日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Targeting mitochondrial deubiquitinase USP30 to induce mitophagy in heteroplasmic mitochondrial diseases.

靶向线粒体去泛素化酶 USP30 以诱导异质性线粒体疾病中的线粒体自噬。

Pinho Brígida R, Martins Vasco, Chacko Anitta R, Nogueira Célia, Duchen Michael R, Oliveira Jorge M A

A transcription termination mechanism for maintaining homogeneous protein expression

维持均一蛋白质表达的转录终止机制

Esteban-Serna, Sofia; Widén, Tove; Gwynne, Mags; Farquhar, Iseabail; Duchen, Michael R; Swain, Peter S; Granneman, Sander

A mismatch in enzyme-redox partnerships underlies divergent cytochrome P450 activities between human hepatocytes and microsomes

人肝细胞和微粒体中细胞色素P450活性差异的根本原因是酶-氧化还原相互作用的不匹配。

Bapiro, Tashinga E; Martin, Scott; Blacker, Thomas S; Wilkinson, Stephen D; Orton, Alexandra L; Hariparsad, Niresh; Jones, Rhys D O; Duchen, Michael R; Harlfinger, Stephanie

Metabolic remodeling in hiPSC-derived myofibers carrying the m.3243A>G mutation.

携带 m.3243A>G 突变的 hiPSC 衍生肌纤维的代谢重塑

Valdebenito Gabriel E, Chacko Anitta R, Chung Chih-Yao, Sheshadri Preethi, Chi Haoyu, O'Callaghan Benjamin, Madej Monika J, Houlden Henry, Rouse Hannah, Morales Valle, Bianchi Katiuscia, Tedesco Francesco Saverio, Pitceathly Robert D S, Duchen Michael R

An iPSC-derived neuronal model reveals manganese's role in neuronal endocytosis, calcium flux and mitochondrial bioenergetics.

利用 iPSC 衍生的神经元模型揭示了锰在神经元内吞作用、钙流和线粒体生物能量学中的作用

Budinger Dimitri, Alhaque Sharmin, González-Méndez Ramón, Dadswell Chris, Barwick Katy, Ferrini Arianna, Roth Charlotte, McCann Conor J, Tuschl Karin, Al Jasmi Fatma, Zaki Maha S, Park Julien H, Dale Russell C, Mohammad Shekeeb, Christodoulou John, Moulding Dale, Duchen Michael R, Barral Serena, Kurian Manju A

Redox-dependent binding and conformational equilibria govern the fluorescence decay of NAD(P)H in living cells

氧化还原依赖性结合和构象平衡控制着活细胞中 NAD(P)H 的荧光衰减。

Blacker, Thomas S; Mistry, Nimit; Plotegher, Nicoletta; Westbrook, Elizabeth R; Sewell, Michael D E; Carroll, John; Szabadkai, Gyorgy; Bain, Angus J; Duchen, Michael R

Mutations in the Key Autophagy Tethering Factor EPG5 Link Neurodevelopmental and Neurodegenerative Disorders Including Early-Onset Parkinsonism

关键自噬锚定因子EPG5的突变与神经发育障碍和神经退行性疾病(包括早发性帕金森病)相关。

Dafsari, Hormos Salimi; Deneubourg, Celine; Singh, Kritarth; Maroofian, Reza; Suprenant, Zita; Kho, Ay Lin; Ingham, Neil J; Steel, Karen P; Sheshadri, Preethi; Baur, Franciska; Hentrich, Lea; Gerisch, Birgit; Zamani, Mina; Alves, Cesar; Siddiqui, Ata; Dafsari, Haidar S; Salari, Mehri; Lang, Anthony E; Harris, Michael; Abdelaleem, Alice; Sadeghian, Saeid; Azizimalamiri, Reza; Galehdari, Hamid; Shariati, Gholamreza; Sedaghat, Alireza; Zeighami, Jawaher; Calame, Daniel; Marafi, Dana; Duan, Ruizhi; Boehnke, Adrian; Clark, Gary D; Rosenfeld, Jill A; Mohila, Carrie A; Steel, Dora; Chopra, Saurabh; Sharma, Suvasini; Kohlschmidt, Nicolai; Patzer, Steffi; Saffari, Afshin; Ebrahimi-Fakhari, Darius; Çavdartepe, Büşra Eser; Chang, Irene J; Beckman, Erika; Peters, Renate; Fennell, Andrew Paul; Lo, Bernice; Averdunk, Luisa; Distelmaier, Felix; Baethmann, Martina; Elmslie, Frances; Joost, Kairit; Nampoothiri, Sheela; Yesodharan, Dhanya; Mandel, Hanna; Kimball, Amy; Kline, Antonie D; Mignot, Cyril; Keren, Boris; Laugel, Vincent; Õunap, Katrin; Devadathan, Kalpana; van Berkestijn, Frederique M C; Silwal, Arpana; Koene, Saskia; Verma, Sumit; Karim, Mohammed Yousuf; Boubidi, Chahynez; Aziz, Majid; ElGhazali, Gehad; Mattas, Lauren; Miryounesi, Mohammad; Hashemi-Gorji, Farzad; Alavi, Shahryar; Nouri, Nayereh; Noruzinia, Mehrdad; Kavousi, Saeideh; Kamath, Arveen; Jayawant, Sandeep; Saneto, Russell; Haridy, Nourelhoda A; Kart, Pinar Ozkan; Cansu, Ali; Joubert, Madeleine; Beneteau, Claire; Stuurman, Kyra E; Wilke, Martina; Barakat, Tahsin Stefan; Tajsharghi, Homa; Scardamaglia, Annarita; Vallian, Sadeq; Hız, Semra; Shoeibi, Ali; Boostani, Reza; Hashemi, Narges; Babaei, Meisam; Alsaleh, Norah Saleh; Porter, Julie; Attié-Bitach, Tania; Marzin, Pauline; Wicher, Dorota; Gold, Jessica I; Schuler, Elisabeth; Kashgari, Amna; Alanazi, Rakan F; Eyaid, Wafaa; Engelen, Marc; Langeveld, Mirjam; Stüve, Burkhard; Li, Yun; Yigit, Gökhan; Wollnik, Bernd; Monje, Mariana H G; Krainc, Dimitri; Mencacci, Niccolò E; Bakhtiari, Somayeh; Kruer, Michael; Argilli, Emanuela; Sherr, Elliott; Jamshidi, Yalda; Karimiani, Ehsan Ghayoor; Cheung, Yiu Wing Sunny; Karin, Ivan; Zifarelli, Giovanni; Bauer, Peter; Chung, Wendy K; Lupski, James R; Kurian, Manju A; Dötsch, Jörg; von Kleist-Retzow, Jürgen-Christoph; Klopstock, Thomas; Wagner, Matias; Yip, Calvin; Roos, Andreas; Carsetti, Rita; Dionisi-Vici, Carlo; Gautel, Mathias; Duchen, Michael R; Antebi, Adam; Houlden, Henry; Fanto, Manolis; Jungbluth, Heinz

Delocalized quinolinium-macrocyclic peptides, an atypical chemotype for CNS penetration

离域喹啉大环肽,一种非典型的中枢神经系统渗透化学类型

Pingitore, Valeria; Pancholi, Jessica; Hornsby, Thomas W; Warne, Justin; Pryce, Gareth; McCormick, Laura J; Hill, Julia; Bhosale, Gauri; Peng, Jing; Newton, Lydia S; Towers, Greg J; Coles, Simon J; Chan, Ah Wing Edith; Duchen, Michael R; Szabadkai, Gyorgy; Baker, David; Selwood, David L

The mitochondrial ATP synthase as an ATP consumer-a surprising therapeutic target

线粒体ATP合酶作为ATP消耗者——一个出人意料的治疗靶点

Valdebenito, Gabriel E; Chacko, Anitta R; Duchen, Michael R

NAD(P)H binding configurations revealed by time-resolved fluorescence and two-photon absorption

通过时间分辨荧光和双光子吸收揭示NAD(P)H结合构型

Blacker, Thomas S; Duchen, Michael R; Bain, Angus J