日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Serum Neurofilaments in Motor Neuron Disease and Their Utility in Differentiating ALS, PMA and PLS.

运动神经元疾病中的血清神经丝及其在区分 ALS、PMA 和 PLS 中的应用

McCluskey Gavin, Morrison Karen E, Donaghy Colette, McConville John, McCarron Mark O, McVerry Ferghal, Duddy William, Duguez Stephanie

Extracellular Vesicles in Amyotrophic Lateral Sclerosis

肌萎缩侧索硬化症中的细胞外囊泡

McCluskey, Gavin; Morrison, Karen E; Donaghy, Colette; Rene, Frederique; Duddy, William; Duguez, Stephanie

The Role of Sphingomyelin and Ceramide in Motor Neuron Diseases

鞘磷脂和神经酰胺在运动神经元疾病中的作用

McCluskey, Gavin; Donaghy, Colette; Morrison, Karen E; McConville, John; Duddy, William; Duguez, Stephanie

"Switchboard" malfunction in motor neuron diseases: Selective pathology of thalamic nuclei in amyotrophic lateral sclerosis and primary lateral sclerosis

运动神经元疾病中的“交换机”功能障碍:肌萎缩侧索硬化症和原发性侧索硬化症中丘脑核团的选择性病理

Chipika, Rangariroyashe H; Finegan, Eoin; Li Hi Shing, Stacey; McKenna, Mary Clare; Christidi, Foteini; Chang, Kai Ming; Doherty, Mark A; Hengeveld, Jennifer C; Vajda, Alice; Pender, Niall; Hutchinson, Siobhan; Donaghy, Colette; McLaughlin, Russell L; Hardiman, Orla; Bede, Peter

A Systematic Review of Genotype-Phenotype Correlation across Cohorts Having Causal Mutations of Different Genes in ALS

对携带不同基因致病突变的ALS患者队列中基因型-表型相关性的系统性综述

Connolly, Owen; Le Gall, Laura; McCluskey, Gavin; Donaghy, Colette G; Duddy, William J; Duguez, Stephanie

Imaging and clinical data indicate considerable disease burden in 'probable' PLS: Patients with UMN symptoms for 2-4 years

影像学和临床数据表明,疑似原发性侧索硬化症(PLS)患者存在相当大的疾病负担:这些患者出现上运动神经元症状2-4年。

Finegan, Eoin; Siah, We Fong; Shing, Stacey Li Hi; Chipika, Rangariroyashe H; Chang, Kai Ming; McKenna, Mary Clare; Doherty, Mark A; Hengeveld, Jennifer C; Vajda, Alice; Donaghy, Colette; Hutchinson, Siobhan; McLaughlin, Russel L; Hardiman, Orla; Bede, Peter

Thalamic, hippocampal and basal ganglia pathology in primary lateral sclerosis and amyotrophic lateral sclerosis: Evidence from quantitative imaging data

原发性侧索硬化症和肌萎缩侧索硬化症的丘脑、海马和基底神经节病理:来自定量成像数据的证据

Finegan, Eoin; Hi Shing, Stacey Li; Chipika, Rangariroyashe H; McKenna, Mary C; Doherty, Mark A; Hengeveld, Jennifer C; Vajda, Alice; Donaghy, Colette; McLaughlin, Russell L; Hutchinson, Siobhan; Hardiman, Orla; Bede, Peter

MRI data confirm the selective involvement of thalamic and amygdalar nuclei in amyotrophic lateral sclerosis and primary lateral sclerosis

MRI 数据证实了丘脑和杏仁核在肌萎缩侧索硬化症和原发性侧索硬化症中的选择性受累。

Chipika, Rangariroyashe H; Siah, We Fong; Shing, Stacey Li Hi; Finegan, Eoin; McKenna, Mary Clare; Christidi, Foteini; Chang, Kai Ming; Karavasilis, Efstratios; Vajda, Alice; Hengeveld, Jennifer C; Doherty, Mark A; Donaghy, Colette; Hutchinson, Siobhan; McLaughlin, Russell L; Hardiman, Orla; Bede, Peter

Progressive brainstem pathology in motor neuron diseases: Imaging data from amyotrophic lateral sclerosis and primary lateral sclerosis

运动神经元疾病中脑干的进行性病变:来自肌萎缩侧索硬化症和原发性侧索硬化症的影像学数据

Bede, Peter; Chipika, Rangariroyashe H; Finegan, Eoin; Li Hi Shing, Stacey; Chang, Kai Ming; Doherty, Mark A; Hengeveld, Jennifer C; Vajda, Alice; Hutchinson, Siobhan; Donaghy, Colette; McLaughlin, Russell L; Hardiman, Orla

Widespread subcortical grey matter degeneration in primary lateral sclerosis: a multimodal imaging study with genetic profiling

原发性侧索硬化症中广泛的皮质下灰质变性:一项结合基因谱分析的多模态成像研究

Finegan, Eoin; Li Hi Shing, Stacey; Chipika, Rangariroyashe H; Doherty, Mark A; Hengeveld, Jennifer C; Vajda, Alice; Donaghy, Colette; Pender, Niall; McLaughlin, Russell L; Hardiman, Orla; Bede, Peter