Correctors and Potentiators Rescue Function of the Truncated W1282X-Cystic Fibrosis Transmembrane Regulator (CFTR) Translation Product
校正剂和增效剂挽救截短的 W1282X-囊性纤维化跨膜调节剂 (CFTR) 翻译产物的功能
期刊:Journal of Biological Chemistry
影响因子:4
doi:10.1074/jbc.M116.764720
Peter M Haggie, Puay-Wah Phuan, Joseph-Anthony Tan, Haijin Xu, Radu G Avramescu, Doranda Perdomo, Lorna Zlock, Dennis W Nielson, Walter E Finkbeiner, Gergely L Lukacs, Alan S Verkman