Immature Acta2(R179C/+) smooth muscle cells cause moyamoya-like cerebrovascular lesions in mice prevented by boosting OXPHOS.
未成熟的 Acta2(R179C/+) 平滑肌细胞会导致小鼠出现类似烟雾病的脑血管病变,而增强 OXPHOS 可以预防这种病变
期刊:Nature Communications
影响因子:15.7
doi:10.1038/s41467-025-61042-3
Kaw Anita, Majumder Suravi, Esparza Pinelo Jose E, Wu Ting, Starosolski Zbigniew, Zhou Zhen, Pedroza Albert J, Duan Xueyan, Kaw Kaveeta, Gonzalez Angie D, Sarkar Ripon, Fischbein Michael P, Lorenzi Philip L, Tan Lin, Martinez Sara A, Mahmud Iqbal, Devkota Laxman, Buja L Maximilian, Taegtmeyer Heinrich, Ghaghada Ketan B, Marrelli Sean P, Kwartler Callie S, Milewicz Dianna M