日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A novel human fetal lung-derived alveolar organoid model reveals mechanisms of surfactant protein C maturation relevant to interstitial lung disease

一种新型的人类胎肺来源的肺泡类器官模型揭示了与间质性肺疾病相关的表面活性蛋白C成熟的机制。

Lim, Kyungtae; Rutherford, Eimear N; Delpiano, Livia; He, Peng; Lin, Weimin; Sun, Dawei; Van den Boomen, Dick J H; Edgar, James R; Bang, Jae Hak; Predeus, Alexander; Teichmann, Sarah A; Marioni, John C; Matesic, Lydia E; Lee, Joo-Hyeon; Lehner, Paul J; Marciniak, Stefan J; Rawlins, Emma L; Dickens, Jennifer A

Succinate Chemosensing Induces Cystic Fibrosis Transmembrane Conductance Regulator-dependent Airway Clearance that Is Impaired in Cystic Fibrosis

琥珀酸化学感受诱导囊性纤维化跨膜电导调节因子依赖性气道清除,而囊性纤维化患者的该功能受损

Apablaza, Tábata; Barros-Poblete, Marisol; Delpiano, Livia; Villanueva, Sandra; Guequen, Anita; Tapia-Balladares, Bárbara; Haq, Iram; Tribiños, Felipe; Hernández-Rivas, Sebastián; Verdon, Bernard; Biggart, Matthew G S; Sánchez, Yenniffer; Ward, Christopher; Baxter, B Dnate'; Restrepo, Diego; Cornejo, Isabel; Tarran, Robert; Catalán, Marcelo A; Gray, Michael A; Flores, Carlos A

Extracellular phosphate enhances the function of F508del-CFTR rescued by CFTR correctors

细胞外磷酸盐增强了CFTR矫正剂可挽救的F508del-CFTR的功能。

Saint-Criq, Vinciane; Wang, Yiting; Delpiano, Livia; Lin, JinHeng; Sheppard, David N; Gray, Michael A

The Application of Bicarbonate Recovers the Chemical-Physical Properties of Airway Surface Liquid in Cystic Fibrosis Epithelia Models

碳酸氢盐的应用可恢复囊性纤维化上皮模型中气道表面液的化学物理性质

Ferrera, Loretta; Capurro, Valeria; Delpiano, Livia; Gianotti, Ambra; Moran, Oscar

Small Molecule Anion Carriers Correct Abnormal Airway Surface Liquid Properties in Cystic Fibrosis Airway Epithelia

小分子阴离子载体可纠正囊性纤维化气道上皮细胞异常的气道表面液体特性

Gianotti, Ambra; Capurro, Valeria; Delpiano, Livia; Mielczarek, Marcin; García-Valverde, María; Carreira-Barral, Israel; Ludovico, Alessandra; Fiore, Michele; Baroni, Debora; Moran, Oscar; Quesada, Roberto; Caci, Emanuela

In vitro Methods for the Development and Analysis of Human Primary Airway Epithelia.

人原代呼吸道上皮细胞体外培养及分析方法

Gianotti Ambra, Delpiano Livia, Caci Emanuela