日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Lupus-like autoimmunity and increased interferon response in patients with STAT3-deficient hyper-IgE syndrome

STAT3缺陷型高IgE综合征患者的狼疮样自身免疫和干扰素反应增强

Goel, Rishi R; Nakabo, Shuichiro; Dizon, Brian L P; Urban, Amanda; Waldman, Meryl; Howard, Lillian; Darnell, Dirk; Buhaya, Munir; Carmona-Rivera, Carmelo; Hasni, Sarfaraz; Kaplan, Mariana J; Freeman, Alexandra F; Gupta, Sarthak

Cryptosporidium infection in dedicator of cytokinesis 8 (DOCK 8) deficiency

隐孢子虫感染与胞质分裂调节因子 8 (DOCK 8) 缺陷有关

Ben Yakov, Gil; Sharma, Disha; Cho, Min H; Shah, Nirali N; Hickstein, Dennis; Urban, Amanda; Darnell, Dirk; Kapuria, Devika; Marko, Jamie; Kleiner, David E; Hadigan, Colleen M; Danielson, Jeffrey; Ham, Hyoungjun; Vittal, Anusha; Su, Helen C; Freeman, Alexandra F; Heller, Theo

Lymphocyte-driven regional immunopathology in pneumonitis caused by impaired central immune tolerance

中枢免疫耐受受损引起的肺炎中淋巴细胞驱动的区域性免疫病理

Ferré, Elise M N; Break, Timothy J; Burbelo, Peter D; Allgäuer, Michael; Kleiner, David E; Jin, Dakai; Xu, Ziyue; Folio, Les R; Mollura, Daniel J; Swamydas, Muthulekha; Gu, Wenjuan; Hunsberger, Sally; Lee, Chyi-Chia R; Bondici, Anamaria; Hoffman, Kevin W; Lim, Jean K; Dobbs, Kerry; Niemela, Julie E; Fleisher, Thomas A; Hsu, Amy P; Snow, Laquita N; Darnell, Dirk N; Ojaimi, Samar; Cooper, Megan A; Bozzola, Martin; Kleiner, Gary I; Martinez, Juan C; Deterding, Robin R; Kuhns, Douglas B; Heller, Theo; Winer, Karen K; Rajan, Arun; Holland, Steven M; Notarangelo, Luigi D; Fennelly, Kevin P; Olivier, Kenneth N; Lionakis, Michail S

First-in-human topical microbiome transplantation with Roseomonas mucosa for atopic dermatitis

首次在人体中进行局部微生物组移植,采用粘膜玫瑰单胞菌治疗特应性皮炎

Myles, Ian A; Earland, Noah J; Anderson, Erik D; Moore, Ian N; Kieh, Mark D; Williams, Kelli W; Saleem, Arhum; Fontecilla, Natalia M; Welch, Pamela A; Darnell, Dirk A; Barnhart, Lisa A; Sun, Ashleigh A; Uzel, Gulbu; Datta, Sandip K

Progressive Multifocal Leukoencephalopathy in Primary Immune Deficiencies: Stat1 Gain of Function and Review of the Literature

原发性免疫缺陷中的进行性多灶性白质脑病:Stat1 功能获得及文献综述

Zerbe, Christa S; Marciano, Beatriz E; Katial, Rohit K; Santos, Carah B; Adamo, Nick; Hsu, Amy P; Hanks, Mary E; Darnell, Dirk N; Quezado, Martha M; Frein, Cathleen; Barnhart, Lisa A; Anderson, Victoria L; Uzel, Gulbu; Freeman, Alexandra F; Lisco, Andrea; Nath, Avindra; Major, Eugene O; Sampaio, Elizabeth P; Holland, Steven M

Common severe infections in chronic granulomatous disease

慢性肉芽肿病中常见的严重感染

Marciano, Beatriz E; Spalding, Christine; Fitzgerald, Alan; Mann, Daphne; Brown, Thomas; Osgood, Sharon; Yockey, Lynne; Darnell, Dirk N; Barnhart, Lisa; Daub, Janine; Boris, Lisa; Rump, Amy P; Anderson, Victoria L; Haney, Carissa; Kuhns, Douglas B; Rosenzweig, Sergio D; Kelly, Corin; Zelazny, Adrian; Mason, Tamika; DeRavin, Suk See; Kang, Elizabeth; Gallin, John I; Malech, Harry L; Olivier, Kenneth N; Uzel, Gulbu; Freeman, Alexandra F; Heller, Theo; Zerbe, Christa S; Holland, Steven M

Bone density and fractures in autosomal dominant hyper IgE syndrome

常染色体显性高IgE综合征的骨密度和骨折

Sowerwine, Kathryn J; Shaw, Pamela A; Gu, Wenjuan; Ling, Jennifer C; Collins, Michael T; Darnell, Dirk N; Anderson, Victoria L; Davis, Joie; Hsu, Amy; Welch, Pamela; Puck, Jennifer M; Holland, Steven M; Freeman, Alexandra F

Neurobehavioral profiles in individuals with hyperimmunoglobulin E Syndrome (HIES) and brain white matter hyperintensities

高免疫球蛋白E综合征(HIES)伴脑白质高信号的个体的神经行为特征

Martin, Staci; Wolters, Pamela; Billings, Nia; Toledo-Tamula, Mary Anne; Hammoud, Dima A; Welch, Pamela; Darnell, Dirk; Holland, Steven M; Freeman, Alexandra F

Pulmonary nontuberculous mycobacterial disease: prospective study of a distinct preexisting syndrome.

肺部非结核分枝杆菌病:一项针对特定既有综合征的前瞻性研究

Kim Richard D, Greenberg David E, Ehrmantraut Mary E, Guide Shireen V, Ding Li, Shea Yvonne, Brown Margaret R, Chernick Milica, Steagall Wendy K, Glasgow Connie G, Lin JingPing, Jolley Clara, Sorbara Lynn, Raffeld Mark, Hill Suvimol, Avila Nilo, Sachdev Vandana, Barnhart Lisa A, Anderson Victoria L, Claypool Reginald, Hilligoss Dianne M, Garofalo Mary, Fitzgerald Alan, Anaya-O'Brien Sandra, Darnell Dirk, DeCastro Rosamma, Menning Heather M, Ricklefs Stacy M, Porcella Stephen F, Olivier Kenneth N, Moss Joel, Holland Steven M