Impact of elexacaftor/tezacaftor/ivacaftor on lung function, nutritional status, pulmonary exacerbation frequency and sweat chloride in people with cystic fibrosis: real-world evidence from the German CF Registry
elexacaftor/tezacaftor/ivacaftor 对囊性纤维化患者肺功能、营养状况、肺部急性加重频率和汗液氯化物的影响:来自德国囊性纤维化登记处的真实世界证据
期刊:Lancet Regional Health-Europe
影响因子:13
doi:10.1016/j.lanepe.2023.100690
Sutharsan, Sivagurunathan; Dillenhoefer, Stefanie; Welsner, Matthias; Stehling, Florian; Brinkmann, Folke; Burkhart, Manuel; Ellemunter, Helmut; Dittrich, Anna-Maria; Smaczny, Christina; Eickmeier, Olaf; Kappler, Matthias; Schwarz, Carsten; Sieber, Sarah; Naehrig, Susanne; Naehrlich, Lutz