日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Рrospective multicenter study of treatment efficacy, safety, and quality of life in a large cohort of patients with inborn errors of immunity receiving subcutaneous immunoglobulin by the rapid push method

一项前瞻性多中心研究,旨在评估采用快速推注法皮下注射免疫球蛋白治疗先天性免疫缺陷患者的疗效、安全性和生活质量。

Avedova, Asmik; Deripapa, Elena; Rodina, Yulia; Mukhina, Anna; Latysheva, Elena; Yukhacheva, Daria; Burlakov, Vasily; Kan, Nellie; Bogdanova, Daria; Moiseeva, Anna; Kuzmenko, Natalia; Nesterenko, Zoya; Deordieva, Ekaterina; Ogneva, Anna; Bludova, Victoria; Roppelt, Anna; Fomina, Daria; Zinovieva, Natalia; Sevostyanova, Yulia; Kalmeteva, Linara; Prolygina, Dilara; Barycheva, Lyudmila; Selezneva, Olga; Shakhova, Natalya; Laba, Olga; Vlasova, Elena; Gorenkova, Alla; Timofeeva, Elena; Trusova, Olga; Guseva, Marina; Yudina, Natalya; Grevtseva, Evgeniya; Ibisheva, Asya; Bambaeva, Zema; Mashkovskaya, Dina; Isakova, Svetlana; Shakirova, Almazia; Selina, Ekaterina; Shilova, Tatyana; Zubova, Elena; Khabaeva, Iman; Kitova, Ekaterina; Mandzhieva, Anastasia; Starikova, Svetlana; Pavlova, Tatyana; Tyulyakova, Elvira; Levin, Pavel; Grachev, Nikolay; Shcherbina, Anna

Simple Measurement of IgA Predicts Immunity and Mortality in Ataxia-Telangiectasia

简单测量IgA即可预测毛细血管扩张性共济失调患者的免疫力和死亡率

Zielen, Stefan; Duecker, Ruth Pia; Woelke, Sandra; Donath, Helena; Bakhtiar, Sharhzad; Buecker, Aileen; Kreyenberg, Hermann; Huenecke, Sabine; Bader, Peter; Mahlaoui, Nizar; Ehl, Stephan; El-Helou, Sabine M; Pietrucha, Barbara; Plebani, Alessandro; van der Flier, Michiel; van Aerde, Koen; Kilic, Sara S; Reda, Shereen M; Kostyuchenko, Larysa; McDermott, Elizabeth; Galal, Nermeen; Pignata, Claudio; Pérez, Juan Luis Santos; Laws, Hans-Juergen; Niehues, Tim; Kutukculer, Necil; Seidel, Markus G; Marques, Laura; Ciznar, Peter; Edgar, John David M; Soler-Palacín, Pere; von Bernuth, Horst; Krueger, Renate; Meyts, Isabelle; Baumann, Ulrich; Kanariou, Maria; Grimbacher, Bodo; Hauck, Fabian; Graf, Dagmar; Granado, Luis Ignacio Gonzalez; Prader, Seraina; Reisli, Ismail; Slatter, Mary; Rodríguez-Gallego, Carlos; Arkwright, Peter D; Bethune, Claire; Deripapa, Elena; Sharapova, Svetlana O; Lehmberg, Kai; Davies, E Graham; Schuetz, Catharina; Kindle, Gerhard; Schubert, Ralf

Outcomes for Nitazoxanide Treatment in a Case Series of Patients with Primary Immunodeficiencies and Rubella Virus-Associated Granuloma

尼他唑尼治疗原发性免疫缺陷和风疹病毒相关肉芽肿患者的病例系列研究结果

Perelygina, Ludmila; Buchbinder, David; Dorsey, Morna J; Eloit, Marc; Hauck, Fabian; Hautala, Timo; Moshous, Despina; Uriarte, Ignacio; Deripapa, Elena; Icenogle, Joseph; Sullivan, Kathleen E

Rubella Virus-Associated Cutaneous Granulomatous Disease: a Unique Complication in Immune-Deficient Patients, Not Limited to DNA Repair Disorders

风疹病毒相关皮肤肉芽肿病:免疫缺陷患者特有的并发症,不仅限于DNA修复障碍

Buchbinder, David; Hauck, Fabian; Albert, Michael H; Rack, Anita; Bakhtiar, Shahrzad; Shcherbina, Anna; Deripapa, Elena; Sullivan, Kathleen E; Perelygina, Ludmila; Eloit, Marc; Neven, Bénédicte; Pérot, Philippe; Moshous, Despina; Suarez, Félipe; Bodemer, Christine; Bonilla, Francisco A; Vaz, Louise E; Krol, Alfons L; Klein, Christoph; Seppanen, Mikko; Nugent, Diane J; Singh, Jasjit; Ochs, Hans D

Hematopoietic stem cell transplantation in a patient with type 1 mosaic variegated aneuploidy syndrome

造血干细胞移植治疗1型嵌合型杂色非整倍体综合征患者

Laberko, Alexandra; Balashov, Dmitry; Deripapa, Elena; Soldatkina, Olga; Raikina, Elena; Maschan, Alexei; Novichkova, Galina; Shcherbina, Anna

Outcome of hematopoietic cell transplantation for DNA double-strand break repair disorders

造血细胞移植治疗DNA双链断裂修复障碍的疗效

Slack, James; Albert, Michael H; Balashov, Dmitry; Belohradsky, Bernd H; Bertaina, Alice; Bleesing, Jack; Booth, Claire; Buechner, Jochen; Buckley, Rebecca H; Ouachée-Chardin, Marie; Deripapa, Elena; Drabko, Katarzyna; Eapen, Mary; Feuchtinger, Tobias; Finocchi, Andrea; Gaspar, H Bobby; Ghosh, Sujal; Gillio, Alfred; Gonzalez-Granado, Luis I; Grunebaum, Eyal; Güngör, Tayfun; Heilmann, Carsten; Helminen, Merja; Higuchi, Kohei; Imai, Kohsuke; Kalwak, Krzysztof; Kanazawa, Nubuo; Karasu, Gülsün; Kucuk, Zeynep Y; Laberko, Alexandra; Lange, Andrzej; Mahlaoui, Nizar; Meisel, Roland; Moshous, D; Muramatsu, Hideki; Parikh, Suhag; Pasic, Srdjan; Schmid, Irene; Schuetz, Catharina; Schulz, Ansgar; Schultz, Kirk R; Shaw, Peter J; Slatter, Mary A; Sykora, Karl-Walter; Tamura, Shinobu; Taskinen, Mervi; Wawer, Angela; Wolska-Kuśnierz, Beata; Cowan, Morton J; Fischer, Alain; Gennery, Andrew R