Mitochondrial and energy metabolism dysfunctions are hallmarks of TDP-43(G376D) fibroblasts from members of an Amyotrophic Lateral Sclerosis family.
肌萎缩侧索硬化症家族成员的 TDP-43(G376D) 成纤维细胞的标志是线粒体和能量代谢功能障碍
期刊:Cell Death & Disease
影响因子:9.6
doi:10.1038/s41419-025-07584-2
Perciballi Elisa, Bovio Federica, Ferro Sara, Forcella Matilde, Rosati Jessica, Carletti Rose Mary, D'Anzi Angela, Gelati Maurizio, La Bella Vincenzo, Innocenti Metello, Spataro Rossella, Pecoraro Martina, Lombardi Ivan, Vulcano Edvige, Ruotolo Giorgia, Mercurio Sara, Sabatelli Mario, Lattante Serena, Malm Tarja, Ohtonen Sohvi, Vescovi Angelo Luigi, Fusi Paola, Ferrari Daniela