日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

Exploring Desmin as a Potential Modifier in Duchenne Muscular Dystrophy-Associated Cardiomyopathy.

探索结蛋白作为杜氏肌营养不良症相关心肌病潜在调节因子的作用。

Guennec Brice-Emmanuel, Hovhannisyan Yeranuhi, Revet Gaëlle, Polat Sila, Hassani Medhi, Mougenot Nathalie, Barthelemy Inès, Blot Stephane, Cieniewski-Bernard Caroline, Ferry Arnaud, Kordeli Ekaterini, Li Zhenlin, Agbulut Onnik

Beneficial effects of resistance training on both mild and severe mouse dystrophic muscle function as a preclinical option for Duchenne muscular dystrophy

抗阻训练对轻度及重度小鼠肌营养不良症肌肉功能的有益作用,可作为杜氏肌营养不良症的临床前研究选择

Hassani, Medhi; Moutachi, Dylan; Lemaitre, Mégane; Boulinguiez, Alexis; Furling, Denis; Agbulut, Onnik; Ferry, Arnaud

The beneficial effect of chronic muscular exercise on muscle fragility is increased by Prox1 gene transfer in dystrophic mdx muscle

在营养不良型mdx肌肉中,Prox1基因转移可增强慢性肌肉锻炼对肌肉脆弱性的有益作用。

Monceau, Alexandra; Delacroix, Clément; Lemaitre, Mégane; Revet, Gaelle; Furling, Denis; Agbulut, Onnik; Klein, Arnaud; Ferry, Arnaud

Lamin-Related Congenital Muscular Dystrophy Alters Mechanical Signaling and Skeletal Muscle Growth

层粘蛋白相关先天性肌营养不良症会改变机械信号传导和骨骼肌生长

Owens, Daniel J; Messéant, Julien; Moog, Sophie; Viggars, Mark; Ferry, Arnaud; Mamchaoui, Kamel; Lacène, Emmanuelle; Roméro, Norma; Brull, Astrid; Bonne, Gisèle; Butler-Browne, Gillian; Coirault, Catherine

Peptide-conjugated oligonucleotides evoke long-lasting myotonic dystrophy correction in patient-derived cells and mice

肽偶联寡核苷酸可在患者来源细胞和小鼠中诱导持久的肌强直性营养不良症矫正

Klein, Arnaud F; Varela, Miguel A; Arandel, Ludovic; Holland, Ashling; Naouar, Naira; Arzumanov, Andrey; Seoane, David; Revillod, Lucile; Bassez, Guillaume; Ferry, Arnaud; Jauvin, Dominic; Gourdon, Genevieve; Puymirat, Jack; Gait, Michael J; Furling, Denis; Wood, Matthew Ja

Aged Nicotinamide Riboside Kinase 2 Deficient Mice Present an Altered Response to Endurance Exercise Training.

老年烟酰胺核苷激酶 2 缺陷小鼠对耐力运动训练的反应发生改变

Deloux Robin, Tannous Cynthia, Ferry Arnaud, Li Zhenlin, Mericskay Mathias

HACD1, a regulator of membrane composition and fluidity, promotes myoblast fusion and skeletal muscle growth

HACD1是膜组成和流动性的调节因子,可促进成肌细胞融合和骨骼肌生长。

Blondelle, Jordan; Ohno, Yusuke; Gache, Vincent; Guyot, Stéphane; Storck, Sébastien; Blanchard-Gutton, Nicolas; Barthélémy, Inès; Walmsley, Gemma; Rahier, Anaëlle; Gadin, Stéphanie; Maurer, Marie; Guillaud, Laurent; Prola, Alexandre; Ferry, Arnaud; Aubin-Houzelstein, Geneviève; Demarquoy, Jean; Relaix, Frédéric; Piercy, Richard J; Blot, Stéphane; Kihara, Akio; Tiret, Laurent; Pilot-Storck, Fanny

Viral-mediated expression of desmin mutants to create mouse models of myofibrillar myopathy

利用病毒介导表达结蛋白突变体构建肌原纤维肌病小鼠模型

Joanne, Pierre; Chourbagi, Oussama; Hourdé, Christophe; Ferry, Arnaud; Butler-Browne, Gillian; Vicart, Patrick; Dumonceaux, Julie; Agbulut, Onnik

Impaired adaptive response to mechanical overloading in dystrophic skeletal muscle.

营养不良骨骼肌对机械超负荷的适应性反应受损

Joanne Pierre, Hourdé Christophe, Ochala Julien, Caudéran Yvain, Medja Fadia, Vignaud Alban, Mouisel Etienne, Hadj-Said Wahiba, Arandel Ludovic, Garcia Luis, Goyenvalle Aurélie, Mounier Rémi, Zibroba Daria, Sakamoto Kei, Butler-Browne Gillian, Agbulut Onnik, Ferry Arnaud

Delivery of AAV2/9-microdystrophin genes incorporating helix 1 of the coiled-coil motif in the C-terminal domain of dystrophin improves muscle pathology and restores the level of α1-syntrophin and α-dystrobrevin in skeletal muscles of mdx mice

将包含肌营养不良蛋白C端结构域中螺旋卷曲基序第1螺旋的AAV2/9-微型肌营养不良蛋白基因递送至mdx小鼠,可改善肌肉病理,并恢复其骨骼肌中α1-合成蛋白和α-肌营养不良蛋白的水平。

Koo, Taeyoung; Malerba, Alberto; Athanasopoulos, Takis; Trollet, Capucine; Boldrin, Luisa; Ferry, Arnaud; Popplewell, Linda; Foster, Helen; Foster, Keith; Dickson, George