日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Excessive IL-10 and IL-18 trigger hemophagocytic lymphohistiocytosis-like hyperinflammation and enhanced myelopoiesis

IL-10 和 IL-18 过量会引发噬血细胞性淋巴组织细胞增生症样过度炎症反应和髓系造血增强。

Yuting Tang ,Qian Xu ,Hui Luo ,Xiaomei Yan ,Gaoxiang Wang ,Liang Hu ,Jin Jin ,David P Witte ,Rebecca A Marsh ,Liang Huang ,Gang Huang ,Jianfeng Zhou

Inherited DNA Repair Defects Disrupt the Structure and Function of Human Skin

遗传性 DNA 修复缺陷破坏人类皮肤的结构和功能

Sonya Ruiz-Torres, Marion G Brusadelli, David P Witte, Kathryn A Wikenheiser-Brokamp, Sharon Sauter, Adam S Nelson, Mathieu Sertorio, Timothy M Chlon, Adam Lane, Parinda A Mehta, Kasiani C Myers, Mary C Bedard, Bidisha Pal, Dorothy M Supp, Paul F Lambert, Kakajan Komurov, Melinda Butsch Kovacic, Ste

Pathobiological Pseudohypoxia as a Putative Mechanism Underlying Myelodysplastic Syndromes

病理性假性缺氧作为骨髓增生异常综合征的潜在机制

Yoshihiro Hayashi # ,Yue Zhang # ,Asumi Yokota # ,Xiaomei Yan ,Jinqin Liu ,Kwangmin Choi ,Bing Li ,Goro Sashida ,Yanyan Peng ,Zefeng Xu ,Rui Huang ,Lulu Zhang ,George M Freudiger ,Jingya Wang ,Yunzhu Dong ,Yile Zhou ,Jieyu Wang ,Lingyun Wu ,Jiachen Bu ,Aili Chen ,Xinghui Zhao ,Xiujuan Sun ,Kashish Chetal ,Andre Olsson ,Miki Watanabe ,Lindsey E Romick-Rosendale ,Hironori Harada ,Lee-Yung Shih ,William Tse ,James P Bridges ,Michael A Caligiuri ,Taosheng Huang ,Yi Zheng ,David P Witte ,Qian-Fei Wang ,Cheng-Kui Qu ,Nathan Salomonis ,H Leighton Grimes ,Stephen D Nimer ,Zhijian Xiao ,Gang Huang

Tissue-specific effects of saposin A and saposin B on glycosphingolipid degradation in mutant mice

Saposin A 和 Saposin B 对突变小鼠鞘糖脂降解的组织特异性影响

Ying Sun, Matt Zamzow, Huimin Ran, Wujuan Zhang, Brian Quinn, Sonya Barnes, David P Witte, Kenneth D R Setchell, Michael T Williams, Charles V Vorhees, Gregory A Grabowski

Neuronopathic Gaucher disease in the mouse: viable combined selective saposin C deficiency and mutant glucocerebrosidase (V394L) mice with glucosylsphingosine and glucosylceramide accumulation and progressive neurological deficits

小鼠神经性戈谢病:选择性鞘氨醇 C 缺乏症和突变型葡萄糖脑苷脂酶 (V394L) 小鼠存活,并伴有葡萄糖鞘氨醇和葡萄糖神经酰胺蓄积以及进行性神经功能缺损

Ying Sun, Benjamin Liou, Huimin Ran, Matthew R Skelton, Michael T Williams, Charles V Vorhees, Kazuyuki Kitatani, Yusuf A Hannun, David P Witte, You-Hai Xu, Gregory A Grabowski

Neurological deficits and glycosphingolipid accumulation in saposin B deficient mice

鞘脂蛋白 B 缺乏小鼠的神经功能障碍和鞘糖脂积累

Ying Sun, David P Witte, Huimin Ran, Matt Zamzow, Sonya Barnes, Hua Cheng, Xianlin Han, Michael T Williams, Matthew R Skelton, Charles V Vorhees, Gregory A Grabowski