日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The Optically Guided and Pre-assembled Implantation Cranial Window Reveals Cortical Spatial Representations during Navigation

光学引导预组装植入式颅窗揭示了导航过程中的皮层空间表征

Zhao, Weihao; Gao, Lin; Wu, Yu; Xiao, Guihua; Li, Angran; Wang, Mingrui; Liu, Hongyu; Yang, Jinyuan; Jin, Dongyue; Zhang, Yuanlong; Yuan, Yongyi; Dai, Pu

Single Administration of AAV-mAtp6v1b2 Gene Therapy Rescues Hearing and Vestibular Disorders Caused by Atp6v1b2-Induced Lysosomal Dysfunction in Hair Cells.

单次注射 AAV-mAtp6v1b2 基因疗法可挽救由 Atp6v1b2 诱导的毛细胞溶酶体功能障碍引起的听力和前庭疾病

Wei Gege, Qiu Shiwei, Gao Xue, Zheng Lu, Chen Yijin, Ma Ying, Feng Haifeng, Yang Jinyuan, Dong Guojie, Nie Huiyi, Zhao Weihao, Li Xiaoge, Wang Guangqin, Xiong Wei, Dai Pu, Yuan Yongyi

Novel autosomal dominant syndromic hearing loss caused by COL4A2 -related basement membrane dysfunction of cochlear capillaries and microcirculation disturbance

一种由COL4A2相关基底膜功能障碍引起的耳蜗毛细血管和微循环紊乱导致的新型常染色体显性遗传综合征性听力损失。

Yang, Jinyuan; Ma, Ying; Gao, Xue; Qiu, Shiwei; Li, Xiaoge; Zhao, Weihao; Chen, Yijin; Dong, Guojie; Lin, Rongfeng; Wei, Gege; Nie, Huiyi; Feng, Haifeng; Gu, Xiaoning; Gao, Bo; Dai, Pu; Yuan, Yongyi

Reevaluation of Enlarged Vestibular Aqueduct

对扩大的前庭导水管的重新评估

Huang, Shasha; Gao, Xue; Jiang, Yi; Guo, Chang; Li, Xiaoge; Wang, Guojian; Han, Mingyu; Zhang, Xin; Yang, Suyan; Wang, Qiuquan; Zhao, Chaoyue; Yang, Jinyuan; Kang, Dongyang; Dai, Pu; Yuan, Yongyi

Functional characterization of MFSD3 in auditory system and zebrafish embryogenesis

MFSD3在听觉系统和斑马鱼胚胎发育中的功能表征

Ma, Ying; Qiu, Shi-Wei; Wang, Wei-Qian; Feng, Hai-Feng; Zheng, Lu; Wei, Ge-Ge; Nie, Hui-Yi; Yang, Jin-Yuan; Chen, Yi-Jin; Dai, Pu; Gao, Xue; Yuan, Yong-Yi

A cohort study of neonatal hearing testing and genetic screening for variants associated with susceptibility to aminoglycoside antibiotic-induced hearing loss in Beijing, China

中国北京一项针对新生儿听力测试和与氨基糖苷类抗生素诱发听力损失易感性相关的基因变异筛查的队列研究

Duan, Hong; Huang, Sha-Sha; Zhu, Feng-Jiao; Wang, Guo-Jian; Gao, Xue; Yuan, Yong-Yi; Dai, Pu

[Perioperative safety assessment and complications follow-up of simultaneous bilateral cochlear implantation in young infants]

[婴幼儿同时双侧人工耳蜗植入术的围手术期安全性评估及并发症随访]

Li, Xiaoge; Dai, Pu; Yuan, Yongyi

[Analysis of complex cochlear implantation electrode repositioning strategies based on intraoperative CT]

[基于术中CT的复杂人工耳蜗植入电极重新定位策略分析]

Zhao, Chaoyue; Gao, Bo; Zhang, Dejun; Zheng, Lu; Wang, Qiuquan; Dai, Pu

Mitochondrial tRNA(Ser(UCN)) mutations associated non-syndromic sensorineural hearing loss in Chinese families

中国家族中线粒体tRNA(Ser(UCN))突变与非综合征性感觉神经性听力损失相关

Zhang, Dejun; Wu, Jie; Yuan, Yongyi; Li, Xiaohong; Gao, Xue; Kang, Dongyang; Zhang, Xin; Huang, Sha-Sha; Dai, Pu

The natural history and genotype-phenotype correlations of TMPRSS3 hearing loss: an international, multi-center, cohort analysis

TMPRSS3 听力损失的自然史和基因型-表型相关性:一项国际多中心队列分析

Colbert, Brett M; Lanting, Cris; Smeal, Molly; Blanton, Susan; Dykxhoorn, Derek M; Tang, Pei-Ciao; Getchell, Richard L; Velde, Hedwig; Fehrmann, Mirthe; Thorpe, Ryan; Chapagain, Prem; Elkhaligy, Heidy; Kremer, Hannie; Yntema, Helger; Haer-Wigman, Lonneke; Redfield, Shelby; Sun, Tieqi; Bruijn, Saskia; Plomp, Astrid; Goderie, Thadé; van de Kamp, Jiddeke; Free, Rolien H; Wassink-Ruiter, Jolien Klein; Widdershoven, Josine; Vanhoutte, Els; Rotteveel, Liselotte; Kriek, Marjolein; van Dooren, Marieke; Hoefsloot, Lies; de Gier, Heriette H W; Schaefer, Amanda; Kolbe, Diana; Azaiez, Hela; Rabie, Grace; Aburayyan, Armal; Kawas, Mariana; Kanaan, Moien; Holder, Jourdan; Usami, Shin-Ichi; Chen, Zhengyi; Dai, Pu; Holt, Jeffrey; Nelson, Rick; Choi, Byung Yoon; Shearer, Eliot; Smith, Richard J H; Pennings, Ronald; Liu, Xue Zhong