日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

CLUH maintains functional mitochondria and translation in motoneuronal axons and prevents peripheral neuropathy

CLUH 可维持运动神经元轴突中线粒体的功能和翻译,并预防周围神经病变。

Marta Zaninello ,Tim Schlegel ,Hendrik Nolte ,Mujeeb Pirzada ,Elisa Savino ,Esther Barth ,Ines Klein ,Hauke Wüstenberg ,Tesmin Uddin ,Lisa Wolff ,Brunhilde Wirth ,Helmar C Lehmann ,Jean-Michel Cioni ,Thomas Langer ,Elena I Rugarli

Fam134c and Fam134b shape axonal endoplasmic reticulum architecture in vivo

Fam134c 和 Fam134b 在体内塑造轴突内质网结构

Francescopaolo Iavarone #, Marta Zaninello #, Michela Perrone, Mariagrazia Monaco, Esther Barth, Felix Gaedke, Maria Teresa Pizzo, Giorgia Di Lorenzo, Vincenzo Desiderio, Eduardo Sommella, Fabrizio Merciai, Emanuela Salviati, Pietro Campiglia, Livio Luongo, Elvira De Leonibus, Elena Rugarli, Carmine

CLUH controls astrin-1 expression to couple mitochondrial metabolism to cell cycle progression

CLUH 控制 astrin-1 表达,将线粒体代谢与细胞周期进程联系起来

Désirée Schatton, Giada Di Pietro, Karolina Szczepanowska, Matteo Veronese, Marie-Charlotte Marx, Kristina Braunöhler, Esther Barth, Stefan Müller, Patrick Giavalisco, Thomas Langer, Aleksandra Trifunovic, Elena I Rugarli

The class 3 PI3K coordinates autophagy and mitochondrial lipid catabolism by controlling nuclear receptor PPARα

类 PI3K 通过控制核受体 PPARα 来协调自噬和线粒体脂质分解代谢

Anton Iershov, Ivan Nemazanyy, Chantal Alkhoury, Muriel Girard, Esther Barth, Nicolas Cagnard, Alexandra Montagner, Dominique Chretien, Elena I Rugarli, Herve Guillou, Mario Pende, Ganna Panasyuk

Loss of the mitochondrial i-AAA protease YME1L leads to ocular dysfunction and spinal axonopathy

线粒体 i-AAA 蛋白酶 YME1L 的缺失会导致眼部功能障碍和脊髓轴突病变

Hans-Georg Sprenger, Gulzar Wani, Annika Hesseling, Tim König, Maria Patron, Thomas MacVicar, Sofia Ahola, Timothy Wai, Esther Barth, Elena I Rugarli, Matteo Bergami, Thomas Langer

Astrocyte-specific deletion of the mitochondrial m-AAA protease reveals glial contribution to neurodegeneration

星形胶质细胞特异性删除线粒体 m-AAA 蛋白酶,揭示神经胶质细胞对神经退行性的影响

Sara Murru, Simon Hess, Esther Barth, Eva R Almajan, Désirée Schatton, Steffen Hermans, Susanne Brodesser, Thomas Langer, Peter Kloppenburg, Elena I Rugarli

CLUH regulates mitochondrial metabolism by controlling translation and decay of target mRNAs

CLUH 通过控制靶 mRNA 的翻译和衰变来调节线粒体代谢

Désirée Schatton, David Pla-Martin, Marie-Charlotte Marx, Henriette Hansen, Arnaud Mourier, Ivan Nemazanyy, Alberto Pessia, Peter Zentis, Teresa Corona, Vangelis Kondylis, Esther Barth, Astrid C Schauss, Vidya Velagapudi, Elena I Rugarli

The Mitochondrial m-AAA Protease Prevents Demyelination and Hair Greying

线粒体 m-AAA 蛋白酶可预防脱髓鞘和头发变白

Shuaiyu Wang, Julie Jacquemyn, Sara Murru, Paola Martinelli, Esther Barth, Thomas Langer, Carien M Niessen, Elena I Rugarli

CLUH regulates mitochondrial biogenesis by binding mRNAs of nuclear-encoded mitochondrial proteins

CLUH 通过结合核编码的线粒体蛋白的 mRNA 来调节线粒体的生物合成

Jie Gao, Désirée Schatton, Paola Martinelli, Henriette Hansen, David Pla-Martin, Esther Barth, Christian Becker, Janine Altmueller, Peter Frommolt, Marco Sardiello, Elena I Rugarli

AFG3L2 supports mitochondrial protein synthesis and Purkinje cell survival

AFG3L2 支持线粒体蛋白质合成和浦肯野细胞存活

Eva R Almajan, Ricarda Richter, Lars Paeger, Paola Martinelli, Esther Barth, Thorsten Decker, Nils-Göran Larsson, Peter Kloppenburg, Thomas Langer, Elena I Rugarli