日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Elexacaftor/Tezacaftor/Ivacaftor for Cystic Fibrosis and Rare CFTR Variants: In Vitro Translation to a Phase 3, Double-Blind, Randomized, Placebo-controlled Trial and Real-World Study

Elexacaftor/Tezacaftor/Ivacaftor 用于囊性纤维化和罕见 CFTR 变异:体外研究向 3 期双盲、随机、安慰剂对照试验和真实世界研究的转化

Castellani, Carlo; Mondejar-Lopez, Pedro; Van Goor, Fredrick; Quon, Bradley S; Alghisi, Federico; Fabrizzi, Benedetta; Ramsey, Bonnie; Taylor-Cousar, Jennifer L; McKone, Edward F; Tullis, Elizabeth; Weinstock, Tanya G; Tan, Vincent; Ahluwalia, Neil; Mahic, Milada; Liu, Lingyun; Saayman, Sheena; Altshuler, David; Waltz, David; Mall, Marcus A; Fajac, Isabelle

Modulation of immune responses by elexacaftor/tezacaftor/ivacaftor therapy in cystic fibrosis: data from a compassionate use program

elexacaftor/tezacaftor/ivacaftor 疗法对囊性纤维化患者免疫反应的调节:来自同情用药计划的数据

Lucca, Francesca; Pianazzola, Anna; Meneghelli, Ilaria; Catanzaro, Giuseppina; Sabbioni, Giuseppe; Tridello, Gloria; Hristodor, Anca Manuela; De Luca, Erik; Menichetti, Giacomo; Breveglieri, Giulia; Altieri, Maria Teresa; Bordicchia, Marica; Fabrizzi, Benedetta; Ferretti, Elisabetta; Lippi, Giuseppe; Ros, Mirco; Borgatti, Monica; Cipolli, Marco; Bezzerri, Valentino

Potentiating anti-inflammatory and antioxidant effects in vitro: the combined action of zofenoprilat and nebivolol.

佐芬诺普利和奈必洛尔的联合作用可增强体外抗炎和抗氧化作用。

Maceroni Eleonora, Cimini Annamaria, d'Angelo Michele, Scenna Marta Sofia, Meto Suada, Baldini Simone, Fabrizzi Paolo, Desideri Giovambattista, Castelli Vanessa

Beyond Trikafta: new models to assess tissue dependent rescue of N1303K-CFTR

Trikafta 之外:评估 N1303K-CFTR 组织依赖性拯救的新模型

Pranke, Iwona; Capurro, Valeria; Chevalier, Benoit; Pesce, Emanuela; Tomati, Valeria; Pastorino, Cristina; Kelly-Aubert, Mairead; Hatton, Aurelie; Dreano, Elise; Lena, Mariateresa; Bocciardi, Renata; Zara, Federico; Pantano, Stefano; Terlizzi, Vito; Lucanto, Cristina; Costa, Stefano; Claut, Laura; Daccò, Valeria; Poli, Piercarlo; Maschio, Massimo; Fabrizzi, Benedetta; Caporelli, Nicole; Cipolli, Marco; Volpi, Sonia; Chedevergne, Frederique; Cosson, Laure; Macey, Julie; Ramel, Sophie; Weiss, Laurence; Grenet, Dominique; Le Clainche-Viala, Laurence; Douvry, Benoit; Ravoninjatovo, Bruno; Audousset, Camille; Tatopoulos, Aurélie; Richaud-Thiriez, Bénédicte; Baravalle, Melissa; Thouvenin, Guillaume; Labbé, Guillaume; Mittaine, Marie; Reix, Philippe; Durieu, Isabelle; Mankikian, Julie; Bui, Stéphanie; Nguyen-Khoa, Thao; Khoukh, Karim; Martin, Clémence; Da Silva, Jennifer; De Carli, Paola; Castellani, Carlo; Cresta, Federico; Galietta, Luis; Guillemaut, Anne; Girodon, Emmanuelle; Remus, Natacha; Bulcaen, Mathis; Ensinck, Marjolein; Zajac, Miroslaw; Carlon, Marianne; LeBihan, Jean; Burgel, Pierre-Régis; Sermet-Gaudelus, Isabelle; Hinzpeter, Alexandre; Pedemonte, Nicoletta

Critical Issues in the Management of CRMS/CFSPID Children: A National Real-World Survey

CRMS/CFSPID患儿管理中的关键问题:一项全国性真实世界调查

Terlizzi, Vito; Fevola, Cristina; Presti, Santiago; Claut, Laura; Ambroni, Maura; Calderazzo, Maria Adelaide; Esposito, Irene; Fabrizzi, Benedetta; Leonetti, Giuseppina; Lombardo, Mariangela; Maschio, Massimo; Palladino, Nicola; Pauro, Francesca; Pisi, Giovanna; Ripani, Pietro; Ros, Mirco; Rotolo, Novella; Salvatore, Donatello; Sepe, Angela; Termini, Lisa; Timpano, Silviana; Troiani, Patrizia; Vitullo, Pamela; Zanda, Maurizio; Blasi, Francesco; Castellani, Carlo

The Human Phenotype Ontology in 2024: phenotypes around the world

2024 年人类表型本体论:世界各地的表型

Gargano, Michael A; Matentzoglu, Nicolas; Coleman, Ben; Addo-Lartey, Eunice B; Anagnostopoulos, Anna V; Anderton, Joel; Avillach, Paul; Bagley, Anita M; Bakštein, Eduard; Balhoff, James P; Baynam, Gareth; Bello, Susan M; Berk, Michael; Bertram, Holli; Bishop, Somer; Blau, Hannah; Bodenstein, David F; Botas, Pablo; Boztug, Kaan; Čady, Jolana; Callahan, Tiffany J; Cameron, Rhiannon; Carbon, Seth J; Castellanos, Francisco; Caufield, J Harry; Chan, Lauren E; Chute, Christopher G; Cruz-Rojo, Jaime; Dahan-Oliel, Noémi; Davids, Jon R; de Dieuleveult, Maud; de Souza, Vinicius; de Vries, Bert B A; de Vries, Esther; DePaulo, J Raymond; Derfalvi, Beata; Dhombres, Ferdinand; Diaz-Byrd, Claudia; Dingemans, Alexander J M; Donadille, Bruno; Duyzend, Michael; Elfeky, Reem; Essaid, Shahim; Fabrizzi, Carolina; Fico, Giovanna; Firth, Helen V; Freudenberg-Hua, Yun; Fullerton, Janice M; Gabriel, Davera L; Gilmour, Kimberly; Giordano, Jessica; Goes, Fernando S; Moses, Rachel Gore; Green, Ian; Griese, Matthias; Groza, Tudor; Gu, Weihong; Guthrie, Julia; Gyori, Benjamin; Hamosh, Ada; Hanauer, Marc; Hanušová, Kateřina; He, Yongqun Oliver; Hegde, Harshad; Helbig, Ingo; Holasová, Kateřina; Hoyt, Charles Tapley; Huang, Shangzhi; Hurwitz, Eric; Jacobsen, Julius O B; Jiang, Xiaofeng; Joseph, Lisa; Keramatian, Kamyar; King, Bryan; Knoflach, Katrin; Koolen, David A; Kraus, Megan L; Kroll, Carlo; Kusters, Maaike; Ladewig, Markus S; Lagorce, David; Lai, Meng-Chuan; Lapunzina, Pablo; Laraway, Bryan; Lewis-Smith, David; Li, Xiarong; Lucano, Caterina; Majd, Marzieh; Marazita, Mary L; Martinez-Glez, Victor; McHenry, Toby H; McInnis, Melvin G; McMurry, Julie A; Mihulová, Michaela; Millett, Caitlin E; Mitchell, Philip B; Moslerová, Veronika; Narutomi, Kenji; Nematollahi, Shahrzad; Nevado, Julian; Nierenberg, Andrew A; Čajbiková, Nikola Novák; Nurnberger, John I Jr; Ogishima, Soichi; Olson, Daniel; Ortiz, Abigail; Pachajoa, Harry; Perez de Nanclares, Guiomar; Peters, Amy; Putman, Tim; Rapp, Christina K; Rath, Ana; Reese, Justin; Rekerle, Lauren; Roberts, Angharad M; Roy, Suzy; Sanders, Stephan J; Schuetz, Catharina; Schulte, Eva C; Schulze, Thomas G; Schwarz, Martin; Scott, Katie; Seelow, Dominik; Seitz, Berthold; Shen, Yiping; Similuk, Morgan N; Simon, Eric S; Singh, Balwinder; Smedley, Damian; Smith, Cynthia L; Smolinsky, Jake T; Sperry, Sarah; Stafford, Elizabeth; Stefancsik, Ray; Steinhaus, Robin; Strawbridge, Rebecca; Sundaramurthi, Jagadish Chandrabose; Talapova, Polina; Tenorio Castano, Jair A; Tesner, Pavel; Thomas, Rhys H; Thurm, Audrey; Turnovec, Marek; van Gijn, Marielle E; Vasilevsky, Nicole A; Vlčková, Markéta; Walden, Anita; Wang, Kai; Wapner, Ron; Ware, James S; Wiafe, Addo A; Wiafe, Samuel A; Wiggins, Lisa D; Williams, Andrew E; Wu, Chen; Wyrwoll, Margot J; Xiong, Hui; Yalin, Nefize; Yamamoto, Yasunori; Yatham, Lakshmi N; Yocum, Anastasia K; Young, Allan H; Yüksel, Zafer; Zandi, Peter P; Zankl, Andreas; Zarante, Ignacio; Zvolský, Miroslav; Toro, Sabrina; Carmody, Leigh C; Harris, Nomi L; Munoz-Torres, Monica C; Danis, Daniel; Mungall, Christopher J; Köhler, Sebastian; Haendel, Melissa A; Robinson, Peter N

Clinically Relevant Characterization and Comparison of Ryaltris and Other Anti-Allergic Nasal Sprays

Ryaltris 与其他抗过敏鼻喷雾剂的临床相关特征及比较

Virginia Patterlini, Fabiola Guareschi, Davide D'Angelo, Simone Baldini, Suada Meto, Dalia Mostafa Kamal, Paolo Fabrizzi, Francesca Buttini, Ralph Mösges, Fabio Sonvico

Dexketoprofen Trometamol and Tramadol Hydrochloride Fixed-Dose Combination in Moderate to Severe Acute Low Back Pain: A Phase IV, Randomized, Parallel Group, Placebo, Active-Controlled Study (DANTE)

右酮洛芬氨丁三醇和盐酸曲马多固定剂量组合治疗中重度急性腰痛:一项 IV 期随机、平行组、安慰剂、活性对照研究 (DANTE)

Varrassi, Giustino; Hanna, Magdi; Coaccioli, Stefano; Fabrizzi, Paolo; Baldini, Simone; Kruljac, Ivan; Brotons, Carles; Perrot, Serge

A Multicentre Italian Study on the Psychological Impact of an Inconclusive Cystic Fibrosis Diagnosis after Positive Neonatal Screening

一项意大利多中心研究:新生儿筛查阳性后囊性纤维化诊断不确定对心理的影响

Tosco, Antonella; Marino, Diletta; Polizzi, Sara; Tradati, Valentina; Padoan, Rita; Giust, Claudia; Fabrizzi, Benedetta; Taccetti, Giovanni; Merli, Lucia; Terlizzi, Vito

Integrative perspective of the healthy aging process considering the metabolome, cardiac autonomic modulation and cardiorespiratory fitness evaluated in age groups

从综合视角审视健康老龄化过程,考虑代谢组、心脏自主神经调节和按年龄组评估的心肺健康状况

Étore De Favari Signini, Alex Castro, Patrícia Rehder-Santos, Juliana Cristina Millan-Mattos, Juliana Magalhães de Oliveira, Vinicius Minatel, Camila Bianca Falasco Pantoni, Heloisa Sobreiro Selistre de Araújo, Fernando Fabrizzi, Alberto Porta, Antônio Gilberto Ferreira, Regina Vincenzi Oliveira, Ap