日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Transmission of Norwegian reindeer CWD to sheep by intracerebral inoculation results in an unusual phenotype and prion distribution

挪威驯鹿慢性疾病 (CWD) 通过脑内接种传播给绵羊,导致异常表型和朊病毒分布

Erez Harpaz #, Federico Angelo Cazzaniga #, Linh Tran, Tram T Vuong, Giuseppe Bufano, Øyvind Salvesen, Maiken Gravdal, Devin Aldaz, Julianna Sun, Sehun Kim, Luigi Celauro, Giuseppe Legname, Glenn C Telling, Michael A Tranulis, Sylvie L Benestad, Arild Espenes, Fabio Moda #, Cecilie Ersdal #

Unfolding Mechanism and Fibril Formation Propensity of Human Prion Protein in the Presence of Molecular Crowding Agents

分子拥挤剂存在下人朊病毒蛋白的去折叠机制和纤维形成倾向

Manoj Madheswaran, Nataliia Ventserova, Gianluca D'Abrosca, Giulia Salzano, Luigi Celauro, Federico Angelo Cazzaniga, Carla Isernia, Gaetano Malgieri, Fabio Moda, Luigi Russo, Giuseppe Legname, Roberto Fattorusso

Different tau fibril types reduce prion level in chronically and de novo infected cells

不同类型的 tau 纤维可降低慢性和新生感染细胞中的朊病毒水平

Luigi Celauro, Anna Burato, Marco Zattoni, Elena De Cecco, Marco Fantuz, Federico Angelo Cazzaniga, Edoardo Bistaffa, Fabio Moda, Giuseppe Legname

Structural and dynamical determinants of a β-sheet-enriched intermediate involved in amyloid fibrillar assembly of human prion protein

参与人类朊病毒淀粉样纤维组装的富含β-片层中间体的结构和动力学决定因素

Luigi Russo, Giulia Salzano, Andrea Corvino, Edoardo Bistaffa, Fabio Moda, Luigi Celauro, Gianluca D'Abrosca, Carla Isernia, Danilo Milardi, Gabriele Giachin, Gaetano Malgieri, Giuseppe Legname, Roberto Fattorusso

Serpin Signatures in Prion and Alzheimer's Diseases

朊病毒和阿尔茨海默病中的丝氨酸蛋白酶抑制剂特征

Marco Zattoni #, Marika Mearelli #, Silvia Vanni, Arianna Colini Baldeschi, Thanh Hoa Tran, Chiara Ferracin, Marcella Catania, Fabio Moda, Giuseppe Di Fede, Giorgio Giaccone, Fabrizio Tagliavini, Gianluigi Zanusso, James W Ironside, Isidre Ferrer, Giuseppe Legname

DNAJB2-related Charcot-Marie-Tooth disease type 2: Pathomechanism insights and phenotypic spectrum widening

DNAJB2相关夏科-马里-图斯病2型:发病机制的深入理解和表型谱的扩展

Paola Saveri ,Stefania Magri ,Emanuela Maderna ,Francesca Balistreri ,Raffaella Lombardi ,Claudia Ciano ,Fabio Moda ,Barbara Garavaglia ,Chiara Reale ,Giuseppe Lauria Pinter ,Franco Taroni ,Davide Pareyson ,Chiara Pisciotta

β2-microglobulin triggers NLRP3 inflammasome activation in tumor-associated macrophages to promote multiple myeloma progression

β2微球蛋白触发肿瘤相关巨噬细胞中的NLRP3炎症小体活化,促进多发性骨髓瘤进展

Daniel Hofbauer, Dimitrios Mougiakakos, Luca Broggini, Mario Zaiss, Maike Büttner-Herold, Christian Bach, Bernd Spriewald, Frank Neumann, Savita Bisht, Jens Nolting, Robert Zeiser, Shaima'a Hamarsheh, Martin Eberhardt, Julio Vera, Cristina Visentin, Chiara Maria Giulia De Luca, Fabio Moda, Stefan Ha

PMCA-generated prions from the olfactory mucosa of patients with Fatal Familial Insomnia cause prion disease in mice

PMCA 从致死性家族性失眠症患者的嗅粘膜中产生的朊病毒会导致小鼠患上朊病毒病

Edoardo Bistaffa #, Alba Marín-Moreno #, Juan Carlos Espinosa, Chiara Maria Giulia De Luca, Federico Angelo Cazzaniga, Sara Maria Portaleone, Luigi Celauro, Giuseppe Legname, Giorgio Giaccone, Juan Maria Torres, Fabio Moda

The Alpha-Synuclein RT-QuIC Products Generated by the Olfactory Mucosa of Patients with Parkinson's Disease and Multiple System Atrophy Induce Inflammatory Responses in SH-SY5Y Cells

帕金森病和多系统萎缩患者嗅黏膜产生的 Alpha-突触核蛋白 RT-QuIC 产物在 SH-SY5Y 细胞中诱发炎症反应

Chiara Maria Giulia De Luca, Alessandra Consonni, Federico Angelo Cazzaniga, Edoardo Bistaffa, Giuseppe Bufano, Giorgia Quitarrini, Luigi Celauro, Giuseppe Legname, Roberto Eleopra, Fulvio Baggi, Giorgio Giaccone, Fabio Moda

The Cellular Prion Protein Increases the Uptake and Toxicity of TDP-43 Fibrils

细胞朊病毒蛋白增加 TDP-43 原纤维的吸收和毒性

Carlo Scialò, Luigi Celauro, Marco Zattoni, Thanh Hoa Tran, Edoardo Bistaffa, Fabio Moda, Robert Kammerer, Emanuele Buratti, Giuseppe Legname