日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Transcriptomic Analysis Reveals the Beneficial Effects of Spermidine in an ALS Mouse Model

转录组分析揭示亚精胺在ALS小鼠模型中的有益作用

Tang, Maoxue; Teng, Sasa; Peng, Yueqing; Kim, Ashley Y; Her, Yoon-Ra; Canoll, Peter; Bruce, Jeffrey N; Faust, Phyllis L; Adhikari, Kailash; De Vivo, Darryl C; Monani, Umrao R; Akman, Nur; Kömüroğlu, Ahmet Ufuk; Çibuk, Salih; Altındağ, Fikret; Yılmaz, Osman; Ateşşahin, Ahmet; Fiorucci, Cristian; Rossi, Marianna Nicoletta; Santo, Rachele Di; Salvatori, Illari; Scaricamazza, Silvia; Giuliani, Stefano; Carletta, Olga; Filomena, Ermes; Laurenti, Davide; Mattioli, Roberto; Mosca, Luciana; Valle, Cristiana; Ferri, Alberto; D’Erchia, Anna Maria; Cervelli, Manuela

The hypothalamus is an early site of mitochondrial failure and neuro-immune circuit disruption in amyotrophic lateral sclerosis

下丘脑是肌萎缩侧索硬化症中线粒体功能衰竭和神经免疫回路紊乱的早期部位

Scaricamazza, Silvia; Nesci, Valentina; Fenili, Gianmarco; Tiberi, Marta; Percio, Anna; Rosina, Marco; Salvatori, Illari; Riggio, Flaminia; Candelise, Niccolò; Pieroni, Luisa; Greco, Viviana; Chiurchiù, Valerio; Ferri, Alberto; Valle, Cristiana

ADSL deficiency is a secondary mitochondrial disease affecting organelle homeostasis and ERK2/AKT signaling in a linear genotype-phenotype relation.

ADSL 缺乏症是一种继发性线粒体疾病,会影响细胞器稳态和 ERK2/AKT 信号传导,呈线性基因型-表型关系。

Bordi Matteo, Testa Beatrice, Compagnucci Claudia, Colasuonno Fiorella, Cipressa Francesca, Betterini Elisabetta, Mancini Andrea, Carsetti Claudia, Salvatori Illari, Ferraina Caterina, Yang Ming, De Cegli Rossella, Del Prete Eugenio, Veroni Chiara, Rizza Salvatore, Mauri Sofia, Ziviani Elena, Macchiaiolo Marina, Vecchio Davide, Panfili Filippo Maria, Rizza Teresa, Weber Gerrit, Carrozzo Rosalba, Ferri Alberto, Campello Silvia, Ballabio Andrea, Frezza Christian, Cestra Gianluca, Tartaglia Marco, Bartuli Andrea, Cecconi Francesco

Neuroglobin regulates autophagy through mTORC1/RAPTOR/ULK-1 pathway in human neuroblastoma cells.

神经球蛋白通过 mTORC1/RAPTOR/ULK-1 通路调节人类神经母细胞瘤细胞的自噬

Manganelli Valeria, Costanzo Michele, Caissutti Daniela, Salvatori Illari, Candelise Niccolò, Montalesi Emiliano, De Simone Giovanna, Ferri Alberto, Garofalo Tina, Sorice Maurizio, Ruoppolo Margherita, Longo Agostina, Misasi Roberta

Physical exercise in amyotrophic lateral sclerosis: a potential co-adjuvant therapeutic option to counteract disease progression

体育锻炼在肌萎缩侧索硬化症中的应用:一种潜在的辅助治疗选择,可对抗疾病进展

Fenili, Gianmarco; Scaricamazza, Silvia; Ferri, Alberto; Valle, Cristiana; Paronetto, Maria Paola

Loss of homeostatic functions in microglia from a murine model of Friedreich's ataxia

弗里德赖希共济失调小鼠模型中小胶质细胞稳态功能丧失

Della Valle, Ilaria; Milani, Martina; Rossi, Simona; Turchi, Riccardo; Tortolici, Flavia; Nesci, Valentina; Ferri, Alberto; Valle, Cristiana; Lettieri-Barbato, Daniele; Aquilano, Katia; Cozzolino, Mauro; Apolloni, Savina; D'Ambrosi, Nadia

Correction: Immune-mediated myogenesis and acetylcholine receptor clustering promote a slow disease progression in ALS mouse models

更正:免疫介导的肌生成和乙酰胆碱受体聚集促进ALS小鼠模型中疾病进展缓慢

Margotta, Cassandra; Fabbrizio, Paola; Ceccanti, Marco; Cambieri, Chiara; Rufolo, Gabriele; D'Agostino, Jessica; Trolese, Maria Chiara; Cifelli, Pierangelo; Alfano, Veronica; Laurini, Christian; Scaricamazza, Silvia; Ferri, Alberto; Sorarù, Gianni; Palma, Eleonora; Inghilleri, Maurizio; Bendotti, Caterina; Nardo, Giovanni

Lipid catabolism and mitochondrial uncoupling are stimulated in brown adipose tissue of amyotrophic lateral sclerosis mouse models

在肌萎缩侧索硬化症小鼠模型中,棕色脂肪组织中的脂质分解代谢和线粒体解偶联受到刺激。

Ciccarone, Fabio; Castelli, Serena; Lazzarino, Giacomo; Scaricamazza, Silvia; Mangione, Renata; Bernardini, Sergio; Apolloni, Savina; D'Ambrosi, Nadia; Ferri, Alberto; Ciriolo, Maria Rosa

Legacy perfluoro-alkyl substances impair LDL-cholesterol uptake independently from PCSK9-function

传统的全氟烷基物质独立于 PCSK9 功能损害 LDL 胆固醇的吸收

Iva Sabovic, Maria Giovanna Lupo, Ilaria Rossi, Federica Pedrucci, Andrea Di Nisio, Stefano Dall'Acqua, Nicola Ferri, Alberto Ferlin, Carlo Foresta, Luca De Toni

Mechanistic Insights of Mitochondrial Dysfunction in Amyotrophic Lateral Sclerosis: An Update on a Lasting Relationship

肌萎缩侧索硬化症中线粒体功能障碍的机制性见解:对持久关系的最新研究进展

Candelise, Niccolò; Salvatori, Illari; Scaricamazza, Silvia; Nesci, Valentina; Zenuni, Henri; Ferri, Alberto; Valle, Cristiana