日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

COQ4 is required for the oxidative decarboxylation of the C1 carbon of coenzyme Q in eukaryotic cells

在真核细胞中,辅酶Q4是辅酶Q C1碳氧化脱羧所必需的。

Ludovic Pelosi ,Laura Morbiato ,Arthur Burgardt ,Fiorella Tonello ,Abigail K Bartlett ,Rachel M Guerra ,Katayoun Kazemzadeh Ferizhendi ,Maria Andrea Desbats ,Bérengère Rascalou ,Marco Marchi ,Luis Vázquez-Fonseca ,Caterina Agosto ,Giuseppe Zanotti ,Morgane Roger-Margueritat ,María Alcázar-Fabra ,Laura García-Corzo ,Ana Sánchez-Cuesta ,Plácido Navas ,Gloria Brea-Calvo ,Eva Trevisson ,Volker F Wendisch ,David J Pagliarini ,Leonardo Salviati ,Fabien Pierrel

Typical NF2 and LTZR1 mutations are retained in an immortalized human schwann cell model of schwannomatosis

典型的 NF2 和 LTZR1 突变在永生化的人类神经鞘瘤细胞模型中得到保留

Valentina Melfi, Tasnim Mohamed, Alessandra Colciago, Alessandra Fasciani, Raffaele De Francesco, Daniela Bettio, Cristina Cerqua, Francesca Boaretto, Elisabetta Basso, Stefano Ferraresi, Marco Montini, Marica Eoli, Laura Papi, Eva Trevisson, Valerio Magnaghi

The Splicing of the Mitochondrial Calcium Uniporter Genuine Activator MICU1 Is Driven by RBFOX2 Splicing Factor during Myogenic Differentiation

线粒体钙单向转运体激活因子 MICU1 的剪接在成肌分化过程中由 RBFOX2 剪接因子驱动

Denis Vecellio Reane, Cristina Cerqua, Sabrina Sacconi, Leonardo Salviati, Eva Trevisson, Anna Raffaello

Vitamin K2 cannot substitute Coenzyme Q10 as electron carrier in the mitochondrial respiratory chain of mammalian cells

维生素 K2 不能替代辅酶 Q10 作为哺乳动物细胞线粒体呼吸链中的电子载体

Cristina Cerqua, Alberto Casarin, Fabien Pierrel, Luis Vazquez Fonseca, Giampiero Viola, Leonardo Salviati, Eva Trevisson

Vanillic Acid Restores Coenzyme Q Biosynthesis and ATP Production in Human Cells Lacking COQ6

香草酸可恢复缺乏 COQ6 的人体细胞中的辅酶 Q 生物合成和 ATP 生成

Manuel J Acosta Lopez, Eva Trevisson, Marcella Canton, Luis Vazquez-Fonseca, Valeria Morbidoni, Elisa Baschiera, Chiara Frasson, Ludovic Pelosi, Bérengère Rascalou, Maria Andrea Desbats, María Alcázar-Fabra, José Julián Ríos, Alicia Sánchez-García, Giuseppe Basso, Placido Navas, Fabien Pierrel, Glor

Mutations in COQ8B (ADCK4) found in patients with steroid-resistant nephrotic syndrome alter COQ8B function

在类固醇耐药性肾病综合征患者中发现的 COQ8B(ADCK4)突变会改变 COQ8B 的功能

Luis Vazquez Fonseca, Mara Doimo, Cristina Calderan, Maria Andrea Desbats, Manuel J Acosta, Cristina Cerqua, Matteo Cassina, Shazia Ashraf, Friedhelm Hildebrandt, Geppo Sartori, Placido Navas, Eva Trevisson, Leonardo Salviati

Molecular characterization of the human COQ5 C-methyltransferase in coenzyme Q10 biosynthesis

辅酶 Q10 生物合成中人类 COQ5 C-甲基转移酶的分子表征

Theresa P T Nguyen, Alberto Casarin, Maria Andrea Desbats, Mara Doimo, Eva Trevisson, Carlos Santos-Ocaña, Placido Navas, Catherine F Clarke, Leonardo Salviati

The conserved mitochondrial twin Cx9C protein Cmc2 Is a Cmc1 homologue essential for cytochrome c oxidase biogenesis

保守的线粒体双胞胎 Cx9C 蛋白 Cmc2 是细胞色素 c 氧化酶生物合成所必需的 Cmc1 同源物

Darryl Horn, Wen Zhou, Eva Trevisson, Hassan Al-Ali, Thomas K Harris, Leonardo Salviati, Antoni Barrientos