日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Revising pathogenesis of AP1S1-related MEDNIK syndrome: a missense variant in the AP1S1 gene as a causal genetic lesion

修正AP1S1相关MEDNIK综合征的发病机制:AP1S1基因中的错义变异是致病基因病变

Rackova, Marketa; Mattera, Rafael; Svaton, Michael; Fencl, Filip; Kanderova, Veronika; Spicakova, Karolina; Park, Sang Yoon; Fabian, Ondrej; Koblizek, Miroslav; Fronkova, Eva; Bonifacino, Juan S; Skvarova Kramarzova, Karolina

Effects of two different dexamethasone dosing regimens on ventilator-free days and long-term mortality in COVID-19 patients with moderate-to-severe ARDS: the REMED randomized clinical trial

两种不同地塞米松给药方案对中重度急性呼吸窘迫综合征(ARDS)COVID-19患者无创通气天数和长期死亡率的影响:REMED随机临床试验

Maláska, Jan; Stašek, Jan; Máca, Jan; Kutěj, Martin; Duška, František; Kafka, Petr; Klementová, Olga; Doubravská, Lenka; Hruda, Jan; Fencl, Marek; Gabrhelík, Tomáš; Číž, Libor; Zatloukal, Jan; Pouska, Jiří; Novotný, Pavel; Balík, Martin; Demlová, Regina; Kubátová, Jana; Vinklerová, Jana; Grodová, Karolína; Štěpánová, Radka; Svobodník, Adam; Kratochvíl, Milan; Klučka, Jozef; Štourač, Petr; Singer, Mervyn

The Czech Home Parenteral Nutrition Registry REDNUP: Comprehensive Analysis of Adult Patients' Data

捷克家庭肠外营养登记处 REDNUP:成人患者数据的综合分析

Koudelková, Kateřina; Waldauf, Petr; Wohl, Petr; Šenkyřík, Michal; Beneš, Petr; Kohout, Pavel; Vejmelka, Jiří; Maňák, Jan; Těšínský, Pavel; Novák, František; Meisnerová, Eva; Fencl, Filip; Gojda, Jan

B cell phenotype and serum levels of interferons, BAFF, and APRIL in multisystem inflammatory syndrome in children associated with COVID-19 (MIS-C)

儿童 COVID-19 相关多系统炎症综合征 (MIS-C) 中 B 细胞表型和血清干扰素、BAFF 和 APRIL 水平

Adam Klocperk # ,Marketa Bloomfield # ,Zuzana Parackova ,Ludovic Aillot ,Jiri Fremuth ,Lumir Sasek ,Jan David ,Filip Fencl ,Aneta Skotnicova ,Katerina Rejlova ,Martin Magner ,Ondrej Hrusak ,Anna Sediva

COVID-19-Associated Paediatric Inflammatory Multisystem Syndrome (PIMS-TS) in Intensive Care: A Retrospective Cohort Trial (PIMS-TS INT)

COVID-19 相关儿童炎症性多系统综合征 (PIMS-TS) 在重症监护中的研究:一项回顾性队列试验 (PIMS-TS INT)

Musilová, Tereza; Jonáš, Jakub; Gombala, Tomáš; David, Jan; Fencl, Filip; Klabusayová, Eva; Klučka, Jozef; Kratochvíl, Milan; Havránková, Pavla; Vrtková, Adéla; Slabá, Kateřina; Tučková, Jana; Homola, Lukáš; Štourač, Petr; Vymazal, Tomáš

Data formats and standards for opportunistic rainfall sensors

机会性降雨传感器的数据格式和标准

Fencl, Martin; Nebuloni, Roberto; C M Andersson, Jafet; Bares, Vojtech; Blettner, Nico; Cazzaniga, Greta; Chwala, Christian; Colli, Matteo; de Vos, Lotte; El Hachem, Abbas; Galdies, Charles; Giannetti, Filippo; Graf, Maximilian; Jacoby, Dror; Victor Habi, Hai; Musil, Petr; Ostrometzky, Jonatan; Roversi, Giacomo; Sapienza, Fabiola; Seidel, Jochen; Spackova, Anna; van de Beek, Remco; Walraven, Bas; Wilgan, Karina; Zheng, Xin

Alteration in DNA-binding affinity of Wilms tumor 1 protein due to WT1 genetic variants associated with steroid - resistant nephrotic syndrome in children

儿童类固醇抵抗性肾病综合征与WT1基因变异引起的Wilms肿瘤1蛋白DNA结合亲和力改变有关

Bezdicka, Martin; Kaufman, Filip; Krizova, Ivana; Dostalkova, Alzbeta; Rumlova, Michaela; Seeman, Tomas; Vondrak, Karel; Fencl, Filip; Zieg, Jakub; Soucek, Ondrej

Nationwide observational study of paediatric inflammatory multisystem syndrome temporally associated with SARS-CoV-2 (PIMS-TS) in the Czech Republic

捷克共和国全国范围内针对与SARS-CoV-2暂时相关的儿童炎症性多系统综合征(PIMS-TS)的观察性研究

David, Jan; Stara, Veronika; Hradsky, Ondrej; Tuckova, Jana; Slaba, Katerina; Jabandziev, Petr; Sasek, Lumir; Huml, Michal; Zidkova, Iveta; Pavlicek, Jan; Palatova, Alzbeta; Klaskova, Eva; Banszka, Karina; Terifajova, Eva; Vyhnanek, Radim; Bloomfield, Marketa; Fingerhutova, Sarka; Dolezalova, Pavla; Prochazkova, Lucie; Chramostova, Gabriela; Fencl, Filip; Lebl, Jan

The Drinking Water Tool: A Community-Driven Data Visualization Tool for Policy Implementation

饮用水工具:一款社区驱动的政策实施数据可视化工具

Pace, Clare; Fencl, Amanda; Baehner, Lauren; Lukacs, Heather; Cushing, Lara J; Morello-Frosch, Rachel

Results of targeted next-generation sequencing in children with cystic kidney diseases often change the clinical diagnosis

对患有囊性肾病的儿童进行靶向二代测序的结果通常会改变临床诊断。

Obeidova, Lena; Seeman, Tomas; Fencl, Filip; Blahova, Kveta; Hojny, Jan; Elisakova, Veronika; Reiterova, Jana; Stekrova, Jitka