日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A new severe congenital neutropenia syndrome associated with autosomal recessive COPZ1 mutations

与常染色体隐性COPZ1基因突变相关的新型严重先天性中性粒细胞减少症

Borbaran Bravo, Natalia; Deordieva, Ekaterina; Doll, Larissa; ElGamacy, Mohammad; Dannenmann, Benjamin; Azevedo, Joana; Iannuzzo, Alberto; Delafontaine, Selket; Lehners, Moritz; Kolodziej, Marius; Hernandez Alvarez, Birte; Hellmuth, Anna-Sophia; Ritter, Malte; Findik, Betül; Zakharova, Viktoria; Bräuning, Sandro; Kandabarau, Sergey; Lengerke, Claudia; Feil, Robert; Meyts, Isabelle; Delon, Jérôme; Templin, Markus; Sturm, Marc; Rieß, Olaf; Zeidler, Cornelia; Welte, Karl; Shcherbina, Anna; Klimiankou, Maksim; Skokowa, Julia

Flavopiridol restores granulopoiesis in experimental models of severe congenital neutropenia.

Flavopiridol 可恢复严重先天性中性粒细胞减少症实验模型中的粒细胞生成

Nasri Masoud, Dannenmann Benjamin, Doll Larissa, Findik Betül, Bernhard Franka, Kandabarau Sergey, Klimiankou Maksim, Gawaz Meinrad, Lengerke Claudia, Zeidler Cornelia, Welte Karl, Skokowa Julia

Targeted inhibition of ELANE expression using adenine base editing to treat severe congenital neutropenia.

利用腺嘌呤碱基编辑靶向抑制 ELANE 表达来治疗重度先天性中性粒细胞减少症。

Findik Betül, Dannenmann Benjamin, Bernhard Franka, Kaufmann Masako Monika, Ammann Sandra, Kandabarau Sergey, Klimiankou Maksim, Mauch Fabian, Münzer Patrick, Borst Oliver, Klefenz Isabel, Steinemann Doris, Lengerke Claudia, Zeidler Cornelia, Cathomen Toni, Welte Karl, Nasri Masoud, Skokowa Julia

Correction: NAMPT/SIRT2-mediated inhibition of the p53-p21 signaling pathway is indispensable for maintenance and hematopoietic differentiation of human iPS cells

更正:NAMPT/SIRT2介导的p53-p21信号通路抑制对于维持人类iPS细胞的造血分化至关重要。

Xu, Yun; Nasri, Masoud; Dannenmann, Benjamin; Mir, Perihan; Zahabi, Azadeh; Welte, Karl; Morishima, Tatsuya; Skokowa, Julia

P938: CARFILZOMIB-LENALIDOMIDE-DEXAMETHASONE CONSOLIDATION IN MYELOMA PATIENTS WITH A POSITIVE FDG PET/CT AFTER UPFRONT AUTOLOGOUS STEM CELL TRANSPLANTATION: A PHASE II STUDY (CONPET)

P938:卡非佐米-来那度胺-地塞米松巩固治疗在接受自体干细胞移植后FDG PET/CT检查结果呈阳性的多发性骨髓瘤患者中的应用:一项II期研究(CONPET)

Tsuyama, Naoko; Sakamoto, Kana; Sakata, Seiji; Dobashi, Akito; Takeuchi, Kengo; Sánchez-Redondo, Noemí Álvarez; Martin, Alejandro; Dorado, Sara; Rufián, Laura; Rodriguez, Margarita; Heredia, Yanira; Robles, Maria Calbacho; Romero, Maria Teresa Cedena; Martinez-Lopez, Joaquín; Barrio, Santiago; Diaz, Rosa Ayala; Nasri, Masoud; Ulrich Ritter, Malte; Mir, Perihan; Dannenmann, Benjamin; Monika Kaufmann, Masako; Xu, Yun; Borbaran-Bravo, Natalia; Klimiankou, Maksim; Lengerke, Claudia; Zeidler, Cornelia; Cathomen, Toni; Welte, Karl; Skokowa, Julia; Liang, MI; Yao, Wei-LI; Lyv, Zhong-Shi; Tang, Shu-Qian; Xing, Tong; Zhang, Yuan-Yuan; Chen, Yu-Hong; Wang, Yu; Xu, Lan-Ping; Zhang, Xiao-Hui; Huang, Xiao-Jun; Kong, Yuan; Nørgaard, J N; Abildgaard, N; Lysén, A; Tsykunova, G; Vangsted, A J; Joao, C; Remen, N; Osnes, L; Connelly, J P; Revheim, M-E R; Schjesvold, F

Simultaneous quantification of DNA damage and mitochondrial copy number by long-run DNA-damage quantification (LORD-Q)

利用长程DNA损伤定量(LORD-Q)技术同时定量DNA损伤和线粒体拷贝数

Dannenmann, Benjamin; Lehle, Simon; Lorscheid, Sebastian; Huber, Stephan M; Essmann, Frank; Schulze-Osthoff, Klaus

Genome surveillance in pluripotent stem cells: Low apoptosis threshold and efficient antioxidant defense

多能干细胞基因组监控:低凋亡阈值和高效的抗氧化防御

Dannenmann, Benjamin; Lehle, Simon; Essmann, Frank; Schulze-Osthoff, Klaus