日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Retinal atrophy, inflammation, phagocytic and metabolic disruptions develop in the MerTK-cleavage-resistant mouse model

在MerTK裂解抗性小鼠模型中,会出现视网膜萎缩、炎症、吞噬功能紊乱和代谢紊乱。

Enderlin, Julie; Rieu, Quentin; Réty, Salomé; Vanoni, Elora M; Roux, Solène; Dégardin, Julie; César, Quénol; Augustin, Sébastien; Nous, Caroline; Cai, Bishuang; Fontaine, Valérie; Sennlaub, Florian; Nandrot, Emeline F

Gas6 and Protein S Ligands Cooperate to Regulate MerTK Rhythmic Activity Required for Circadian Retinal Phagocytosis

Gas6 和 Protein S 配体协同调节昼夜节律视网膜吞噬作用所需的 MerTK 节律活动

Célia Parinot, Jonathan Chatagnon, Quentin Rieu, Solène Roux, Dorine Néel, Florian Hamieh, Emeline F Nandrot

Deletion of IFT20 exclusively in the RPE ablates primary cilia and leads to retinal degeneration

仅在 RPE 中删除 IFT20 会导致初级纤毛消融并导致视网膜变性

Viola Kretschmer, Sandra Schneider, Peter Andreas Matthiessen, Dominik Reichert, Nathan Hotaling, Gunnar Glasßer, Ingo Lieberwirth, Kapil Bharti, Rossella De Cegli, Ivan Conte, Emeline F Nandrot, Helen Louise May-Simera

Modeling PRPF31 retinitis pigmentosa using retinal pigment epithelium and organoids combined with gene augmentation rescue

使用视网膜色素上皮和类器官结合基因增强拯救来建模 PRPF31 视网膜色素变性

Amélie Rodrigues, Amélie Slembrouck-Brec, Céline Nanteau, Angélique Terray, Yelyzaveta Tymoshenko, Yvrick Zagar, Sacha Reichman, Zhouhuan Xi, José-Alain Sahel, Stéphane Fouquet, Gael Orieux, Emeline F Nandrot, Leah C Byrne, Isabelle Audo, Jérôme E Roger, Olivier Goureau

Pleiotropic Roles of Scavenger Receptors in Circadian Retinal Phagocytosis: A New Function for Lysosomal SR-B2/LIMP-2 at the RPE Cell Surface

清道夫受体在昼夜节律视网膜吞噬作用中的多效性作用:RPE 细胞表面溶酶体 SR-B2/LIMP-2 的新功能

Quentin Rieu, Antoine Bougoüin, Yvrick Zagar, Jonathan Chatagnon, Abdallah Hamieh, Julie Enderlin, Thierry Huby, Emeline F Nandrot

Lack of the antioxidant enzyme methionine sulfoxide reductase A in mice impairs RPE phagocytosis and causes photoreceptor cone dysfunction

小鼠缺乏抗氧化酶蛋氨酸亚砜还原酶 A 会损害 RPE 吞噬功能并导致感光锥细胞功能障碍

Francesca Mazzoni, Ying Dun, Jade A Vargas, Emeline F Nandrot, Silvia C Finnemann

Cystoid maculopathy is a frequent feature of Cohen syndrome-associated retinopathy

囊样黄斑病变是科恩综合征相关视网膜病变的常见特征。

Gabrielle, Pierre-Henry; Faivre, Laurence; Audo, Isabelle; Zanlonghi, Xavier; Dollfus, Hélène; Thiadens, Alberta A H J; Zeitz, Christina; Mancini, Grazia M S; Perdomo, Yaumara; Mohand-Saïd, Saddek; Lizé, Eléonore; Lhussiez, Vincent; Nandrot, Emeline F; Acar, Niyazi; Creuzot-Garcher, Catherine; Sahel, José-Alain; Ansar, Muhammad; Thauvin-Robinet, Christel; Duplomb, Laurence; Da Costa, Romain

Identification of cell surface markers and establishment of monolayer differentiation to retinal pigment epithelial cells

细胞表面标志物的鉴定和单层细胞向视网膜色素上皮细胞分化的建立

Alvaro Plaza Reyes # ,Sandra Petrus-Reurer # ,Sara Padrell Sánchez ,Pankaj Kumar ,Iyadh Douagi ,Hammurabi Bartuma ,Monica Aronsson ,Sofie Westman ,Emma Lardner ,Helder André ,Anna Falk ,Emeline F Nandrot ,Anders Kvanta ,Fredrik Lanner

Preclinical safety studies of human embryonic stem cell-derived retinal pigment epithelial cells for the treatment of age-related macular degeneration

人类胚胎干细胞来源的视网膜色素上皮细胞治疗年龄相关性黄斑变性的临床前安全性研究

Sandra Petrus-Reurer, Pankaj Kumar, Sara Padrell Sánchez, Monica Aronsson, Helder André, Hammurabi Bartuma, Alvaro Plaza Reyes, Emeline F Nandrot, Anders Kvanta, Fredrik Lanner

Cohen Syndrome-Associated Cataract Is Explained by VPS13B Functions in Lens Homeostasis and Is Modified by Additional Genetic Factors

科恩综合征相关白内障可通过 VPS13B 在晶状体稳态中的作用来解释,并受其他遗传因素的影响

Vincent Lhussiez, Elisabeth Dubus, Quénol Cesar, Niyazi Acar, Emeline F Nandrot, Manuel Simonutti, Isabelle Audo, Eléonore Lizé, Sylvie Nguyen, Audrey Geissler, André Bouchot, Muhammad Ansar, Serge Picaud, Christel Thauvin-Robinet, Laurence Olivier-Faivre, Laurence Duplomb, Romain Da Costa