日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Allosteric Modulation of Pathological Ataxin-3 Aggregation: A Path to Spinocerebellar Ataxia Type-3 Therapies

病理性共济失调蛋白 3 聚集的变构调节:脊髓小脑共济失调 3 型治疗的途径

Alexandra Silva, Sara Duarte-Silva, Pedro M Martins, Beatriz Rodrigues, Débora Serrenho, Daniela Vilasboas-Campos, Andreia Teixeira-Castro, Julio Vieyto-Nuñez, Joel Mieres-Perez, Francisco Figueiredo, Joana Fraga, James Noble, Carter Lantz, Niki Sepanj, Daniela Monteiro-Fernandes, Sara Guerreiro, An

Glucocorticoid receptor-dependent therapeutic efficacy of tauroursodeoxycholic acid in preclinical models of spinocerebellar ataxia type 3

牛磺熊去氧胆酸对脊髓小脑性共济失调 3 型临床前模型的糖皮质激素受体依赖性治疗效果

Sara Duarte-Silva, Jorge Diogo Da Silva, Daniela Monteiro-Fernandes, Marta Daniela Costa, Andreia Neves-Carvalho, Mafalda Raposo, Carina Soares-Cunha, Joana S Correia, Gonçalo Nogueira-Goncalves, Henrique S Fernandes, Stephanie Oliveira, Ana Rita Ferreira-Fernandes, Fernando Rodrigues, Joana Pereira

Microglial Depletion Has No Impact on Disease Progression in a Mouse Model of Machado-Joseph Disease

小胶质细胞耗竭对马查多-约瑟夫病小鼠模型的病情进展没有影响

Ana Bela Campos, Sara Duarte-Silva, Bruno Fernandes, Bárbara Coimbra, Jonas Campos, Daniela Monteiro-Fernandes, Andreia Teixeira-Castro, António Francisco Ambrósio, Patrícia Maciel

Cerebellar neuronal dysfunction accompanies early motor symptoms in spinocerebellar ataxia type 3

脊髓小脑性共济失调 3 型的早期运动症状伴随小脑神经元功能障碍

Kristin Mayoral-Palarz, Andreia Neves-Carvalho, Sara Duarte-Silva, Daniela Monteiro-Fernandes, Patrícia Maciel, Kamran Khodakhah

Profiling Microglia in a Mouse Model of Machado-Joseph Disease

对马查多-约瑟夫病小鼠模型中的小胶质细胞进行分析

Ana Bela Campos, Sara Duarte-Silva, Bruno Fernandes, Sofia Pereira das Neves, Fernanda Marques, Andreia Teixeira-Castro, Andreia Neves-Carvalho, Daniela Monteiro-Fernandes, Camila Cabral Portugal, Renato Socodato, Teresa Summavielle, António Francisco Ambrósio, João Bettencourt Relvas, Patrícia Maci

Unilateral Intrastriatal 6-Hydroxydopamine Lesion in Mice: A Closer Look into Non-Motor Phenotype and Glial Response

小鼠单侧纹状体内 6-羟基多巴胺损伤:进一步研究非运动表型和神经胶质反应

Bárbara Mendes-Pinheiro, Carina Soares-Cunha, Ana Marote, Eduardo Loureiro-Campos, Jonas Campos, Sandra Barata-Antunes, Daniela Monteiro-Fernandes, Diogo Santos, Sara Duarte-Silva, Luísa Pinto, António José Salgado