日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

A novel HDAC6 inhibitor, CKD-504, is effective in treating preclinical models of huntington's disease

一种新型HDAC6抑制剂CKD-504在治疗亨廷顿病临床前模型中有效。

Li, Endan; Choi, Jiwoo; Sim, Hye-Ri; Kim, Jiyeon; Jun, Jae Hyun; Kyung, Jangbeen; Ha, Nina; Kim, Semi; Ryu, Keun Ho; Chung, Seung Soo; Kim, Hyun Sook; Lee, Sungsu; Seol, Wongi; Song, Jihwan

Neural stem cells derived from the developing forebrain of YAC128 mice exhibit pathological features of Huntington's disease

来自 YAC128 小鼠发育前脑的神经干细胞表现出亨廷顿氏病的病理特征

Endan Li, Hee Ra Park, Chang Pyo Hong, Younghoon Kim, Jiwoo Choi, Suji Lee, Hyun Jung Park, Bomi Lee, Tae Aug Kim, Seong Jin Kim, Hyun Sook Kim, Jihwan Song

Neural Transplants From Human Induced Pluripotent Stem Cells Rescue the Pathology and Behavioral Defects in a Rodent Model of Huntington's Disease

来自人类诱导性多能干细胞的神经移植可挽救亨廷顿氏病啮齿动物模型中的病理和行为缺陷

Yongwoo Yoon, Hyun Sook Kim, Chang Pyo Hong, Endan Li, Iksoo Jeon, Hyun Jung Park, Nayeon Lee, Zhong Pei, Jihwan Song

Human-to-mouse prion-like propagation of mutant huntingtin protein

突变亨廷顿蛋白在人与鼠之间以类似朊病毒的方式传播

Iksoo Jeon, Francesca Cicchetti, Giulia Cisbani, Suji Lee, Endan Li, Jiwoo Bae, Nayeon Lee, Ling Li, Wooseok Im, Manho Kim, Hyun Sook Kim, Seung-Hun Oh, Tae-Aug Kim, Jung Jae Ko, Benoit Aubé, Abid Oueslati, Yun Joong Kim, Jihwan Song

Ghrelin protects spinal cord motoneurons against chronic glutamate excitotoxicity by inhibiting microglial activation

胃饥饿素通过抑制小胶质细胞活化来保护脊髓运动神经元免受慢性谷氨酸兴奋性毒性损伤。

Lee, Sungyoub; Kim, Yumi; Li, Endan; Park, Seungjoon