日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

ERS/EULAR clinical practice guidelines for connective tissue disease-associated interstitial lung disease

ERS/EULAR 结缔组织病相关间质性肺疾病临床实践指南

Antoniou, Katerina M; Distler, Oliver; Gheorghiu, Ana-Maria; Moor, Catharina C; Vikse, Jens; Bizymi, Nikoleta; Galetti, Ilaria; Brown, Graham; Bargagli, Elena; Allanore, Yannick; Corte, Tamera J; Dieudé, Philippe; Cottin, Vincent; Fisher, Benjamin A; Fabre, Aurelie; Giles, Jon T; Kreuter, Michael; Lundberg, Ingrid E; Poletti, Venerino; Maurer, Britta; Renzoni, Elisabetta A; Müller-Ladner, Ulf; Strek, Mary E; Sverzellati, Nicola; Studenic, Paul; Mohammed, Jibril; Nagavci, Blin; Stamm, Tanja; Tonia, Thomy; Crestani, Bruno; Hoffmann-Vold, Anna-Maria

Adult male patients with DKC1 mutations present early-onset pulmonary fibrosis and severe prognosis

携带 DKC1 基因突变的成年男性患者会出现早发性肺纤维化,预后不良。

Evrard, Ophélie; Philippot, Quentin; Kannengiesser, Caroline; Debray, Marie Pierre; Guyard, Alice; Fattori, Antonin; Schuller, Armelle; Nunes, Hilario; Montani, David; Bours, Vincent; Cottin, Vincent; Traclet, Julie; Benattia, Amira; Berthoux, Emilie; Daniel, Adrien; Yan-Min, Xu; Lainey, Elodie; Saussereau, Julien; Chelbi Viallon, Malika; Oudin, Claire; Morel, Héléne; Crestani, Bruno; Borie, Raphaël; Ba, Ibrahima

Behavioural changes in exposure patterns after genetic counselling among asymptomatic first-degree relatives of patients with pulmonary fibrosis and carriers of a telomere-related gene variant

遗传咨询后,肺纤维化患者无症状一级亲属和端粒相关基因变异携带者的暴露模式行为发生改变

Sesé, Lucile; Bouvry, Diane; Kannengiesser, Caroline; Wémeau-Stervinou, Lidwine; Jouneau, Stephane; Prevot, Grégoire; Vagnarelli, Stephane; Guérin, Cécile; Lassus, Albane; Crestani, Bruno; Bonniaud, Philippe; Cottin, Vincent; Gueguen, Sonia; Nunes, Hilario; Borie, Raphael

Efficacy and safety of danazol for pulmonary fibrosis or bone-marrow failure associated with telomere-related gene mutation

达那唑治疗与端粒相关基因突变相关的肺纤维化或骨髓衰竭的疗效和安全性

Sicre de Fontbrune, Flore; Jouneau, Stéphane; Cottin, Vincent; Prevot, Grégoire; Nunes, Hilario; Terriou, Louis; Marchand-Adam, Sylvain; Crestani, Bruno; Marcais, Ambroise; Bergeron, Anne; Debray, Marie-Pierre; Plessier, Aurélie; Lainey, Elodie; Ba, Ibrahima; Kannengiesser, Caroline; Desseaux, Kristell; Resche-Rigon, Matthieu; Biard, Lucie; Borie, Raphael

Dominant Form of SFTPB: A New Paradigm

SFTPB 的主要形式:一种新的范式

Louvrier, Camille; Crestani, Bruno; Borie, Raphaël

Impact of A Multidisciplinary Team Discussion for Genetic Lung Fibrosis

多学科团队讨论对遗传性肺纤维化的影响

Franco, Giovanni; Ba, Ibrahima; Nathan, Nadia; Guerin, Cécile; Lassus, Albane; Kannengiesser, Caroline; Froidure, Antoine; Manali, Effrosyni; Bunel, Vincent; Bonniaud, Philippe; Bouvry, Diane; Debray, Marie Pierre; Juge, Pierre Antoine; Epaud, Ralph; Louvrier, Camille; Plessier, Aurélie; de Fontbrune, Flore Sicre; Wémeau-Stervinou, Lidwine; Adam, Sylvain Marchand; Chabrol, Alexandre; Maurac, Arnaud; Savale, Laurent; Montani, David; Raynal, Caroline; Konyukh, Marina; Mageau, Arthur; Crestani, Bruno; Cottin, Vincent; de Becdelièvre, Alix; Borie, Raphaël

Efficacy and safety of CFTR modulators in patients with interstitial lung disease caused by ABCA3 transporter deficiency

CFTR调节剂治疗ABCA3转运蛋白缺乏引起的间质性肺病患者的疗效和安全性

Le Brun, Mathilde; Nathan, Nadia; Louvrier, Camille; Legendre, Marie; Feuillet, Severine; Frija-Masson, Justine; Onanga, Mwetty; Morer, Lise; Debray, Marie-Pierre; Fajac, Isabelle; Burgel, Pierre-Régis; Marchand-Adam, Sylvain; Crestani, Bruno; Borie, Raphaël

The interstitial lung disease patient pathway: from referral to diagnosis

间质性肺病患者诊疗路径:从转诊到诊断

Lough, Graham; Abdulqawi, Rayid; Amanda, Gina; Antoniou, Katerina; Azuma, Arata; Baldi, Milind; Bayoumy, Ahmed; Behr, Jürgen; Bendstrup, Elisabeth; Bouros, Demosthenes; Brown, Kevin; Chaudhuri, Nazia; Corte, Tamera J; Cottin, Vincent; Crestani, Bruno; Flaherty, Kevin R; Glaspole, Ian; Kawano-Dourado, Leticia; Keane, Michael P; Kolb, Martin; Martinez, Fernando J; Molina-Molina, Maria; Ojanguren, Iñigo; Pearmain, Laurence; Raghu, Ganesh; Rottoli, Paola; Stanel, Stefan C; Tabaj, Gabriela; Vancheri, Carlo; Varela, Brenda; Wang, Bonnie; Wells, Athol; Rivera-Ortega, Pilar

Uncovering an antifibrotic Prrx1-lineage mesenchymal cell subpopulation in fibrotic lungs

在纤维化肺中发现抗纤维化 Prrx1 谱系间充质细胞亚群

Homps-Legrand, Meline; Jaillet, Madeleine; Deneuville, Lou; Gautier, Gregory; Crestani, Bruno; Mailleux, Arnaud A

Pulmonary Hypertension Drives Prognosis in Idiopathic Pulmonary Fibrosis: Insights from the European IPF Registry

肺动脉高压影响特发性肺纤维化的预后:来自欧洲特发性肺纤维化注册研究的启示

Guenther, Andreas; Tello, Silke; Schoppe, Marc Carre; Pons-Kuehnemann, Joern; Seeger, Werner; Stiben, Johannes; Tello, Khodr; Molina Molina, Maria; Vancheri, Carlo; Crestani, Bruno; Krauss, Ekaterina