日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A Pilot Study of Bone Marrow Transplantation in a GALT-Null Rat Model of Classic Galactosemia

在经典半乳糖血症的GALT基因敲除大鼠模型中开展骨髓移植的初步研究

Rasmussen, Shauna A; Seemiller, Madelyn M; Smith, Ingrid; Wilson, Madeleine; Daenzer, Jennifer M I; Wiggins, Keenan; Fridovich-Keil, Judith L

AgBioDatabase Finder: an online tool to help researchers find and submit agricultural genomic, genetic, and breeding data

AgBioDatabase Finder:一个帮助研究人员查找和提交农业基因组、遗传和育种数据的在线工具

Cabugos, Leyla; Buble, Katheryn; Daenzer, Jenna; Jung, Sook; Main, Dorrie; Marrano, Annarita; Molik, David; Raciti, Daniela; Wright, Adam; Yook, Karen; Reiser, Leonore

Restoring galactose metabolism without restoring GALT rescues both compromised survival in larvae and an adult climbing deficit in a GALT-null D. Melanogaster model of classic galactosemia

在经典半乳糖血症的GALT基因敲除果蝇模型中,恢复半乳糖代谢而不恢复GALT功能,既能挽救幼虫存活率受损的问题,又能改善成虫攀爬能力缺陷。

Daenzer, Jennifer M I; Druss, Jared J; Fridovich-Keil, Judith L

Juvenile survival of little owls decreases with snow cover

积雪覆盖会降低小猫头鹰幼鸟的存活率。

Perrig, Marco; Oppel, Steffen; Tschumi, Matthias; Keil, Herbert; Naef-Daenzer, Beat; Grüebler, Martin U

Neonatal GALT gene replacement offers metabolic and phenotypic correction through early adulthood in a rat model of classic galactosemia

新生儿 GALT 基因置换可为经典半乳糖血症大鼠模型提供代谢和表型矫正,直至成年早期

Jennifer M I Daenzer, Shauna A Rasmussen, Sneh Patel, James McKenna 3rd, Judith L Fridovich-Keil

Reduced habitat quality increases intrinsic but not ecological costs of reproduction

栖息地质量下降会增加繁殖的内在成本,但不会增加繁殖的生态成本。

Michel, Vanja T; Tschumi, Matthias; Naef-Daenzer, Beat; Keil, Herbert; Grüebler, Martin U

A pilot study of neonatal GALT gene replacement using AAV9 dramatically lowers galactose metabolites in blood, liver, and brain and minimizes cataracts in GALT-null rat pups

一项使用 AAV9 进行新生儿 GALT 基因替换的初步研究显著降低了血液、肝脏和脑中的半乳糖代谢物,并最大限度地减少了 GALT 基因缺失的幼鼠的白内障

Shauna A Rasmussen, Jennifer M I Daenzer, Judith L Fridovich-Keil

A galactose-1-phosphate uridylyltransferase-null rat model of classic galactosemia mimics relevant patient outcomes and reveals tissue-specific and longitudinal differences in galactose metabolism

经典半乳糖血症的半乳糖-1-磷酸尿苷酰转移酶敲除大鼠模型能够模拟相关患者的临床结局,并揭示半乳糖代谢的组织特异性和纵向差异。

Rasmussen, Shauna A; Daenzer, Jennifer M I; MacWilliams, Jessica A; Head, S Taylor; Williams, Martine B; Geurts, Aron M; Schroeder, Jason P; Weinshenker, David; Fridovich-Keil, Judith L

Political borders impact associations between habitat suitability predictions and resource availability

政治边界会影响栖息地适宜性预测与资源可用性之间的关联。

Tschumi, Matthias; Scherler, Patrick; Fattebert, Julien; Naef-Daenzer, Beat; Grüebler, Martin U

Experimentally disentangling intrinsic and extrinsic drivers of natal dispersal in a nocturnal raptor

通过实验厘清夜行猛禽出生地扩散的内在和外在驱动因素

Fattebert, Julien; Perrig, Marco; Naef-Daenzer, Beat; Grüebler, Martin U