Failure of metabolic checkpoint control during late-stage granulopoiesis drives neutropenia in reticular dysgenesis
晚期粒细胞生成过程中代谢检查点控制的失败导致网状细胞发育不全患者出现中性粒细胞减少症。
期刊:Blood
影响因子:23.1
doi:10.1182/blood.2024024123
Wang, Wenqing; Arreola, Martin; Mathews, Thomas; DeVilbiss, Andrew; Zhao, Zhiyu; Martin-Sandoval, Misty; Mohammed, Abdulvasey; Benegiamo, Giorgia; Awani, Avni; Goeminne, Ludger; Dever, Daniel; Nakauchi, Yusuke; Porteus, Matthew H; Pavel-Dinu, Mara; Al-Herz, Waleed; Auwerx, Johan; Morrison, Sean J; Weinacht, Katja G