日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

NRF2 deficit prevents pathologic Tau seeding and spreading in an induced tauopathy mouse model.

在诱导性 tau 蛋白病小鼠模型中,NRF2 缺陷可阻止病理性 Tau 蛋白的播散和扩散。

López-Sampere Yaiza, Mengod Soler Pol, Roca-Pereira Sergio, Vinyals Antonia, Mato-Blanco Xoel, Vela-Martínez Marta, Dakterzada Farida, Romero Leila, Santamaría Enrique, Fernández-Irigoyen Joaquín, Ferrer Isidro, Povedano Mónica, Del Rio José Antonio, Santpere Gabriel, Portero-Otín Manuel, Piñol-Ripoll Gerard, Andrés-Benito Pol

Rapid iPSC inclusionopathy models shed light on formation, consequence, and molecular subtype of α-synuclein inclusions

快速诱导多能干细胞包涵体病模型揭示了α-突触核蛋白包涵体的形成、后果和分子亚型

Lam, Isabel; Ndayisaba, Alain; Lewis, Amanda J; Fu, YuHong; Sagredo, Giselle T; Kuzkina, Anastasia; Zaccagnini, Ludovica; Celikag, Meral; Sandoe, Jackson; Sanz, Ricardo L; Vahdatshoar, Aazam; Martin, Timothy D; Morshed, Nader; Ichihashi, Toru; Tripathi, Arati; Ramalingam, Nagendran; Oettgen-Suazo, Charlotte; Bartels, Theresa; Boussouf, Manel; Schäbinger, Max; Hallacli, Erinc; Jiang, Xin; Verma, Amrita; Tea, Challana; Wang, Zichen; Hakozaki, Hiroyuki; Yu, Xiao; Hyles, Kelly; Park, Chansaem; Wang, Xinyuan; Theunissen, Thorold W; Wang, Haoyi; Jaenisch, Rudolf; Lindquist, Susan; Stevens, Beth; Stefanova, Nadia; Wenning, Gregor; van de Berg, Wilma D J; Luk, Kelvin C; Sanchez-Pernaute, Rosario; Gómez-Esteban, Juan Carlos; Felsky, Daniel; Kiyota, Yasujiro; Sahni, Nidhi; Yi, S Stephen; Chung, Chee Yeun; Stahlberg, Henning; Ferrer, Isidro; Schöneberg, Johannes; Elledge, Stephen J; Dettmer, Ulf; Halliday, Glenda M; Bartels, Tim; Khurana, Vikram

Distinct tau filament folds in human MAPT mutants P301L and P301T

人类MAPT突变体P301L和P301T中tau蛋白丝的独特折叠

Schweighauser, Manuel; Shi, Yang; Murzin, Alexey G; Garringer, Holly J; Vidal, Ruben; Murrell, Jill R; Erro, M Elena; Seelaar, Harro; Ferrer, Isidro; van Swieten, John C; Ghetti, Bernardino; Scheres, Sjors H W; Goedert, Michel

Neurodegeneration Biomarkers in Adult Spinal Muscular Atrophy (SMA) Patients Treated with Nusinersen

接受诺西那生治疗的成人脊髓性肌萎缩症 (SMA) 患者的神经退行性生物标志物

Andrés-Benito, Pol; Vázquez-Costa, Juan Francisco; Ñungo Garzón, Nancy Carolina; Colomina, María J; Marco, Carla; González, Laura; Terrafeta, Cristina; Domínguez, Raúl; Ferrer, Isidro; Povedano, Mónica

Alzheimer's Disease Neuropathological Change in Aged Non-Primate Mammals

老年非灵长类哺乳动物的阿尔茨海默病神经病理学变化

Ferrer, Isidro

Glycogen accumulation modulates life span in a mouse model of amyotrophic lateral sclerosis.

糖原积累调节肌萎缩侧索硬化症小鼠模型的寿命

Brewer M Kathryn, Torres Pascual, Ayala Victòria, Portero-Otin Manuel, Pamplona Reinald, Andrés-Benito Pol, Ferrer Isidro, Gentry Matthew S, Guinovart Joan J, Duran Jordi

Microvascular abnormalities in skin capillaries of individuals with amyotrophic lateral sclerosis

肌萎缩侧索硬化症患者皮肤毛细血管的微血管异常

Assialioui, Abdelilah; Marco-Pascual, Carla; Torrente-Segarra, Vicenç; Domínguez, Raul; Santos, Naiara; Peñafiel, Judith; Juanola, Xavier; Povedano, Mónica; Ferrer, Isidro

Amyloid-β Pathology Is the Common Nominator Proteinopathy of the Primate Brain Aging

淀粉样β蛋白病理是灵长类动物大脑衰老过程中常见的蛋白质病变

Ferrer, Isidro

Hypothesis review: Alzheimer's overture guidelines

假设回顾:阿尔茨海默病序曲指南

Ferrer, Isidro

Primary Feline Tauopathy: Clinical, Morphological, Immunohistochemical, and Genetic Studies.

原发性猫 Tau 蛋白病:临床、形态学、免疫组织化学和遗传学研究

Vidal-Palencia Laura, Font Cristina, Rebollada-Merino Agustín, Santpere Gabriel, Andrés-Benito Pol, Ferrer Isidro, Pumarola Martí