日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Accurate Quantification of Mutant and Wild-Type polyQ Proteins Using Simple Western Capillary Immunoassays.

利用简单的蛋白质毛细管免疫测定法对突变型和野生型polyQ蛋白进行精确定量

Röttgering Bas, Testerink Janwillem, Weij Rudie, Beekman Chantal, Datson Nicole

Correction: Use of capillary Western immunoassay (Wes) for quantification of dystrophin levels in skeletal muscle of healthy controls and individuals with Becker and Duchenne muscular dystrophy

更正:使用毛细管Western免疫测定法(Wes)定量健康对照组以及贝克尔型和杜氏肌营养不良症患者骨骼肌中的肌营养不良蛋白水平

Beekman, Chantal; Janson, Anneke A; Baghat, Aabed; van Deutekom, Judith C; Datson, Nicole A

High Levels of Mutant Huntingtin Protein in Tear Fluid From Huntington's Disease Gene Expansion Carriers

亨廷顿病基因扩增携带者泪液中突变亨廷顿蛋白含量高

Gijs, Marlies; Jorna, Nynke; Datson, Nicole; Beekman, Chantal; Dansokho, Cira; Weiss, Alexander; Linden, David E J; Oosterloo, Mayke

Report of a TREAT-NMD/World Duchenne Organisation Meeting on Dystrophin Quantification Methodology

TREAT-NMD/世界杜氏肌营养不良症组织关于肌营养不良蛋白定量方法学的会议报告

Aartsma-Rus, Annemieke; Morgan, Jennifer; Lonkar, Pallavi; Neubert, Hendrik; Owens, Jane; Binks, Michael; Montolio, Marisol; Phadke, Rahul; Datson, Nicole; Van Deutekom, Judith; Morris, Glenn E; Rao, V Ashutosh; Hoffman, Eric P; Muntoni, Francesco; Arechavala-Gomeza, Virginia

Intracellular Distribution and Nuclear Activity of Antisense Oligonucleotides After Unassisted Uptake in Myoblasts and Differentiated Myotubes In Vitro

体外肌母细胞和分化肌管细胞中反义寡核苷酸在非辅助摄取后的细胞内分布和核活性

González-Barriga, Anchel; Nillessen, Bram; Kranzen, Julia; van Kessel, Ingeborg D G; Croes, Huib J E; Aguilera, Begoña; de Visser, Peter C; Datson, Nicole A; Mulders, Susan A M; van Deutekom, Judith C T; Wieringa, Bé; Wansink, Derick G

Stress and corticosteroids regulate rat hippocampal mitochondrial DNA gene expression via the glucocorticoid receptor

应激和皮质类固醇通过糖皮质激素受体调节大鼠海马线粒体DNA基因表达。

Hunter, Richard G; Seligsohn, Ma'ayan; Rubin, Todd G; Griffiths, Brian B; Ozdemir, Yildirim; Pfaff, Donald W; Datson, Nicole A; McEwen, Bruce S

Genome-wide coexpression of steroid receptors in the mouse brain: Identifying signaling pathways and functionally coordinated regions

小鼠脑内类固醇受体的全基因组共表达:信号通路和功能协调区域的鉴定

Mahfouz, Ahmed; Lelieveldt, Boudewijn P F; Grefhorst, Aldo; van Weert, Lisa T C M; Mol, Isabel M; Sips, Hetty C M; van den Heuvel, José K; Datson, Nicole A; Visser, Jenny A; Reinders, Marcel J T; Meijer, Onno C

Digital Droplet PCR for the Absolute Quantification of Exon Skipping Induced by Antisense Oligonucleotides in (Pre-)Clinical Development for Duchenne Muscular Dystrophy

数字液滴PCR技术用于绝对定量杜氏肌营养不良症(临床前)开发中反义寡核苷酸诱导的外显子跳跃

Verheul, Ruurd C; van Deutekom, Judith C T; Datson, Nicole A

Epigenetic mechanisms in migraine: a promising avenue?

偏头痛的表观遗传机制:一条充满希望的研究途径?

Eising, Else; A Datson, Nicole; van den Maagdenberg, Arn M J M; Ferrari, Michel D

Antisense-mediated isoform switching of steroid receptor coactivator-1 in the central nucleus of the amygdala of the mouse brain

小鼠脑杏仁核中央核中类固醇受体共激活因子-1的反义介导异构体转换

Zalachoras, Ioannis; Grootaers, Gwendolynn; van Weert, Lisa T C M; Aubert, Yves; de Kreij, Suzanne R; Datson, Nicole A; van Roon-Mom, Willeke M C; Aartsma-Rus, Annemieke; Meijer, Onno C