日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Premature skeletal muscle aging in VPS13A deficiency relates to impaired autophagy

VPS13A缺陷导致的骨骼肌过早衰老与自噬功能受损有关

Riccardi, Veronica; Viscomi, Carlo Fiore; Sandri, Marco; D'Alessandro, Angelo; Dzieciatkowska, Monika; Stephenson, Daniel; Federti, Enrica; Hermann, Andreas; Salviati, Leonardo; Siciliano, Angela; Andolfo, Immacolata; Alper, Seth L; Ceolan, Jacopo; Iolascon, Achille; Vattemi, Gaetano; Danek, Adrian; Walker, Ruth H; Mensch, Alexander; Otto, Markus; Deschauer, Marcus; Armbrust, Moritz; Beninca', Cristiane; Salari, Valentina; Fabene, Paolo; Peikert, Kevin; De Franceschi, Lucia

Epeleuton, a novel synthetic ω-3 fatty acid, reduces hypoxia/ reperfusion stress in a mouse model of sickle cell disease

新型合成ω-3脂肪酸Epeleuton可减轻镰状细胞病小鼠模型中的缺氧/再灌注应激。

Mattè, Alessandro; Federti, Enrica; Recchiuti, Antonio; Hamza, Moayed; Ferri, Giulia; Riccardi, Veronica; Ceolan, Jacopo; Passarini, Alice; Mazzi, Filippo; Siciliano, Angela; Bhatt, Deepak L; Coughlan, David; Climax, John; Gremese, Elisa; Brugnara, Carlo; De Franceschi, Lucia

Nrf2 Plays a Key Role in Erythropoiesis during Aging

Nrf2 在衰老过程中的红细胞生成中起着关键作用

Serge Cedrick Toya Mbiandjeu, Angela Siciliano, Alessandro Mattè, Enrica Federti, Massimiliano Perduca, Davide Melisi, Immacolata Andolfo, Angela Amoresano, Achille Iolascon, Maria Teresa Valenti, Francesco Turrini, Michele Bovi, Arianna Pisani, Antonio Recchiuti, Domenico Mattoscio, Veronica Riccar

Duality of Nrf2 in iron-overload cardiomyopathy

Nrf2在铁过载性心肌病中的双重作用

Federti, Enrica; Vinchi, Francesca; Iatcenko, Iana; Ghigo, Alessandra; Matte, Alessandro; Toya, Serge Cedrick Mbiandjeu; Siciliano, Angela; Chiabrando, Deborah; Tolosano, Emanuela; Vance, Steven Zebulon; Riccardi, Veronica; Andolfo, Immacolata; Iezzi, Manuela; Lamolinara, Alessia; Iolascon, Achille; De Franceschi, Lucia

Mitapivat, a pyruvate kinase activator, improves transfusion burden and reduces iron overload in β-thalassemic mice

米塔皮伐特(Mitapivat)是一种丙酮酸激酶激活剂,可减轻β-地中海贫血小鼠的输血负担并降低其铁过载。

Mattè, Alessandro; Kosinski, Penelope A; Federti, Enrica; Dang, Lenny; Recchiuti, Antonio; Russo, Roberta; Siciliano, Angela; Riccardi, Veronica; Janin, Anne; Mucci, Matteo; Leboeuf, Christophe; Iolascon, Achille; Brugnara, Carlo; De Franceschi, Lucia

In Humanized Sickle Cell Mice, Imatinib Protects Against Sickle Cell-Related Injury

在人源化镰状细胞小鼠中,伊马替尼可预防镰状细胞相关损伤

Enrica Federti, Alessandro Matte, Antonio Recchiuti, Francesca Garello, Alessandra Ghigo, Wassim El Nemer, Enzo Terreno, Angela Amoresano, Domenico Mattoscio, Franco Turrini, Christophe Lebouef, Anne Janin, Antonella Pantaleo, Roberta Russo, Mickael Marin, Iana Iatcencko, Veronica Riccardi, Angela S

Mitapivat reprograms the RBC metabolome and improves anemia in a mouse model of hereditary spherocytosis

Mitapivat 重新编程红细胞代谢组并改善遗传性球形红细胞增多症小鼠模型中的贫血

Alessandro Matte, Anand B Wilson, Federica Gevi, Enrica Federti, Antonio Recchiuti, Giulia Ferri, Anna Maria Brunati, Mario Angelo Pagano, Roberta Russo, Christophe Leboeuf, Anne Janin, Anna Maria Timperio, Achille Iolascon, Elisa Gremese, Lenny Dang, Narla Mohandas, Carlo Brugnara, Lucia De Frances

Evidence of protective effects of recombinant ADAMTS13 in a humanized model of sickle cell disease

重组ADAMTS13在人源化镰状细胞病模型中的保护作用证据

Rossato, Paolo; Federti, Enrica; Matte, Alessandro; Glantschnig, Helmut; Canneva, Fabio; Schuster, Maria; Coulibaly, Sogue; Schrenk, Gerald; Voelkel, Dirk; Dockal, Michael; Plaimauer, Barbara; Andolfo, Immacolata; Iolascon, Achille; Rottensteiner, Hanspeter; Gritsch, Herbert; Scheiflinger, Friedrich; Hoellriegl, Werner; Franceschi, Lucia De

P1654: COMPLEMENT ACTIVATION REGULATES PLATELET HOMEOSTASIS BY ARRESTING THE ANTI-INFLAMMATORY EFFECTS OF INTERLEUKIN-35 IN IMMUNE THROMBOCYTOPENIA

P1654:补体激活通过抑制白细胞介素-35在免疫性血小板减少症中的抗炎作用来调节血小板稳态

Wasi, P; Zamanillo, Irene; Barrio, Santiago; Martin, Alejandro; Dorado, Sara; Heredia, Yanira; Rodriguez, Margarita; Rapado, Inmaculada; Isabel Jimenez Ubieto, Ana; Ayala Diaz, Rosa; Martinez-Lopez, Joaquín; Teresa Cedena Romero, Maria; Hebert, L; Shah, P; Diaz, O; Street, A A; Li, J; Rudenko, E; Zlotnicki, A M; Morrison, C; Bomben, R; Huang, Y; Medina Herrera, A; Wong, A; Gleen, S; Federti, E; Matte’, A; Hamza, M; Lafferty, A; Coughlan, D; Weissbach, M; Bhatt, D L; Riccardi, V; Perissinotto, R; Siciliano, A; Climax, J; Brugnara, C; De Franceschi, L; Gui, R-Y; Wu, Y; Chen, Y-X; Liu, F-Q; Qu, Q-Y; Huang, X-J; Zhang, X-H

The pyruvate kinase activator mitapivat reduces hemolysis and improves anemia in a β-thalassemia mouse model

丙酮酸激酶激活剂米塔匹伐可减少溶血并改善β-地中海贫血小鼠模型中的贫血。

Matte, Alessandro; Federti, Enrica; Kung, Charles; Kosinski, Penelope A; Narayanaswamy, Rohini; Russo, Roberta; Federico, Giorgia; Carlomagno, Francesca; Desbats, Maria Andrea; Salviati, Leonardo; Leboeuf, Christophe; Valenti, Maria Teresa; Turrini, Francesco; Janin, Anne; Yu, Shaoxia; Beneduce, Elisabetta; Ronseaux, Sebastien; Iatcenko, Iana; Dang, Lenny; Ganz, Tomas; Jung, Chun-Ling; Iolascon, Achille; Brugnara, Carlo; De Franceschi, Lucia