日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Mutational analysis implicates the amyloid fibril as the toxic entity in Huntington's disease

突变分析表明,淀粉样蛋白原纤维是亨廷顿病中的毒性物质。

Drombosky, Kenneth W; Rode, Sascha; Kodali, Ravi; Jacob, Tija C; Palladino, Michael J; Wetzel, Ronald

Folding Landscape of Mutant Huntingtin Exon1: Diffusible Multimers, Oligomers and Fibrils, and No Detectable Monomer.

突变亨廷顿蛋白外显子1的折叠景观:可扩散的多聚体、寡聚体和原纤维,以及未检测到的单体

Sahoo Bankanidhi, Arduini Irene, Drombosky Kenneth W, Kodali Ravindra, Sanders Laurie H, Greenamyre J Timothy, Wetzel Ronald

D-polyglutamine amyloid recruits L-polyglutamine monomers and kills cells

D-聚谷氨酰胺淀粉样蛋白募集L-聚谷氨酰胺单体并杀死细胞。

Kar, Karunakar; Arduini, Irene; Drombosky, Kenneth W; van der Wel, Patrick C A; Wetzel, Ronald