日期:
2020 年 — 2026 年
2020
2021
2022
2023
2024
2025
2026
影响因子:

The CHCHD2-CHCHD10 protein complex is modulated by mitochondrial dysfunction and alters lipid homeostasis in the mouse brain

CHCHD2-CHCHD10蛋白复合物受线粒体功能障碍调控,并改变小鼠脑内的脂质稳态。

Gerlach, Jule; Pireddu, Paola; Zhang, Xiaoqun; Wetzel, Simon; Mennuni, Mara; Milenkovic, Dusanka; Nolte, Hendrik; da Silva Rodrigues, Fernanda; Branzell, Niclas; Kaya, Ibrahim; Villegas, Rodolfo Garcia; Rubalcava-Gracia, Diana; Alsina, David; Feederle, Regina; Andrén, Per E; Langer, Thomas; Svenningsson, Per; Filograna, Roberta

Tissue-specific responses to TFAM and mtDNA copy number manipulation in prematurely ageing mice.

TFAM 和 mtDNA 拷贝数操纵对早衰小鼠的组织特异性反应

Kremer Laura Sophie, Gao Guanbin, Rigoni Giovanni, Filograna Roberta, Mennuni Mara, Wibom Rolf, Végvári Ákos, Koolmeister Camilla, Larsson Nils-Göran

Reduced mtDNA Copy Number Links to Vascular Calcification and Restores After Transplantation

线粒体DNA拷贝数减少与血管钙化有关,移植后可恢复

Schwarz, Angelina; Qureshi, Abdul Rashid; Hernandez, Leah; Wennberg, Lars; Wernerson, Annika; Kublickiene, Karolina; Shiels, Paul G; Filograna, Roberta; Stenvinkel, Peter; Witasp, Anna

Mammalian RNase H1 directs RNA primer formation for mtDNA replication initiation and is also necessary for mtDNA replication completion

哺乳动物 RNase H1 指导 RNA 引物的形成,启动线粒体 DNA 复制,并且对于线粒体 DNA 复制的完成也是必需的。

Misic, Jelena; Milenkovic, Dusanka; Al-Behadili, Ali; Xie, Xie; Jiang, Min; Jiang, Shan; Filograna, Roberta; Koolmeister, Camilla; Siira, Stefan J; Jenninger, Louise; Filipovska, Aleksandra; Clausen, Anders R; Caporali, Leonardo; Valentino, Maria Lucia; La Morgia, Chiara; Carelli, Valerio; Nicholls, Thomas J; Wredenberg, Anna; Falkenberg, Maria; Larsson, Nils-Göran

Editorial: Defective macroautophagy in organelle turnover: From basic mechanisms to human disease

社论:细胞器周转中巨自噬缺陷:从基本机制到人类疾病

Bejarano, Eloy; Rodríguez-Navarro, José Antonio; Filograna, Roberta; Calvo-Garrido, Javier

Mitochondrial DNA copy number in human disease: the more the better?

线粒体DNA拷贝数与人类疾病的关系:越多越好吗?

Filograna, Roberta; Mennuni, Mara; Alsina, David; Larsson, Nils-Göran

Erratum to: Leucine-rich repeat kinase 2 positively regulates inflammation and down-regulates NF-κB p50 signaling in cultured microglia cells

更正:富含亮氨酸重复激酶2正向调节培养的小胶质细胞中的炎症并下调NF-κB p50信号通路

Russo, Isabella; Berti, Giulia; Plotegher, Nicoletta; Bernardo, Greta; Filograna, Roberta; Bubacco, Luigi; Greggio, Elisa

A Phenotype-Driven Approach to Generate Mouse Models with Pathogenic mtDNA Mutations Causing Mitochondrial Disease

利用表型驱动方法构建携带致病性线粒体DNA突变的小鼠模型,以治疗线粒体疾病

Kauppila, Johanna H K; Baines, Holly L; Bratic, Ana; Simard, Marie-Lune; Freyer, Christoph; Mourier, Arnaud; Stamp, Craig; Filograna, Roberta; Larsson, Nils-Göran; Greaves, Laura C; Stewart, James B

Anti-Oxidants in Parkinson's Disease Therapy: A Critical Point of View

抗氧化剂在帕金森病治疗中的应用:批判性观点

Filograna, Roberta; Beltramini, Mariano; Bubacco, Luigi; Bisaglia, Marco

Analysis of the Catecholaminergic Phenotype in Human SH-SY5Y and BE(2)-M17 Neuroblastoma Cell Lines upon Differentiation

人SH-SY5Y和BE(2)-M17神经母细胞瘤细胞系分化过程中儿茶酚胺能表型的分析

Filograna, Roberta; Civiero, Laura; Ferrari, Vanni; Codolo, Gaia; Greggio, Elisa; Bubacco, Luigi; Beltramini, Mariano; Bisaglia, Marco