日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Changes in sputum viscoelastic properties and airway inflammation in primary ciliary dyskinesia are comparable to cystic fibrosis on elexacaftor/tezacaftor/ivacaftor therapy

原发性纤毛运动障碍患者的痰液粘弹性改变和气道炎症与接受依来卡托/替扎卡托/伊伐卡托治疗的囊性纤维化患者相似。

Nussstein, Hannah; Urbantat, Ruth M; Fentker, Kerstin; Loewe, Aditi; Duerr, Julia; Haji, Mohamed; Doellinger, Felix; Stahl, Mirjam; Graeber, Simon Y; Gradzielski, Michael; Röhmel, Jobst; Mertins, Philipp; Schaupp, Laura; Mall, Marcus A

Chemical Synthesis of Pseudomonas aeruginosa, Staphylococcus aureus, and Acinetobacter baumannii Capsular Polysaccharide Fragments as Leads for Cross-Protection

铜绿假单胞菌、金黄色葡萄球菌和鲍曼不动杆菌荚膜多糖片段的化学合成及其作为交叉保护先导化合物的应用

Mishra, Amar Kumar; Reuber, Emelie E; Rai, Diksha; Sander, Leif E; Duerr, Julia; Graeber, Simon Y; Mall, Marcus A; Fries, Bettina C; Seeberger, Peter H; Kulkarni, Suvarn S

Reduction of systemic inflammation by elexacaftor/tezacaftor/ivacaftor correlates with lung function improvement in cystic fibrosis

elexacaftor/tezacaftor/ivacaftor 降低全身炎症与囊性纤维化患者肺功能改善相关

Halle, Olga; Graeber, Simon Y; Kontsendorn, Julia; Kessemeier, Claudia; Falke, Jan-Niklas; Schwabe, Jannik; Schütz, Katharina; Pallenberg, Sophia T; Dalferth, Rebecca; Grychtol, Ruth; Ringshausen, Felix C; Stahl, Mirjam; Thee, Stephanie; Roehmel, Jobst F; Syunyaeva, Zulfiya; Duerr, Julia; Chung, Jaehi; Hirtz, Stephanie; Uselmann, Tatjana; Kühbandner, Iris; Rückes-Nilges, Claudia; Bagheri-Pothoff, Azadeh; Barth, Sandra; Schaub, Bianca; Brinkmann, Folke; Weber, Stefanie; van Koningsbruggen-Rietschel, Silke; Abdo, Mustafa; Weckmann, Markus; Widder, Stefanie; Hansen, Gesine; Tümmler, Burkhard; Sommerburg, Olaf; Naehrlich, Lutz; Mall, Marcus A; Dittrich, Anna-Maria

Functional Lung Imaging Identifies Peripheral Ventilation Changes in ꞵ-ENaC Mice

功能性肺成像识别出ꞵ-ENaC小鼠的外周通气变化

Reyne, Nicole; Smith, Ronan; Cmielewski, Patricia; Eikelis, Nina; Nilsen, Kris; Louise, Jennie; Duerr, Julia; Mall, Marcus A; Lawrence, Mark; Parsons, David; Donnelley, Martin

Lack of SLC26A9-mediated chloride secretion causes mucus plugging and severe respiratory distress in neonatal mice

新生小鼠缺乏SLC26A9介导的氯离子分泌会导致黏液栓塞和严重的呼吸窘迫。

Millar-Büchner, Pamela; Salomon, Johanna J; Duerr, Julia; Spahn, Stephan; Anagnostopoulou, Pinelopi; Wagner, Willi L; Wielpütz, Mark O; Groene, Hermann-Josef; Balázs, Anita; Mall, Marcus A

Intestinal current measurement detects age-dependent differences in CFTR function in rectal epithelium

肠道电流测量可检测直肠上皮细胞中CFTR功能的年龄依赖性差异。

Graeber, Simon Y; Sommerburg, Olaf; Yu, Yin; Berges, Julian; Hirtz, Stephanie; Scheuermann, Heike; Berger, Jasmin; Duerr, Julia; Mall, Marcus A

Reflection confocal microscopy for quantitative assessment of airway surface layer dysregulation and pharmacological rescue in cystic fibrosis under near-physiological conditions

在接近生理条件下,利用反射式共聚焦显微镜对囊性纤维化患者气道表面层功能紊乱及药物治疗效果进行定量评估

Agircan, Ayça Seyhan; Lampe, Marko; Scheuermann, Heike; Albrecht, Tobias; Graeber, Simon Y; Balázs, Anita; Baumann, Ingo; Block, Stephan; Pepperkok, Rainer; Mall, Marcus A; Duerr, Julia

High-resolution multimodal imaging reveals spatial and temporal heterogeneity of airway mucus plugging in mice with muco-obstructive lung disease

高分辨率多模态成像揭示了患有黏液阻塞性肺病的小鼠气道黏液栓塞的空间和时间异质性

Benke, Claudia V; Duerr, Julia; Engel, Annika; Dullin, Christian; Stiller, Wolfram; Horstmann, Heinz; Redenbach, Claudia; Ackermann, Maximilian; Kauczor, Hans-Ulrich; Kuner, Thomas; Wielpütz, Mark O; Mall, Marcus A; Wagner, Willi L

Longitudinal microcomputed tomography detects onset and progression of pulmonary fibrosis in conditional Nedd4-2 deficient mice

纵向微型计算机断层扫描可检测条件性 Nedd4-2 缺陷小鼠肺纤维化的发生和进展

Leitz, Dominik H W; Konietzke, Philip; Wagner, Willi L; Mertiny, Mara; Benke, Claudia; Schneider, Thomas; Morty, Rory E; Dullin, Christian; Stiller, Wolfram; Kauczor, Hans-Ulrich; Mall, Marcus A; Duerr, Julia; Wielpütz, Mark O

Genetic Deletion of Mmp9 Does Not Reduce Airway Inflammation and Structural Lung Damage in Mice with Cystic Fibrosis-like Lung Disease.

基因敲除 Mmp9 并不能减轻患有囊性纤维化样肺病的鼠的气道炎症和肺结构损伤

Wagner Claudius, Balázs Anita, Schatterny Jolanthe, Zhou-Suckow Zhe, Duerr Julia, Schultz Carsten, Mall Marcus A