouring the human Hsp70 network uncovers diverse chaperone safeguards buffering TDP-43 toxicity.

对人类 Hsp70 网络的深入研究揭示了多种分子伴侣保护机制,可以缓冲 TDP-43 的毒性

Barbieri Edward M, Linsenmeier Miriam, Whiteman Katherine R, Cheng Yan, Braganza Sylvanne, Copley Katie E, Miranda-Castrodad Paola, Lewis Brennen, Villafañe Kevin, Amado Defne A, Davidson Beverly L, Shorter James

Repetitive elements in aging and neurodegeneration

衰老和神经退行性疾病中的重复性因素

Copley, Katie E; Shorter, James

C-terminal frameshift variant of TDP-43 with pronounced aggregation-propensity causes rimmed vacuole myopathy but not ALS/FTD

TDP-43 C 端移码变异体具有显著的聚集倾向,可导致边缘空泡肌病,但不会导致肌萎缩侧索硬化症/额颞叶痴呆。

Ervilha Pereira, Pedro; Schuermans, Nika; Meylemans, Antoon; LeBlanc, Pontus; Versluys, Lauren; Copley, Katie E; Rubien, Jack D; Altheimer, Christopher; Peetermans, Myra; Debackere, Elke; Vanakker, Olivier; Janssens, Sandra; Baets, Jonathan; Verhoeven, Kristof; Lammens, Martin; Symoens, Sofie; De Paepe, Boel; Barmada, Sami J; Shorter, James; De Bleecker, Jan L; Bogaert, Elke; Dermaut, Bart

Defining RNA oligonucleotides that reverse deleterious phase transitions of RNA-binding proteins with prion-like domains

确定能够逆转具有朊病毒样结构域的RNA结合蛋白的有害相变的RNA寡核苷酸

Guo, Lin; Mann, Jacob R; Mauna, Jocelyn C; Copley, Katie E; Wang, Hejia; Rubien, Jack D; Odeh, Hana M; Lin, JiaBei; Lee, Bo Lim; Ganser, Laura; Robinson, Emma; Kim, Kevin M; Murthy, Anastasia C; Paul, Tapas; Portz, Bede; Gleixner, Amanda M; Diaz, Zamia; Carey, Jenny L; Smirnov, Ashleigh; Padilla, George; Lavorando, Ellen; Espy, Carolann; Shang, Yulei; Huang, Eric J; Chesi, Alessandra; Fawzi, Nicolas L; Myong, Sua; Donnelly, Christopher J; Shorter, James