日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Efficacy and safety of steroid-sparing strategy in the treatment of AIHA associated with KSHV/HHV-8 positive multicentric Castleman disease

类固醇替代疗法治疗伴有KSHV/HHV-8阳性多中心Castleman病的自身免疫性溶血性贫血的疗效和安全性

Dieudonné, Yannick; Gourguechon, Clément; Stammler, Romain; Delestre, Florence; Sorin, Boris; Dunogué, Bertrand; Dumas, Guillaume; Fouquet, Guillemette; Ronchetti, Anne-Marie; Paule, Romain; Meliani, Pascal; Pansu, Nathalie; Buzele, Rodolphe; Noel, Robin; Fadlallah, Jehane; Malphettes, Marion; Corvilain, Emilie; Meignin, Véronique; Guillaud, Constance; Dossier, Antoine; Dion, Jérémie; Gérard, Laurence; Oksenhendler, Eric; Galicier, Lionel; Boutboul, David

Optimizing ADAMTS13 prophylaxis to reduce relapse and organ failure in congenital thrombotic thrombocytopenic purpura

优化ADAMTS13预防以减少先天性血栓性血小板减少性紫癜的复发和器官衰竭

Joly, Bérangère S; Joseph, Adrien; Bouzid, Raïda; Boisseau, Pierre; Kwon, Thérésa; Dossier, Claire; Gouge-Biebuyck, Nathalie; Boyer, Olivia; Tsatsaris, Vassilis; Harambat, Jérôme; Delmas, Yahsou; Moranne, Olivier; Sellier-Leclerc, Anne-Laure; Marie, Manon; Barbet, Christelle; Provôt, François; Benhamou, Ygal; Veyradier, Agnès; Coppo, Paul; Augusto, Jean-François; Azoulay, Elie; Barbay, Virginie; Benhamou, Ygal; Arnaud, Jaccard; Charvet-Rumpler, Anne; Chauveau, Dominique; Choukroun, Gabriel; Coindre, Jean-Philippe; Coppo, Paul; Delmas, Yahsou; Celia, Salanoubat; Dossier, Antoine; Simon, Ville; Frémeaux-Bacchi, Véronique; Galicier, Lionel; Grangé, Steven; Guidet, Bertrand; Halimi, Jean-Michel; Antoine, Neel; Jacobs, Frédéric; Joly, Bérangère; Kanouni, Tarik; Kaplanski, Gilles; Virginie, Rieu; Le Guern, Véronique; Moulin, Bruno; Rebibou, Jean-Michel; Ojeda Uribe, Mario; Parquet, Nathalie; Pène, Frédéric; Perez, Pierre; Poullin, Pascale; Pouteil-Noble, Claire; Presne, Claire; Provôt, Françoi; Laurent, Mesnard; Saheb, Samir; Seguin, Amélie; Servais, Aude; Stépanian, Alain; Veyradier, Agnè; Vigneau, Cécile; Wynckel, Alain; Zunic, Patricia; Krummel, Thierry; Ulrich, Marc; Hertig, Alexandre; Benoît, Suzon; Laurent, Gilardin; Le Quintrec, Moglie; Kwon, Theresa; Chatelet, Valérie; Ducheyron, Damien; Martis, Nihal; Marie, Manon; Ribes, David; Ronchetti, Anne-Marie

Kidney Transplantation in Childhood-Onset ANCA-Associated Vasculitis: Long-Term Outcomes and Prognostic Factors

儿童期发病的ANCA相关性血管炎肾移植:长期结果和预后因素

Trivioli, Giorgio; Allinovi, Marco; Di Marcantonio, Elio; Jawa, Natasha A; Trivelli, Antonella; Yang, Jing; Grenda, Ryszard; Rubik, Jacek; Mohammad, Aladdin J; Testa, Sara; Jahnukainen, Timo; Gulhan, Bora; Topaloglu, Rezan; Puéchal, Xavier; Kosałka-Węgiel, Joanna; Dursun, Ismail; Guzzo, Isabella; Pasini, Andrea; Kostik, Mikhail M; Oni, Louise; Buti, Elisa; Becherucci, Francesca; Palazzini, Giulia; Moroni, Gabriella; Ozen, Seza; Laurent, Audrey; Harambat, Jerome; Dossier, Claire; Marks, Stephen D; Bruchfeld, Annette; Lugli, Gianmarco; Bettiol, Alessandra; Emmi, Giacomo; Romagnani, Paola; Saleem, Moin A; Ware, Nicholas; Zhou, Jianhua; Teoh, Chia Wei; Ghiggeri, Gian Marco; Noone, Damien; Vaglio, Augusto

Hemolytic Uremic Syndrome Outbreak in Adults and Shiga Toxin-Producing Escherichia coli Negative for Locus of Enterocyte Effacement, France, 2025

法国,2025年,成人溶血性尿毒综合征暴发及产志贺毒素大肠杆菌肠细胞黏附位点阴性

de Larminat, Justine; La, Kevin; Bidet, Philippe; Birgy, André; Liguori, Sandrine; Phlipaux, Pierre; Courroux, Celine; Crombé, Florence; Blanco, Jorge; Coppo, Paul; Dossier, Antoine; Armand-Lefevre, Laurence; Weill, François Xavier; Nodari, Carolina Silva; Jones, Gabrielle; Cointe, Aurelie; Bonacorsi, Stéphane

Outcomes in Children and Adults With Antiglomerular Basement Membrane Disease

抗肾小球基底膜病患儿及成人的预后

Suhlrie, Adriana; van der Meijden, Wilbert A G; Faguer, Stanislas; Alberici, Federico; Idrizi, Anisa; Audard, Vincent; Servais, Aude; Boyer, Olivia; Dossier, Claire; Radermacher, Jörg; Skalioti, Chrysanthi; Zieg, Jakub; Aksenova, Marina; Raes, Ann; Renson, Thomas; Mastrangelo, Antonio; Dorresteijn, Eiske; Terzi, Alexandra; Bouts, Antonia; Teixeira, Ana Fernandes; Herrero-Goñi, Maria; Haffner, Dieter; Kanzelmeyer, Nele

Efficacy and Thrombotic Risk of Thrombopoietin Receptor Agonists for Immune Thrombocytopenia Secondary to Systemic Lupus and Antiphospholipid Syndrome: French Experience With 80 Patients

血小板生成素受体激动剂治疗系统性红斑狼疮和抗磷脂综合征继发性免疫性血小板减少症的疗效和血栓风险:法国80例患者的经验

Marques, Cindy; Moulis, Guillaume; Roussotte, Mickaël; Bonnotte, Bernard; Viallard, Jean-François; Graveleau, Julie; Lobbes, Hervé; Costedoat-Chalumeau, Nathalie; Deroux, Alban; Gobert, Delphine; Dossier, Antoine; Gilardin, Laurent; Lambotte, Olivier; Dufrenoy, Mylène; Mahévas, Matthieu; Michel, Marc; Sève, Pascal; Godeau, Bertrand

Real-Life Data of 2-Year Lumasiran Use in the DAILY-LUMA Cohort

DAILY-LUMA队列中Lumasiran使用2年的真实世界数据

Sellier-Leclerc, Anne-Laure; Cloarec, Melissa; Knebelmann, Bertrand; Allard, Lise; Boyer, Olivia; Cloarec, Sylvie; Dossier, Claire; Le Quintrec, Moglie; Nobili, François; Stehlé, Thomas; Vrillon, Isabelle; Burtey, Stéphane; Cornec-Le Gall, Emilie; Courbebaisse, Marie; Frouget, Thierry; Garnier, Arnaud; Krummel, Thierry; Lemoine, Sandrine; Monet-Didailler, Catherine; Rousset-Rouvière, Caroline; Ryckewaert, Amélie; Schendel, Adeline; Flammier, Sacha; Acquaviva-Bourdain, Cécile; Bacchetta, Justine

Genotype-phenotype correlations and clinical outcomes of genetic TRPC6 podocytopathies

基因型-表型相关性及遗传性TRPC6足细胞病临床结局

McAnallen, Susan M; Elhassan, Elhussein A E; Stoneman, Sinead; Pinto E Vairo, Filippo; Hogan, Marie C; Hoefele, Julia; Clince, Michelle; Mekraksakit, Poemlarp; Titan, Silvia M; Jorge, Sofia; Calado, Joaquim; Decramer, Stéphane; Colliou, Eloïse; Tellier, Stéphanie; Francisco, Telma; Servais, Aude; Cornet, Joséphine; de Fallois, Jonathan; Dossier, Claire; Fenoglio, Roberta; Renieri, Alessandra; Pinto, Anna Maria; Daga, Sergio; Loberti, Lorenzo; Fila, Marc; Quintana, Luis F; Becherucci, Francesca; Godefroid, Nathalie; Dubrasquet, Astrid; Kálmán, Tory; Dolan, Niamh; Alawi, Bushra Al; Sweeney, Clodagh; Riordan, Michael; Stack, Maria; Awan, Atif; Hui, Ng Kar; McCarthy, Hugh J; Biros, Erik; Harris, Trudie; Kidd, Kendrah; Haeberle, Stefanie; Bleyer, Anthony J; Mallett, Andrew J; Sayer, John A; Schafer, Franz; Benson, Katherine A; McCann, Emma; Conlon, Peter J

A "Trial within a Cohort" platform for pediatric clinical trials on idiopathic nephrotic syndrome: scope, objectives, and design of the retrospective-prospective cohort PIN'SNP

针对特发性肾病综合征儿科临床试验的“队列内试验”平台:回顾性-前瞻性队列研究PIN'SNP的范围、目标和设计

Bahans, Claire; Boyer, Olivia; Dunand, Olivier; Parmentier, Cyrielle; Ranchin, Bruno; Roussey, Gwenaëlle; Samaille, Charlotte; Tellier, Stéphanie; Vrillon, Isabelle; Preka, Evgenia; Mériguet, Théo; Dubrasquet, Astrid; Ichay, Lydia; Clavé, Stéphanie; Bernardor, Julie; Merieau, Elodie; Dossier, Claire; Guigonis, Vincent

Obinutuzumab versus Rituximab to maintain remission in children with steroid-dependent and frequently relapsing nephrotic syndrome: the OBIRINS study protocol, a double-blind randomised controlled trial

奥妥珠单抗与利妥昔单抗维持激素依赖型且频繁复发的儿童肾病综合征缓解的疗效比较:OBIRINS 研究方案,一项双盲随机对照试验

Dossier, Claire; Sellier-Leclerc, Anne-Laure; Simon, Thomas; Parmentier, Cyrielle; Boyer, Olivia; Samaille, Charlotte; Fila, Marc; Roussey-Kesler, Gwenaelle; Magnavacca, Marie; Chartier, Yannis; Louillet, Ferielle; Zaloszyc, Ariane; Vrillon, Isabelle; Elaribi, Djamel; Bouatia, Sabrina; Kaguelidou, Florentia; Guilmin-Crepon, Sophie; Hogan, Julien